K00.4
BillableDisturbances in tooth formation
Disturbances in tooth formation
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Aplasia and hypoplasia of cementum
- Dilaceration of tooth
- Enamel hypoplasia (neonatal) (postnatal) (prenatal)
- Regional odontodysplasia
- Turner's tooth
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- •certain conditions originating in the perinatal periodP04-P96
- •certain infectious and parasitic diseasesA00-B99
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
- •embedded and impacted teethK01
- •mottled teethK00.3
Related Codes(9)
K00.0Anodontia
K00.1Supernumerary teeth
K00.2Abnormalities of size and form of teeth
K00.3Mottled teeth
K00.5Hereditary disturbances in tooth structure, NEC
K00.6Disturbances in tooth eruption
K00.7Teething syndrome
K00.8Other disorders of tooth development
K00.9Disorder of tooth development, unspecified
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(291)
SNOMED CT
- XTE syndrome7037003
- Xeroderma, talipes AND enamel defect7037003
- Xeroderma, talipes and enamel defect (XTE) syndrome7037003
- Xeroderma, talipes and enamel defect syndrome7037003
- Enamel hypoplasia of single tooth10078003
- Localised enamel or dentine hypoplasia10078003
- Localized enamel or dentine hypoplasia10078003
- Turner tooth10078003
- Turner's hypoplasia10078003
- Turner's tooth10078003
- Enamel hypoplasia26597004
- Hypocalcification of teeth26748006
- Hypomineralisation of teeth26748006
- Hypomineralization of teeth26748006
- Hypoplasia of cementum35156002
- Dilaceration of tooth35452009
- Hypohidrosis45004005
- Hypohydrosis45004005
- Oligohidrosis45004005
- Ghost teeth66063001
- Odontogenic dysplasia66063001
- Regional odontodysplasia66063001
- Aplasia of cementum80289005
- Secondary dental caries associated with local or systemic factors95253003
- Developmental anomaly of crown and root formation109435002
- Amelocerebrohypohidrotic syndrome109478007
- Epilepsy, dementia and amelogenesis imperfecta109478007
- Epilepsy, mental deterioration and yellow teeth109478007
- Kohlschutter syndrome109478007
- Kohlschutter's syndrome109478007
- Kohlschütter Tönz syndrome109478007
- Generalised enamel hypoplasia of undetermined aetiology109479004
- Generalized enamel hypoplasia of undetermined etiology109479004
- Generalised enamel hypoplasia associated with systemic disease109480001
- Generalized enamel hypoplasia associated with systemic disease109480001
- Generalised enamel hypoplasia associated with radiation therapy109482009
- Generalized enamel hypoplasia associated with radiation therapy109482009
- Generalised enamel hypoplasia associated with ingestion of drugs109483004
- Generalized enamel hypoplasia associated with ingestion of drugs109483004
- Localised enamel hypoplasia of undetermined aetiology109484005
- Localized enamel hypoplasia of undetermined etiology109484005
- Localised enamel hypoplasia associated with localised trauma109485006
- Localized enamel hypoplasia associated with localized trauma109485006
- Localised enamel hypoplasia associated with local infection109486007
- Localized enamel hypoplasia associated with local infection109486007
- Enamel hypomineralisation109487003
- Enamel hypomineralization109487003
- Hypocalcification of enamel109487003
- Hypocalcification of enamel of tooth109487003
- Hypomineralisation of enamel of tooth109487003
- Hypomineralization of enamel of tooth109487003
- Localised enamel hypomineralisation of undetermined aetiology109488008
- Localized enamel hypomineralization of undetermined etiology109488008
- Localised enamel hypomineralisation associated with localised trauma109489000
- Localized enamel hypomineralization associated with localized trauma109489000
- Localised enamel hypomineralisation associated with localised infection109490009
- Localized enamel hypomineralization associated with localized infection109490009
- Generalised enamel hypomineralisation109491008
- Generalized enamel hypomineralization109491008
- Dental caries associated with enamel hypocalcification109564008
- Dental caries associated with enamel hypomineralisation109564008
- Dental caries associated with enamel hypomineralization109564008
- Dental caries associated with enamel hypoplasia109566005
- Dental caries secondary to developmental defects of tooth structure109568006
- Antenatal enamel hypoplasia196278005
- Neonatal enamel hypoplasia196279002
- Vestibular root angulation of tooth234958007
- Hypoplastic enamel-onycholysis-hypohidrosis syndrome400036004
- Witkop-Brearley-Gentry syndrome400036004
- Intellectual disability, congenital heart disease, blepharophimosis, blepharoptosis and hypoplastic teeth412787009
- Mental retardation, congenital heart disease, blepharophimosis, blepharoptosis and hypoplastic teeth412787009
- Ohdo blepharophimosis syndrome412787009
- Angulation of tooth root698005000
- Root angulation of tooth698005000
- Tooth root angulation698005000
- Molar incisor hypomineralisation698053001
- Molar incisor hypomineralization698053001
- Agenesis of enamel699382004
- Enamel agenesis699382004
- Enamel dysplasia699421005
- Hypoplasia of enamel due to congenital syphilis703134008
- Syphilitic hypoplasia of enamel703134008
- Localised enamel hypoplasia707255004
- Localized enamel hypoplasia707255004
- Cementum dysplasia707623008
- Dysplasia of cementum707623008
- Divergence of root of tooth708517006
- Root divergence708517006
- Deafness, enamel hypoplasia, nail defect syndrome721085000
- Heimler syndrome721085000
- PPT (Pfeiffer Palm Teller) syndrome726672000
- Pfeiffer Palm Teller syndrome726672000
- Short stature, unique facies, enamel hypoplasia, progressive joint stiffness, high-pitched voice syndrome726672000
- Hypohidrosis, enamel hypoplasia, palmoplantar keratoderma, intellectual disability syndrome773553003
- Shaheen syndrome773553003
- Blepharophimosis, intellectual disability syndrome788584007
- Hypoplasia of tooth1144341001
- Enamel hypocalcification of primary second molar tooth1258856003
- Enamel hypomineralisation of primary second molar tooth1258856003
- Enamel hypomineralization of primary second molar tooth1258856003
- Hypomineralisation of enamel of deciduous second molar tooth1258856003
- Hypomineralisation of enamel of second primary molar tooth1258856003
- Hypomineralization of enamel of deciduous second molar tooth1258856003
- Hypomineralization of enamel of second primary molar tooth1258856003
- Dilaceration of crown of permanent tooth due to and following dental trauma1258870003
- Hypocalcification of tooth1258914003
- Hypomineralisation of tooth1258914003
- Hypomineralization of tooth1258914003
- Hypocalcification of enamel of teeth1258915002
- Hypomineralisation of enamel of teeth1258915002
- Hypomineralization of enamel of teeth1258915002
- Partial arrest of formation of root of tooth due to and following dental trauma1259169006
- Partial arrest of growth of root of tooth due to and following dental trauma1259169006
- Arrest of formation of root of tooth due to and following dental trauma1259173009
- Arrest of growth of root of tooth due to and following dental trauma1259173009
- Hypomineralisation of enamel of molar tooth1290339005
- Hypomineralization of enamel of molar tooth1290339005
- MH (molar hypomineralisation) of enamel1290339005
- MH (molar hypomineralization) of enamel1290339005
- Molar enamel hypomineralisation1290339005
- Molar enamel hypomineralization1290339005
UMLS
- Aplasia and hypoplasia of cementumC0865859
- Dilaceration of toothC0266048
- Dilaceration of tooth (disorder)C0266048
- Disturbances in tooth formationC3495540
- Dysplasia, OdontogenicC0206554
- Dysplasias, OdontogenicC0206554
- Ghost TeethC0206554
- Ghost ToothC0206554
- Ghost teethC0206554
- OdontodysplasiaC0206554
- OdontodysplasiasC0206554
- Odontogenic DysplasiaC0206554
- Odontogenic DysplasiasC0206554
- Odontogenic dysplasiaC0206554
- Regional odontodysplasiaC0206554
- Regional odontodysplasia (disorder)C0206554
- Shell teethC0206554
- Teeth with dentinal dysplasiaC0206554
- Teeth with thin dentin and large pulp chambersC0206554
- Teeth with type iii dentinogenesis imperfectaC0206554
- Teeth, GhostC0206554
- Tooth, GhostC0206554
- ghost teethC0206554
- odontodysplasiaC0206554
- Enamel hypoplasia (neonatal) (postnatal) (prenatal)C2887515
- Enamel hypoplasia of single toothC0266027
- Localised enamel or dentine hypoplasiaC0266027
- Localized enamel or dentine hypoplasiaC0266027
- Turner toothC0266027
- Turner's hypoplasiaC0266027
- Turner's toothC0266027
- Turner's tooth (disorder)C0266027
Clinical Terms
- Dysplasias, Odontogenic
- Hypomineralization of enamel of teeth
- Regional odontodysplasia (disorder)
- Localised enamel hypomineralisation associated with localised trauma
- Teeth with thin dentin and large pulp chambers
- Aplasia of cementum
- Cementum dysplasia
- Hypoplasia of enamel due to congenital syphilis
- Ghost Teeth
- Localised enamel hypoplasia associated with local infection
- Dental caries associated with enamel hypocalcification
- Divergence of root of tooth
- Epilepsy, mental deterioration and yellow teeth
- Hypomineralization of enamel of second primary molar tooth
- Localised enamel hypoplasia of undetermined aetiology
- Odontogenic dysplasia
- Arrest of formation of root of tooth due to and following dental trauma
- Generalised enamel hypoplasia associated with systemic disease
- Localised enamel hypomineralisation of undetermined aetiology
- Molar incisor hypomineralisation
- Molar enamel hypomineralization
- Dilaceration of tooth (disorder)
- Hypocalcification of teeth
- Hypoplastic enamel-onycholysis-hypohidrosis syndrome
- Generalized enamel hypoplasia associated with systemic disease
- Ghost Tooth
- Kohlschutter syndrome
- Localised enamel hypoplasia associated with localised trauma
- Localized enamel hypomineralization of undetermined etiology
- Hypoplasia of tooth
- Hypocalcification of enamel of teeth
- Localized enamel hypoplasia
- Localized enamel hypomineralization associated with localized infection
- Ohdo blepharophimosis syndrome
- Generalized enamel hypoplasia associated with radiation therapy
- Dysplasia of cementum
- Heimler syndrome
- Localised enamel hypomineralisation associated with localised infection
- Shaheen syndrome
- Partial arrest of growth of root of tooth due to and following dental trauma
- Witkop-Brearley-Gentry syndrome
- Molar enamel hypomineralisation
- Localised enamel or dentine hypoplasia
- Localized enamel hypoplasia of undetermined etiology
- Xeroderma, talipes and enamel defect (XTE) syndrome
- Secondary dental caries associated with local or systemic factors
- Deafness, enamel hypoplasia, nail defect syndrome
- Dental caries associated with enamel hypomineralisation
- Turner's hypoplasia
- Mental retardation, congenital heart disease, blepharophimosis, blepharoptosis and hypoplastic teeth
- Enamel hypomineralization of primary second molar tooth
- Kohlschutter's syndrome
- Generalized enamel hypomineralization
- Localized enamel hypoplasia associated with localized trauma
- Amelocerebrohypohidrotic syndrome
- Hypomineralisation of enamel of tooth
- Dental caries associated with enamel hypomineralization
- Generalized enamel hypoplasia associated with ingestion of drugs
- Hypomineralisation of enamel of molar tooth
- Enamel hypocalcification of primary second molar tooth
- Enamel agenesis
- Generalised enamel hypoplasia of undetermined aetiology
- Generalised enamel hypomineralisation
- Shell teeth
- Hypomineralisation of enamel of teeth
- Tooth, Ghost
- Enamel hypoplasia (neonatal) (postnatal) (prenatal)
- Teeth, Ghost
- Angulation of tooth root
- Dilaceration of tooth
- Hypomineralisation of teeth
- Enamel hypomineralisation
- Intellectual disability, congenital heart disease, blepharophimosis, blepharoptosis and hypoplastic teeth
- Teeth with type iii dentinogenesis imperfecta
- MH (molar hypomineralization) of enamel
- Hypocalcification of enamel of tooth
- Localized enamel hypomineralization associated with localized trauma
- Aplasia and hypoplasia of cementum
- Partial arrest of formation of root of tooth due to and following dental trauma
- Neonatal enamel hypoplasia
- Root angulation of tooth
- Oligohidrosis
- Enamel hypoplasia of single tooth
- Turner's tooth
- Odontogenic Dysplasias
- Pfeiffer Palm Teller syndrome
- Localized enamel or dentine hypoplasia
- Developmental anomaly of crown and root formation
- Agenesis of enamel
- Regional odontodysplasia
- Syphilitic hypoplasia of enamel
- Short stature, unique facies, enamel hypoplasia, progressive joint stiffness, high-pitched voice syndrome
- Teeth with dentinal dysplasia
- Odontodysplasias
- MH (molar hypomineralisation) of enamel
- Turner's tooth (disorder)
- Xeroderma, talipes and enamel defect syndrome
- Blepharophimosis, intellectual disability syndrome
- Hypomineralization of enamel of deciduous second molar tooth
- Turner tooth
- Hypomineralisation of tooth
- Kohlschütter Tönz syndrome
- Hypohydrosis
- Odontodysplasia
- Enamel hypomineralisation of primary second molar tooth
- Enamel hypomineralization
- Molar incisor hypomineralization
- Hypomineralization of tooth
- Hypomineralization of teeth
- Hypomineralization of enamel of molar tooth
- Generalized enamel hypoplasia of undetermined etiology
- Generalised enamel hypoplasia associated with radiation therapy
- Generalised enamel hypoplasia associated with ingestion of drugs
- XTE syndrome
- Hypomineralization of enamel of tooth
- Localized enamel hypoplasia associated with local infection
- Enamel dysplasia
- Hypoplasia of cementum
- Hypohidrosis
- Dysplasia, Odontogenic
- Xeroderma, talipes AND enamel defect
- PPT (Pfeiffer Palm Teller) syndrome
- Root divergence
- Epilepsy, dementia and amelogenesis imperfecta
- Dental caries secondary to developmental defects of tooth structure
- Hypomineralisation of enamel of second primary molar tooth
- Antenatal enamel hypoplasia
- Arrest of growth of root of tooth due to and following dental trauma
- Hypomineralisation of enamel of deciduous second molar tooth
- Enamel hypoplasia
- Vestibular root angulation of tooth
- Hypohidrosis, enamel hypoplasia, palmoplantar keratoderma, intellectual disability syndrome
- Localised enamel hypoplasia
- Dental caries associated with enamel hypoplasia
- Hypocalcification of enamel
- Tooth root angulation
- Dilaceration of crown of permanent tooth due to and following dental trauma
- Hypocalcification of tooth
Frequently Asked Questions
What is the ICD-10 code for disturbances in tooth formation?
The ICD-10-CM code for disturbances in tooth formation is K00.4. The full clinical description is "Disturbances in tooth formation". K00.4 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code K00.4 mean?
ICD-10-CM code K00.4 represents “Disturbances in tooth formation”. It is classified under Chapter 11: Diseases of the Digestive System and is a billable/specific code that can be used on a claim.
Is K00.4 a billable code?
Yes, K00.4 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is K00.4 in?
K00.4 is in Chapter 11: Diseases of the Digestive System (codes K00-K95).
What codes cannot be used with K00.4?
K00.4 has Excludes1 notes indicating codes that cannot be used together with it, including: Hutchinson's teeth and mulberry molars in congenital syphilis (A50.5).
What SNOMED CT codes does K00.4 map to?
K00.4 maps to 52 SNOMED CT concepts: 699382004, 109478007, 698005000, 196278005, 80289005, and 47 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for K00.4?
K00.4 is linked to 6 UMLS Concept Unique Identifiers: C0865859, C0266048, C3495540, C0206554, C2887515, and 1 more. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does K00.4 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like disturbances in tooth formation affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of K00.4?
K00.4 maps to the ICD-11 code: DA07.3 (Disturbances in tooth formation).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.