Radicular dentine dysplasia
Coronal dentine dysplasia
Hypomineralization of enamel of teeth
Goldblatt chondrodysplasia
Dermo-odonto dysplasia
Congenital abnormality of sclera
Osteosclerosis
Suarez Stickler syndrome
Amelogenesis imperfecta, hypomaturation type
Dentinogenesis imperfecta without osteogenesis imperfecta
Amelogenesis imperfecta, nephrocalcinosis and impaired renal concentration
dentinogenesis imperfecta
Anomalous dysplasia of dentine
dentinal dysplasia
Dysplasia, Dentin
Enamel renal syndrome
Dentinogenesis imperfecta, short stature, hearing loss, intellectual disability syndrome
Dermoodonto dysplasia
Dentin Dysplasia
Atypical dentin dysplasia due to SPARC related modular calcium binding 2 deficiency
Amelogenesis imperfecta - hypomaturation - snow capped teeth
Brachyolmia and amelogenesis imperfecta syndrome
Amelogenesis imperfecta - hypoplastic autosomal dominant - smooth
Hypocalcification of teeth
Microdontia
Odontogenesis imperfecta
Dentinogenesis imperfecta (disorder)
Amelogenesis imperfecta - hypoplastic
Congenital enamel hypoplasia
Hyperplastic gingiva
Hyperplasia of gingiva
Hypocalcification of enamel of teeth
Dentinogenesis imperfecta with osteogenesis imperfecta
Amelogenesis imperfecta - hypomaturation - recessive pigmented
Chondrodysplasia, dentinogenesis imperfecta, joint laxity syndrome
Osteogenesis imperfecta with opalescent teeth
Atypical dentin dysplasia due to SMOC2 deficiency
Horner teeth
Amelogenesis Imperfecta
Capdepont teeth
Pronounced occlusal groove
Amelogenesis imperfecta co-occurrent with cone rod dystrophy
Amelogenesis imperfecta (disorder)
Dentin dysplasia (disorder)
Amelogenesis imperfecta, hypoplastic type
Dentin dysplasia type 1 with microdontia and shape anomalies
Osteogenesis imperfecta with blue sclerae AND dentinogenesis imperfecta
Dentin dysplasia, sclerotic bones syndrome
Hypomineralisation of enamel of tooth
Microdontism
Hereditary opalescent dentine
Enamel-renal syndrome
Amelogenesis imperfecta, pigmented hypomaturation type
Shell teeth
Amelogenesis imperfecta - hypocalcified
Hypomineralisation of enamel of teeth
Dentinogenesis imperfecta - Shield's type II
Amelogenesis imperfecta and gingival hyperplasia syndrome
Amelogenesis imperfecta, hypocalcification type
Hypomineralisation of teeth
van de Hoeve syndrome
Trichodysplasia with amelogenesis imperfecta syndrome
Enamel hypomineralisation
Dentine dysplasia
Shell teeth (disorder)
Hereditary opalescent dentin
Hypocalcification of enamel of tooth
Rootless teeth
Platyspondyly amelogenesis imperfecta
Amelogenesis imperfecta - hypomaturation - autosomal dominant - hypoplastic with taurodontism
Verloes Bourguignon syndrome
Goldblatt syndrome
DGI
Amelogenesis imperfecta and nephrocalcinosis
Dentin dysplasia, type I
Dentine dysplasia - Shield's type I
Amelogenesis imperfecta - hypoplastic autosomal dominant - rough
Brachyolmia
Pulpal dysplasia
Dentin dysplasia with sclerotic bone syndrome
Odontochondrodysplasia
Amelogenesis imperfecta, hypomaturation hypoplasia type with taurodontism
Taurodontism
Dentinogenesis imperfecta - Shield's type I
Amelogenesis imperfecta - hypomaturation
Jalili syndrome
Brandywine type of dentinogenesis imperfecta
Dentinogenesis imperfecta - Shield's type III
Deep occlusal groove
Amelogenesis imperfecta, hypoplastic type with microdontia
Dermo odontodysplasia
Dentine dysplasia - Shield's type II
Horner's teeth
Amelogenesis imperfecta - recessive - rough
Osteogenesis imperfecta type IB
Odontogenesis imperfecta (disorder)
Enamel hypomineralization
Hypomineralization of teeth
Dentin dysplasia, type II
Opalescent teeth with osteogenesis imperfecta
Amelogenesis imperfecta - hypoplastic autosomal dominant - local
Autosomal recessive brachyolmia and amelogenesis imperfecta syndrome
Osteogenesis imperfecta type I
Skeletal dysplasia with wormian bone, multiple fractures, dentinogenesis imperfecta syndrome
Hypomineralization of enamel of tooth
Dentin Dysplasias
McGibbon Lubinsky syndrome
Amelogenesis imperfecta - hypomineralization
Dysplasias, Dentin
Hypocalcification of enamel
AI - Amelogenesis imperfecta
Amelogenesis imperfecta - hypomineralisation
Congenital anomaly of sclera

Frequently Asked Questions

What is the ICD-10 code for hereditary disturbances in tooth structure, nec?

The ICD-10-CM code for hereditary disturbances in tooth structure, nec is K00.5. The full clinical description is "Hereditary disturbances in tooth structure, not elsewhere classified". K00.5 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code K00.5 mean?

ICD-10-CM code K00.5 represents “Hereditary disturbances in tooth structure, not elsewhere classified”. It is classified under Chapter 11: Diseases of the Digestive System and is a billable/specific code that can be used on a claim.

Is K00.5 a billable code?

Yes, K00.5 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is K00.5 in?

K00.5 is in Chapter 11: Diseases of the Digestive System (codes K00-K95).

What SNOMED CT codes does K00.5 map to?

K00.5 maps to 46 SNOMED CT concepts: 78494001, 109471001, 109475005, 109472008, 234965004, and 41 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for K00.5?

K00.5 is linked to 6 UMLS Concept Unique Identifiers: C0002452, C0011436, C0011430, C0868847, C0028878, and 1 more. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does K00.5 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like hereditary disturbances in tooth structure, nec affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of K00.5?

K00.5 maps to the ICD-11 code: LA30.Z (Structural developmental anomalies of teeth and periodontal tissues, unspecified).

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.