Q22.0
BillablePulmonary valve atresia
Pulmonary valve atresia
Coding Notes
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(8)
Q22.1Congenital pulmonary valve stenosis
Q22.2Congenital pulmonary valve insufficiency
Q22.3Other congenital malformations of pulmonary valve
Q22.4Congenital tricuspid stenosis
Q22.5Ebstein's anomaly
Q22.6Hypoplastic right heart syndrome
Q22.8Other congenital malformations of tricuspid valve
Q22.9Congenital malformation of tricuspid valve, unspecified
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(145)
SNOMED CT
- Absent pulmonary valve6996004
- Congenital absence of pulmonary valve6996004
- Congenital absence of pulmonic valve6996004
- PDA - Patent ductus arteriosus83330001
- Patent arterial duct83330001
- Patent ductus Botalli83330001
- Patent ductus arteriosus83330001
- Fallot's tetralogy86299006
- Subpulmonic stenosis, ventricular septal defect, overriding aorta, AND right ventricular hypertrophy86299006
- TOF - Tetralogy of Fallot86299006
- Tetralogy of Fallot86299006
- Absent ductus arteriosus92965002
- Congenital absence of ductus arteriosus92965002
- Congenital hypoplasia of pulmonary valve93287006
- Congenital hypoplasia of pulmonic valve93287006
- Congenital small pulmonic valve93287006
- Congenital atresia of pulmonary valve204342004
- Imperforate pulmonary valve204342004
- Hypoplasia of pulmonary valve204343009
- Fallot's type pulmonary valve atresia253513005
- Tetralogy of Fallot with atresia of pulmonary valve253513005
- Tetralogy of Fallot with pulmonary valve atresia253513005
- Pulmonary valve cusp hypoplasia253585006
- PAIV - Pulmonary atresia with intact ventricular septum253590009
- Pulmonary atresia with intact ventricular septum253590009
- PAVSD - Pulmonary atresia with ventricular septal defect253591008
- Pulmonary atresia with ventricular septal defect253591008
- Pulmonary valve atresia without ventricular outflow tract253592001
- Muscular pulmonary atresia253594000
- APVS - Absent pulmonary valve syndrome253596003
- Absent pulmonary valve syndrome253596003
- Congenital abnormality of thoracic aorta and pulmonary arteries271573009
- Tetralogy of Fallot with absent pulmonary valve399228007
- Pulmonary atresia and ventricular septal defect with aorta from left ventricle447838003
- Pulmonary atresia and ventricular septal defect with aorta from right ventricle447839006
- Pulmonary atresia with ventricular septal defect of Fallot type448155003
- Absent pulmonary valve syndrome with ventricular septal defect of non Fallot type448475002
- Absence of pulmonary valve cusp449133000
- Hypoplasia of pulmonary cusps of absent pulmonary valve type449354002
- Rudimentary pulmonary cusps (absent pulmonary valve type)449354002
- Atresia of pulmonary valve719955006
- Pulmonary valve atresia719955006
- Tetralogy of Fallot with pulmonary atresia and systemic-to-pulmonary collateral artery762433009
- Tetralogy of Fallot with pulmonary atresia co-occurrent with systemic-to-pulmonary collateral artery762433009
- Absence of pulmonary valve, Fallot tetralogy, absence of ductus arteriosus syndrome766976003
- Pulmonary valve agenesis, tetralogy of Fallot, absence of ductus arteriosus syndrome766976003
- APV (agenesis pulmonary valve) PDA (patent ductus arteriosus) non-Fallot type784353002
- Pulmonary valve agenesis, intact ventricular septum, persistent ductus arteriosus syndrome784353002
- Agenesis of artery789097007
UMLS
- ATRESIA PULMC0242855
- ATRESIA PULM VALVEC0242855
- ATRESIAS PULMC0242855
- ATRESIAS PULM VALVEC0242855
- Atresia of pulmonary valve, congenitalC0242855
- Atresia, PulmonaryC0242855
- Atresia, Pulmonary ValveC0242855
- Atresias, PulmonaryC0242855
- Atresias, Pulmonary ValveC0242855
- Congenital atresia of pulmonary valveC0242855
- Congenital atresia of pulmonary valve (disorder)C0242855
- Congenital pulmonary valve atresiaC0242855
- Imperforate pulmonary valveC0242855
- PULM ATRESIAC0242855
- PULM ATRESIASC0242855
- PULM VALVE ATRESIAC0242855
- PULM VALVE ATRESIASC0242855
- Pulmonary AtresiaC0242855
- Pulmonary AtresiasC0242855
- Pulmonary Valve AtresiaC0242855
- Pulmonary Valve AtresiasC0242855
- Pulmonary valve atresiaC0242855
- Valve Atresia, PulmonaryC0242855
- Valve Atresias, PulmonaryC0242855
- atresia pulmonaryC0242855
- pulmonary atresiaC0242855
- pulmonary valve atresiaC0242855
Clinical Terms
- Absent pulmonary valve
- Hypoplasia of pulmonary cusps of absent pulmonary valve type
- PULM ATRESIA
- Pulmonary atresia with ventricular septal defect
- Atresia, Pulmonary
- PDA - Patent ductus arteriosus
- Pulmonary atresia and ventricular septal defect with aorta from left ventricle
- Congenital absence of ductus arteriosus
- Absence of pulmonary valve, Fallot tetralogy, absence of ductus arteriosus syndrome
- Tetralogy of Fallot with pulmonary atresia and systemic-to-pulmonary collateral artery
- Congenital hypoplasia of pulmonic valve
- Absence of pulmonary valve cusp
- Congenital atresia of pulmonary valve
- Tetralogy of Fallot with pulmonary valve atresia
- ATRESIA PULM
- Congenital hypoplasia of pulmonary valve
- Patent arterial duct
- Atresia, Pulmonary Valve
- Atresia of pulmonary valve
- Congenital pulmonary valve atresia
- Agenesis of artery
- ATRESIAS PULM VALVE
- PULM VALVE ATRESIA
- Pulmonary valve cusp hypoplasia
- Atresias, Pulmonary
- Muscular pulmonary atresia
- Fallot's type pulmonary valve atresia
- Absent ductus arteriosus
- PAIV - Pulmonary atresia with intact ventricular septum
- Congenital abnormality of thoracic aorta and pulmonary arteries
- APVS - Absent pulmonary valve syndrome
- Patent ductus Botalli
- Tetralogy of Fallot with absent pulmonary valve
- Tetralogy of Fallot
- Pulmonary Valve Atresias
- APV (agenesis pulmonary valve) PDA (patent ductus arteriosus) non-Fallot type
- Congenital small pulmonic valve
- Pulmonary atresia with intact ventricular septum
- Subpulmonic stenosis, ventricular septal defect, overriding aorta, AND right ventricular hypertrophy
- Atresia of pulmonary valve, congenital
- Pulmonary valve agenesis, tetralogy of Fallot, absence of ductus arteriosus syndrome
- Valve Atresia, Pulmonary
- pulmonary atresia
- Pulmonary atresia with ventricular septal defect of Fallot type
- Tetralogy of Fallot with atresia of pulmonary valve
- Absent pulmonary valve syndrome with ventricular septal defect of non Fallot type
- PULM VALVE ATRESIAS
- TOF - Tetralogy of Fallot
- Congenital atresia of pulmonary valve (disorder)
- Pulmonary valve atresia without ventricular outflow tract
- Hypoplasia of pulmonary valve
- ATRESIAS PULM
- Absent pulmonary valve syndrome
- Imperforate pulmonary valve
- ATRESIA PULM VALVE
- Fallot's tetralogy
- atresia pulmonary
- PAVSD - Pulmonary atresia with ventricular septal defect
- Tetralogy of Fallot with pulmonary atresia co-occurrent with systemic-to-pulmonary collateral artery
- Congenital absence of pulmonic valve
- Atresias, Pulmonary Valve
- PULM ATRESIAS
- Patent ductus arteriosus
- Pulmonary Atresias
- Rudimentary pulmonary cusps (absent pulmonary valve type)
- Valve Atresias, Pulmonary
- Congenital absence of pulmonary valve
- Pulmonary atresia and ventricular septal defect with aorta from right ventricle
- Pulmonary valve agenesis, intact ventricular septum, persistent ductus arteriosus syndrome
Frequently Asked Questions
What is the ICD-10 code for pulmonary valve atresia?
The ICD-10-CM code for pulmonary valve atresia is Q22.0. The full clinical description is "Pulmonary valve atresia". Q22.0 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q22.0 mean?
ICD-10-CM code Q22.0 represents “Pulmonary valve atresia”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q22.0 a billable code?
Yes, Q22.0 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q22.0 in?
Q22.0 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What SNOMED CT codes does Q22.0 map to?
Q22.0 maps to 27 SNOMED CT concepts: 784353002, 253596003, 449133000, 766976003, 92965002, and 22 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q22.0?
Q22.0 is linked to 1 UMLS Concept Unique Identifier: C0242855. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q22.0 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like pulmonary valve atresia affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q22.0?
Q22.0 maps to the ICD-11 code: LA8A.1Z (Congenital pulmonary atresia, unspecified).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.