I42.4
BillableEndocardial fibroelastosis
Endocardial fibroelastosis
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Congenital cardiomyopathy
- Elastomyofibrosis
Includes
Conditions included under this code
- myocardiopathy
Excludes 2
Conditions not included here, but the patient may have both
- •certain conditions originating in the perinatal periodP04-P96
- •certain infectious and parasitic diseasesA00-B99
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations, and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
- •systemic connective tissue disordersM30-M36
- •transient cerebral ischemic attacks and related syndromesG45
- •ischemic cardiomyopathyI25.5
- •peripartum cardiomyopathyO90.3
- •ventricular hypertrophyI51.7
Code First
The underlying condition must be sequenced before this code
Related Codes(9)
I42.0Dilated cardiomyopathy
I42.1Obstructive hypertrophic cardiomyopathy
I42.2Other hypertrophic cardiomyopathy
I42.3Endomyocardial (eosinophilic) disease
I42.5Other restrictive cardiomyopathy
I42.6Alcoholic cardiomyopathy
I42.7Cardiomyopathy due to drug and external agent
I42.8Other cardiomyopathies
I42.9Cardiomyopathy, unspecified
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(66)
SNOMED CT
- Isolated endocardial fibroelastosis8239009
- Primary endocardial fibroelastosis8239009
- Restrictive cardiomyopathy secondary to endocardial fibroelastosis33006007
- EFE - Endocardial fibroelastosis65457005
- Elastomyofibrosis65457005
- Endocardial fibroelastosis65457005
- Endocardial fibroelastosis of right atrium253348002
- Right atrial endocardial fibroelastosis253348002
- Endocardial fibroelastosis of left atrium253359006
- Left atrial endocardial fibroelastosis253359006
- EFE - Primary right ventricular endocardial fibroelastosis253523001
- Primary endocardial fibroelastosis of right ventricle253523001
- Primary right ventricular endocardial fibroelastosis253523001
- EFE - Primary left ventricular endocardial fibroelastosis253543007
- Primary endocardial fibroelastosis of left ventricle253543007
- Primary left ventricular endocardial fibroelastosis253543007
- Secondary restrictive cardiomyopathy415509000
- Cardiomyopathy and renal anomaly syndrome720610008
- HEC (hydrocephalus, endocardial fibroelastosis, cataract) syndrome721015008
- HEC syndrome721015008
- Hydrocephalus with endocardial fibroelastosis and cataract syndrome721015008
- Congenital endocardial fibroelastosis1141882007
- Fibroelastosis cordis1141882007
UMLS
- Congenital cardiomyopathyC1391997
- EFEC0014117
- EFE - Endocardial fibroelastosisC0014117
- ENDOCARDIAL FIBROELASTOSISC0014117
- ElastomyofibrosisC0014117
- Endocardial FibroelastosesC0014117
- Endocardial FibroelastosisC0014117
- Endocardial fibroelastosisC0014117
- Endocardial fibroelastosis (disorder)C0014117
- Endomyocardial FibroelastosisC0014117
- Endomyocardial fibroelastosisC0014117
- Fibroelastoses, EndocardialC0014117
- Fibroelastosis, EndocardialC0014117
- endocardial fibroelastosisC0014117
Clinical Terms
- Secondary restrictive cardiomyopathy
- Left atrial endocardial fibroelastosis
- EFE
- EFE - Endocardial fibroelastosis
- Congenital cardiomyopathy
- Cardiomyopathy and renal anomaly syndrome
- Endomyocardial fibroelastosis
- Congenital endocardial fibroelastosis
- EFE - Primary left ventricular endocardial fibroelastosis
- Endocardial fibroelastosis (disorder)
- HEC syndrome
- Fibroelastosis cordis
- Primary left ventricular endocardial fibroelastosis
- Fibroelastosis, Endocardial
- Restrictive cardiomyopathy secondary to endocardial fibroelastosis
- HEC (hydrocephalus, endocardial fibroelastosis, cataract) syndrome
- Primary endocardial fibroelastosis of right ventricle
- EFE - Primary right ventricular endocardial fibroelastosis
- Endocardial fibroelastosis of left atrium
- Isolated endocardial fibroelastosis
- Right atrial endocardial fibroelastosis
- Elastomyofibrosis
- Primary endocardial fibroelastosis of left ventricle
- Hydrocephalus with endocardial fibroelastosis and cataract syndrome
- Endocardial fibroelastosis of right atrium
- Primary endocardial fibroelastosis
- Endocardial Fibroelastoses
- Fibroelastoses, Endocardial
- Primary right ventricular endocardial fibroelastosis
Frequently Asked Questions
What is the ICD-10 code for endocardial fibroelastosis?
The ICD-10-CM code for endocardial fibroelastosis is I42.4. The full clinical description is "Endocardial fibroelastosis". I42.4 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code I42.4 mean?
ICD-10-CM code I42.4 represents “Endocardial fibroelastosis”. It is classified under Chapter 9: Diseases of the Circulatory System and is a billable/specific code that can be used on a claim.
Is I42.4 a billable code?
Yes, I42.4 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is I42.4 in?
I42.4 is in Chapter 9: Diseases of the Circulatory System (codes I00-I99).
What SNOMED CT codes does I42.4 map to?
I42.4 maps to 11 SNOMED CT concepts: 720610008, 1141882007, 65457005, 253543007, 253523001, and 6 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for I42.4?
I42.4 is linked to 2 UMLS Concept Unique Identifiers: C1391997, C0014117. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does I42.4 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like endocardial fibroelastosis affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of I42.4?
I42.4 maps to the ICD-11 code: BC43.3 (Endocardial fibroelastosis).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.