Q07.9
BillableCongenital malformation of nervous system, unspecified
Congenital malformation of nervous system, unspecified
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Congenital anomaly NOS of nervous system
- Congenital deformity NOS of nervous system
- Congenital disease or lesion NOS of nervous system
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(2)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(229)
SNOMED CT
- Pili torti17170005
- Twisted hair17170005
- Congenital anomaly of the peripheral nervous system22133005
- Congenital anomaly of peripheral nerve23880008
- Congenital hepatic fibrosis79607001
- Congenital anomaly of nervous system88425004
- Congenital deformity of nervous system88425004
- Congenital disease of nervous system88425004
- Congenital lesion of nervous system88425004
- Congenital malformation of the nervous system88425004
- Cerebrofacial dysplasia109561000
- COD-MD - Cerebro-oculo-dysgenesis-muscular dystrophy syndrome111505001
- Cerebro-oculo-dysgenesis-muscular dystrophy syndrome111505001
- Muscle-eye-brain disease, congenital muscular dystrophy111505001
- Congenital anomaly of central nervous system128124001
- Congenital malformation of central nervous system128124001
- Congenital polyneuropathy230560008
- NTD - Neural tube defect253098009
- Neural tube defect253098009
- Vascular malformation of the nervous system253193002
- Congenital anomaly of the meninges253199003
- Congenital malformation of the meninges253199003
- Combined malformation of central nervous system and skeletal muscle277949001
- Muscle eye brain disease277950001
- Congenital anomaly of nervous system of head/neck287080001
- Congenital anomaly of neural structure of trunk363034005
- Immature autonomic stability371109001
- Immature autonomic system371109001
- Hypertrophic mitochondrial cardiomyopathy472316006
- Naevus sebaceous707136009
- Naevus sebaceous of Jadassohn707136009
- Nevus sebaceous707136009
- Nevus sebaceous of Jadassohn707136009
- Organoid naevus707136009
- Organoid nevus707136009
- Sebaceous naevus707136009
- Sebaceous nevus707136009
- Pili torti with developmental delay and neurological abnormality syndrome716194005
- Congenital cataract, nephropathy, encephalopathy syndrome722381004
- Crome syndrome722381004
- Congenital malformation of autonomic nervous system722996009
- Coenzyme Q10 deficiency724575009
- Freire Maia Pinheiro Opitz syndrome725908007
- NFDR (neurofaciodigitorenal) syndrome725908007
- Neurofaciodigitorenal syndrome725908007
- Cyprus facial neuromusculoskeletal syndrome732261005
- Ectodermal dysplasia, intellectual disability, central nervous system malformation syndrome734017008
- Encephalopathy, hypertrophic cardiomyopathy, renal tubular disease syndrome763280005
- HIVEP2 (human immunodeficiency virus type I enhancer binding protein 2) related intellectual disability765434008
- HIVEP2-related intellectual disability765434008
- Human immunodeficiency virus type I enhancer binding protein 2 related intellectual disability765434008
- Goldston syndrome773737004
- Meckel syndrome type 7773737004
- Meckel-like syndrome type 1773737004
- NPHP3 (nephrocystin 3) related Meckel-like syndrome773737004
- NPHP3-related Meckel-like syndrome773737004
- Nephrocystin 3-related Meckel-like syndrome773737004
- Renal, hepatic, pancreatic dysplasia, Dandy-Walker cysts syndrome773737004
- FBLN1-related developmental delay, central nervous system anomaly, syndactyly syndrome774070008
- Fibulin 1-related developmental delay, central nervous system anomaly, syndactyly syndrome774070008
- SCALP syndrome774208009
- Sebaceous naevus, central nervous system malformations, aplasia cutis congenita, limbal dermoid, pigmented naevus syndrome774208009
- Sebaceous nevus, central nervous system malformations, aplasia cutis congenita, limbal dermoid, pigmented nevus syndrome774208009
- MEND (male emopamil-binding protein disorder with neurological defect) syndrome782739000
- Male EBP (emopamil-binding protein) disorder with neurological defect782739000
- Male emopamil-binding protein disorder with neurological defect782739000
- Cortical dysgenesis with pontocerebellar hypoplasia due to TUBB3 mutation784344009
- Cortical dysgenesis with pontocerebellar hypoplasia due to tubulin beta 3 class III mutation784344009
- Navajo neurohepatopathy784346006
- Navajo neuropathy784346006
- Hypoplasia of optic nerve due to central nervous system malformation1003422005
- Global developmental delay, neuro-ophthalmological abnormalities, seizures, intellectual disability syndrome1172630000
UMLS
- ABNORM CONGEN NERVOUS SYSTEMC0497552
- ABNORM NERVOUS SYSTEMC0497552
- Abnormalities, Congenital, Nervous SystemC0497552
- Abnormalities, Nervous SystemC0497552
- Abnormality of the nervous systemC0497552
- Abnormality, Nervous SystemC0497552
- Anomalies, Nervous SystemC0497552
- Anomaly, Nervous SystemC0497552
- CONGEN ABNORM NERVOUS SYSTEMC0497552
- CONGEN ANOMALIES NERVOUS SYSTEMC0497552
- CONGEN MALFORMATIONS NERVOUS SYSTEMC0497552
- Congenital Abnormalities, Nervous SystemC0497552
- Congenital Anomalies, Nervous SystemC0497552
- Congenital Malformations, Nervous SystemC0497552
- Congenital Nervous System DisorderC0497552
- Congenital anomaly NOS of nervous systemC0497552
- Congenital anomaly of nervous systemC0497552
- Congenital anomaly of nervous system (disorder)C0497552
- Congenital deformity NOS of nervous systemC0497552
- Congenital deformity of nervous systemC0497552
- Congenital disease of nervous systemC0497552
- Congenital lesion of nervous systemC0497552
- Congenital malformation of nervous system, unspecifiedC0497552
- Congenital malformation of the nervous systemC0497552
- Congenital malformations of the nervous system (Q00-Q07)C0497552
- MALFORMATIONS NERVOUS SYSTEM CONGENC0497552
- Malformation, Nervous SystemC0497552
- Malformations, Nervous SystemC0497552
- Malformations, Nervous System, CongenitalC0497552
- NERVOUS SYSTEM ABNORMC0497552
- NERVOUS SYSTEM CONGEN ABNORMC0497552
- NERVOUS SYSTEM CONGEN MALFORMATIONSC0497552
- NERVOUS SYSTEM MALFORMATIONS CONGENC0497552
- Nervous System AbnormalitiesC0497552
- Nervous System AbnormalityC0497552
- Nervous System AnomaliesC0497552
- Nervous System AnomalyC0497552
- Nervous System Congenital AbnormalitiesC0497552
- Nervous System Congenital MalformationsC0497552
- Nervous System MalformationC0497552
- Nervous System MalformationsC0497552
- Nervous System Malformations, CongenitalC0497552
- Neurologic abnormalitiesC0497552
- Neurological abnormalityC0497552
- congenital nervous system disorderC0497552
- Congenital disease or lesion NOS of nervous systemC2910110
Clinical Terms
- Sebaceous naevus
- NERVOUS SYSTEM ABNORM
- Congenital anomaly of central nervous system
- Congenital malformation of central nervous system
- Navajo neuropathy
- Nervous System Malformations
- Congenital Malformations, Nervous System
- NERVOUS SYSTEM MALFORMATIONS CONGEN
- SCALP syndrome
- Coenzyme Q10 deficiency
- Pili torti with developmental delay and neurological abnormality syndrome
- Cortical dysgenesis with pontocerebellar hypoplasia due to TUBB3 mutation
- Neurofaciodigitorenal syndrome
- Abnormalities, Nervous System
- Sebaceous nevus
- Renal, hepatic, pancreatic dysplasia, Dandy-Walker cysts syndrome
- Crome syndrome
- Congenital anomaly of peripheral nerve
- Sebaceous nevus, central nervous system malformations, aplasia cutis congenita, limbal dermoid, pigmented nevus syndrome
- CONGEN MALFORMATIONS NERVOUS SYSTEM
- Congenital lesion of nervous system
- Congenital polyneuropathy
- Nervous System Anomalies
- Male emopamil-binding protein disorder with neurological defect
- Abnormality of the nervous system
- Nevus sebaceous of Jadassohn
- Congenital Anomalies, Nervous System
- Cyprus facial neuromusculoskeletal syndrome
- NERVOUS SYSTEM CONGEN ABNORM
- Twisted hair
- Navajo neurohepatopathy
- Meckel syndrome type 7
- Cortical dysgenesis with pontocerebellar hypoplasia due to tubulin beta 3 class III mutation
- Nervous System Malformation
- Congenital cataract, nephropathy, encephalopathy syndrome
- NTD - Neural tube defect
- Hypertrophic mitochondrial cardiomyopathy
- Congenital disease of nervous system
- Congenital malformations of the nervous system (Q00-Q07)
- Congenital malformation of the nervous system
- Nervous System Congenital Abnormalities
- Muscle-eye-brain disease, congenital muscular dystrophy
- Congenital anomaly of the meninges
- Sebaceous naevus, central nervous system malformations, aplasia cutis congenita, limbal dermoid, pigmented naevus syndrome
- Congenital deformity of nervous system
- Congenital deformity NOS of nervous system
- Vascular malformation of the nervous system
- Nervous System Abnormality
- Encephalopathy, hypertrophic cardiomyopathy, renal tubular disease syndrome
- HIVEP2-related intellectual disability
- Cerebro-oculo-dysgenesis-muscular dystrophy syndrome
- NPHP3 (nephrocystin 3) related Meckel-like syndrome
- Congenital malformation of the meninges
- Human immunodeficiency virus type I enhancer binding protein 2 related intellectual disability
- Naevus sebaceous
- Malformations, Nervous System
- CONGEN ABNORM NERVOUS SYSTEM
- ABNORM NERVOUS SYSTEM
- Nervous System Abnormalities
- Congenital anomaly of nervous system
- Neural tube defect
- NERVOUS SYSTEM CONGEN MALFORMATIONS
- ABNORM CONGEN NERVOUS SYSTEM
- Anomaly, Nervous System
- COD-MD - Cerebro-oculo-dysgenesis-muscular dystrophy syndrome
- NPHP3-related Meckel-like syndrome
- Immature autonomic system
- Nephrocystin 3-related Meckel-like syndrome
- Congenital malformation of autonomic nervous system
- Combined malformation of central nervous system and skeletal muscle
- Congenital anomaly of the peripheral nervous system
- Anomalies, Nervous System
- Nevus sebaceous
- Ectodermal dysplasia, intellectual disability, central nervous system malformation syndrome
- Abnormality, Nervous System
- Congenital Nervous System Disorder
- Malformation, Nervous System
- Congenital anomaly of nervous system of head/neck
- Congenital disease or lesion NOS of nervous system
- Immature autonomic stability
- Nervous System Malformations, Congenital
- Abnormalities, Congenital, Nervous System
- Nervous System Congenital Malformations
- Global developmental delay, neuro-ophthalmological abnormalities, seizures, intellectual disability syndrome
- Organoid nevus
- CONGEN ANOMALIES NERVOUS SYSTEM
- Cerebrofacial dysplasia
- FBLN1-related developmental delay, central nervous system anomaly, syndactyly syndrome
- Male EBP (emopamil-binding protein) disorder with neurological defect
- Congenital Abnormalities, Nervous System
- Congenital anomaly of nervous system (disorder)
- Goldston syndrome
- Naevus sebaceous of Jadassohn
- Hypoplasia of optic nerve due to central nervous system malformation
- Meckel-like syndrome type 1
- Congenital anomaly NOS of nervous system
- Freire Maia Pinheiro Opitz syndrome
- Fibulin 1-related developmental delay, central nervous system anomaly, syndactyly syndrome
- Neurologic abnormalities
- HIVEP2 (human immunodeficiency virus type I enhancer binding protein 2) related intellectual disability
- NFDR (neurofaciodigitorenal) syndrome
- MALFORMATIONS NERVOUS SYSTEM CONGEN
- MEND (male emopamil-binding protein disorder with neurological defect) syndrome
- Congenital anomaly of neural structure of trunk
- Organoid naevus
- Neurological abnormality
- Nervous System Anomaly
- Muscle eye brain disease
- Congenital hepatic fibrosis
- Malformations, Nervous System, Congenital
- Pili torti
Frequently Asked Questions
What is the ICD-10 code for congenital malformation of nervous system, unspecified?
The ICD-10-CM code for congenital malformation of nervous system, unspecified is Q07.9. The full clinical description is "Congenital malformation of nervous system, unspecified". Q07.9 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q07.9 mean?
ICD-10-CM code Q07.9 represents “Congenital malformation of nervous system, unspecified”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q07.9 a billable code?
Yes, Q07.9 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q07.9 in?
Q07.9 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What SNOMED CT codes does Q07.9 map to?
Q07.9 maps to 36 SNOMED CT concepts: 111505001, 109561000, 724575009, 277949001, 128124001, and 31 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q07.9?
Q07.9 is linked to 2 UMLS Concept Unique Identifiers: C0497552, C2910110. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q07.9 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like congenital malformation of nervous system, unspecified affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q07.9?
Q07.9 maps to the ICD-11 code: LA0Z (Structural developmental anomalies of the nervous system, unspecified).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.