L81.3
BillableCafe au lait spots
Cafe au lait spots
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- •certain conditions originating in the perinatal periodP04-P96
- •certain infectious and parasitic diseasesA00-B99
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations, and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •lipomelanotic reticulosisI89.8
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
- •systemic connective tissue disordersM30-M36
- •viral wartsB07
- nevus - see Alphabetical Index
Related Codes(9)
L81.0Postinflammatory hyperpigmentation
L81.1Chloasma
L81.2Freckles
L81.4Other melanin hyperpigmentation
L81.5Leukoderma, not elsewhere classified
L81.6Other disorders of diminished melanin formation
L81.7Pigmented purpuric dermatosis
L81.8Other specified disorders of pigmentation
L81.9Disorder of pigmentation, unspecified
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(86)
SNOMED CT
- Multiple non-ossifying fibromatosis92824003
- NF1 - Neurofibromatosis type 192824003
- Neurofibromatosis 192824003
- Neurofibromatosis type 192824003
- Neurofibromatosis, peripheral type92824003
- Von Recklinghausen disease92824003
- Cafe au lait spots201281002
- Cafe-au-lait spots201281002
- Café au lait spot201281002
- Café au lait spots201281002
- Multiple cafe-au-lait macules due to neurofibromatosis403816002
- Multiple café-au-lait macules due to neurofibromatosis403816002
- Cafe-au-lait macules with pulmonary stenosis403820003
- Café-au-lait macules with pulmonary stenosis403820003
- Watson syndrome403820003
- Cafe-au-lait macules with temporal dysrhythmia403821004
- Café-au-lait macules with temporal dysrhythmia403821004
- Intrauterine growth restriction, congenital multiple café au lait macules, increased sister chromatid exchange syndrome1177178005
- Familial CALMs (café-au-lait macules) isolated1208340009
- Familial café-au-lait spots1208340009
- Familial isolated café-au-lait macules1208340009
- Familial isolated café-au-lait spots1208340009
- Multiple café-au-lait spots1208340009
- Multiple café-au-lait syndrome1208340009
- NF6 - neurofibromatosis type 61208340009
- Neurofibromatosis type 61208340009
UMLS
- Cafe Au Lait PatchC0221263
- Cafe Au Lait SpotC0221263
- Cafe au Lait SpotsC0221263
- Cafe au lait spotC0221263
- Cafe au lait spotsC0221263
- Cafe-au-Lait SpotC0221263
- Cafe-au-Lait SpotsC0221263
- Cafe-au-lait maculeC0221263
- Cafe-au-lait maculesC0221263
- Cafe-au-lait patchesC0221263
- Cafe-au-lait spotC0221263
- Cafe-au-lait spotsC0221263
- Café Au Lait PatchC0221263
- Café Au Lait SpotC0221263
- Café au lait spotC0221263
- Café au lait spot (disorder)C0221263
- Café au lait spotsC0221263
- Spot, Cafe-au-LaitC0221263
- Spots, Cafe-au-LaitC0221263
- au cafe lait spotsC0221263
- cafe au lait spotC0221263
- cafe au lait spotsC0221263
- cafe-au-lait spotC0221263
- cafe-au-lait spotsC0221263
Clinical Terms
- Cafe-au-Lait Spot
- Watson syndrome
- Von Recklinghausen disease
- Cafe-au-Lait Spots
- Cafe-au-lait macule
- Café Au Lait Spot
- Café-au-lait macules with temporal dysrhythmia
- Multiple café-au-lait syndrome
- Cafe-au-lait macules with temporal dysrhythmia
- au cafe lait spots
- Familial CALMs (café-au-lait macules) isolated
- Café Au Lait Patch
- Café-au-lait macules with pulmonary stenosis
- Spots, Cafe-au-Lait
- Intrauterine growth restriction, congenital multiple café au lait macules, increased sister chromatid exchange syndrome
- Familial isolated café-au-lait macules
- Cafe Au Lait Patch
- Neurofibromatosis 1
- Neurofibromatosis, peripheral type
- Cafe au lait spot
- Neurofibromatosis type 1
- NF6 - neurofibromatosis type 6
- Familial café-au-lait spots
- Café au lait spots
- Multiple cafe-au-lait macules due to neurofibromatosis
- Café au lait spot (disorder)
- Spot, Cafe-au-Lait
- Multiple non-ossifying fibromatosis
- Multiple café-au-lait spots
- Neurofibromatosis type 6
- Familial isolated café-au-lait spots
- Cafe-au-lait patches
- Cafe-au-lait macules
- Cafe-au-lait macules with pulmonary stenosis
- NF1 - Neurofibromatosis type 1
- Multiple café-au-lait macules due to neurofibromatosis
Frequently Asked Questions
What is the ICD-10 code for cafe au lait spots?
The ICD-10-CM code for cafe au lait spots is L81.3. The full clinical description is "Cafe au lait spots". L81.3 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code L81.3 mean?
ICD-10-CM code L81.3 represents “Cafe au lait spots”. It is classified under Chapter 12: Diseases of the Skin and Subcutaneous Tissue and is a billable/specific code that can be used on a claim.
Is L81.3 a billable code?
Yes, L81.3 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is L81.3 in?
L81.3 is in Chapter 12: Diseases of the Skin and Subcutaneous Tissue (codes L00-L99).
What codes cannot be used with L81.3?
L81.3 has Excludes1 notes indicating codes that cannot be used together with it, including: birthmark NOS (Q82.5); Peutz-Jeghers syndrome (Q85.89).
What SNOMED CT codes does L81.3 map to?
L81.3 maps to 7 SNOMED CT concepts: 201281002, 403820003, 403821004, 1208340009, 1177178005, and 2 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for L81.3?
L81.3 is linked to 1 UMLS Concept Unique Identifier: C0221263. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does L81.3 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like cafe au lait spots affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of L81.3?
L81.3 maps to the ICD-11 code: EC23.0 (Non-syndromic genetically-determined hypermelanosis or lentiginosis).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.