Q13.81
BillableRieger anomaly
Rieger anomaly
Status
Billable / Specific
Parent Code
Q13.8Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Axenfeld-Rieger syndrome
Excludes 2
Conditions not included here, but the patient may have both
- •inborn errors of metabolismE70-E88
- •cleft lip and cleft palateQ35-Q37
- •congenital malformation of cervical spine, , ,Q05.0, Q05.5, Q67.5, Q76.0-Q76.4
- •congenital malformation of larynxQ31
- •congenital malformation of lip NECQ38.0
- •congenital malformation of noseQ30
- •congenital malformation of parathyroid glandQ89.2
- •congenital malformation of thyroid glandQ89.2
Code Also
A second code may be required; sequencing depends on circumstances
- any other associated congenital malformations such as cardiac defects
Also Known As / Clinical Terms(63)
SNOMED CT
- Rieger anomaly47507006
- Rieger syndrome47507006
- Rieger's syndrome47507006
- Acquired partial lipodystrophy75659004
- Barraquer syndrome75659004
- Barraquer-Simons disease75659004
- Barraquer-Simons syndrome75659004
- Hollander-Simons syndrome75659004
- Lipodystrophic diabetes with partial lipoatrophy75659004
- Macrodystrophia lipomatosa progressiva75659004
- Partial lipoatrophy75659004
- Progressive lipodystrophy75659004
- Progressive partial lipodystrophy75659004
- Irido-trabecular dysgenesis204154009
- Mesodermal dysgenesis of iris204154009
- Lipodystrophy, partial, with Rieger anomaly, short stature, and insulinopenic diabetes mellitus237608006
- Axenfeld syndrome417604002
- Axenfeld-Rieger syndrome417604002
UMLS
- ARSC3495488
- AXRSC3495488
- Axenfeld syndromeC3495488
- Axenfeld-Rieger syndromeC3495488
- Axenfeld-Rieger syndrome (disorder)C3495488
- Iridogoniodysgenesis with somatic anomaliesC3495488
- Rieger SyndromeC0265341
- Rieger anomalyC0265341
- Rieger syndromeC0265341
- Rieger syndrome (disorder)C0265341
- Rieger's anomalyC0265341
- Rieger's syndromeC0265341
- axenfeld syndromeC0265341
- axenfeld's syndromeC0265341
- axenfelds syndromeC0265341
- rieger anomalyC0265341
- rieger syndromeC0265341
- rieger's syndromeC0265341
- riegers syndromeC0265341
Clinical Terms
- Acquired partial lipodystrophy
- Irido-trabecular dysgenesis
- Axenfeld syndrome
- axenfelds syndrome
- rieger's syndrome
- Iridogoniodysgenesis with somatic anomalies
- Macrodystrophia lipomatosa progressiva
- riegers syndrome
- Lipodystrophic diabetes with partial lipoatrophy
- Partial lipoatrophy
- rieger syndrome
- AXRS
- axenfeld's syndrome
- Rieger's anomaly
- Axenfeld-Rieger syndrome
- Hollander-Simons syndrome
- Rieger syndrome (disorder)
- Mesodermal dysgenesis of iris
- Barraquer-Simons disease
- Barraquer syndrome
- Progressive lipodystrophy
- ARS
- Barraquer-Simons syndrome
- Axenfeld-Rieger syndrome (disorder)
- Lipodystrophy, partial, with Rieger anomaly, short stature, and insulinopenic diabetes mellitus
- Progressive partial lipodystrophy
Frequently Asked Questions
What is the ICD-10 code for rieger anomaly?
The ICD-10-CM code for rieger anomaly is Q13.81. The full clinical description is "Rieger anomaly". Q13.81 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q13.81 mean?
ICD-10-CM code Q13.81 represents “Rieger anomaly”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q13.81 a billable code?
Yes, Q13.81 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q13.81 in?
Q13.81 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
Are additional codes required with Q13.81?
Yes, when using Q13.81, also report: associated glaucoma (H42).
What SNOMED CT codes does Q13.81 map to?
Q13.81 maps to 5 SNOMED CT concepts: 75659004, 417604002, 204154009, 237608006, 47507006. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q13.81?
Q13.81 is linked to 2 UMLS Concept Unique Identifiers: C3495488, C0265341. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q13.81 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like rieger anomaly affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q13.81?
There is no direct ICD-11 mapping available for Q13.81 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.