I42.0
BillableDilated cardiomyopathy
Dilated cardiomyopathy
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Congestive cardiomyopathy
Includes
Conditions included under this code
- myocardiopathy
Excludes 2
Conditions not included here, but the patient may have both
- •certain conditions originating in the perinatal periodP04-P96
- •certain infectious and parasitic diseasesA00-B99
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations, and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
- •systemic connective tissue disordersM30-M36
- •transient cerebral ischemic attacks and related syndromesG45
- •ischemic cardiomyopathyI25.5
- •peripartum cardiomyopathyO90.3
- •ventricular hypertrophyI51.7
Code First
The underlying condition must be sequenced before this code
Related Codes(9)
I42.1Obstructive hypertrophic cardiomyopathy
I42.2Other hypertrophic cardiomyopathy
I42.3Endomyocardial (eosinophilic) disease
I42.4Endocardial fibroelastosis
I42.5Other restrictive cardiomyopathy
I42.6Alcoholic cardiomyopathy
I42.7Cardiomyopathy due to drug and external agent
I42.8Other cardiomyopathies
I42.9Cardiomyopathy, unspecified
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(301)
SNOMED CT
- Dilated cardiomyopathy due to myotonic dystrophy2816000
- Dilated cardiomyopathy secondary to myotonic dystrophy2816000
- Dilated cardiomyopathy due to sarcoidosis6022005
- Dilated cardiomyopathy due to haemochromatosis8209004
- Dilated cardiomyopathy due to hemochromatosis8209004
- Dilated cardiomyopathy secondary to haemochromatosis8209004
- Dilated cardiomyopathy secondary to hemochromatosis8209004
- Dilated cardiomyopathy due to phytanic acid storage disease11104006
- Dilated cardiomyopathy secondary to Refsum disease11104006
- Dilated cardiomyopathy secondary to Refsum's disease11104006
- Dilated cardiomyopathy secondary to phytanic acid storage disease11104006
- Dilated cardiomyopathy caused by radiation12563008
- Secondary dilated cardiomyopathy20529002
- Dilated cardiomyopathy due to rheumatoid arthritis21430002
- Dilated cardiomyopathy due to muscular dystrophy28869005
- Dilated cardiomyopathy secondary to muscular dystrophy28869005
- Dilated cardiomyopathy due to viral myocarditis30496006
- Dilated cardiomyopathy secondary to viral myocarditis30496006
- Dilated cardiomyopathy due to systemic sclerosis35719004
- Familial cardiomyopathy35728003
- Primary familial cardiomyopathy35728003
- Dilated cardiomyopathy due to granuloma39693003
- Dilated cardiomyopathy due to protozoal myocarditis40532006
- Dilated cardiomyopathy due to protozoan myocarditis40532006
- Dilated cardiomyopathy secondary to protozoal myocarditis40532006
- Dilated cardiomyopathy due to fungal myocarditis44630002
- Dilated cardiomyopathy secondary to fungal myocarditis44630002
- Dilated cardiomyopathy due to dermatomyositis46696008
- Dilated cardiomyopathy due to Friedreich ataxia50270004
- Dilated cardiomyopathy due to Friedreich's ataxia50270004
- Familial dilated cardiomyopathy52029003
- Primary familial dilated cardiomyopathy52029003
- Primary idiopathic dilated cardiomyopathy53043001
- Dilated cardiomyopathy due to bacterial myocarditis54830008
- Dilated cardiomyopathy secondary to bacterial myocarditis54830008
- Dilated cardiomyopathy due to amyloidosis58629009
- Dilated cardiomyopathy secondary to amyloidosis58629009
- Dilated cardiomyopathy due to glycogen storage disease58911001
- Dilated cardiomyopathy secondary to glycogen storage disease58911001
- Dilated cardiomyopathy due to familial storage disease60514000
- Dilated cardiomyopathy due to infiltration64749001
- Infiltrative dilated cardiomyopathy64749001
- Dilated cardiomyopathy caused by drug72972005
- Dilated cardiomyopathy secondary to drug72972005
- Drug-induced cardiomyopathy72972005
- Drug-induced specific heart muscle disorder72972005
- Dilated cardiomyopathy due to malignancy74249003
- Dilated cardiomyopathy due to neuromuscular disorder79152002
- Dilated cardiomyopathy due to nutritional deficiency84733009
- Nutritional cardiomyopathy84733009
- Dilated cardiomyopathy due to infection86194008
- Dilated cardiomyopathy due to infectious disease86194008
- Dilated cardiomyopathy due to mucopolysaccharidosis86995005
- Dilated cardiomyopathy due to polyarteritis nodosa91604001
- Dilated cardiomyopathy due to metabolic disorder111285003
- Dilated cardiomyopathy secondary to metabolic disorder111285003
- Metabolic cardiomyopathy111285003
- Primary dilated cardiomyopathy195021004
- Cardiomyopathy due to mucopolysaccharidosis195027000
- Mucopolysaccharidosis cardiomyopathy195027000
- Cardiomyopathy in Friedreich ataxia195030007
- Cardiomyopathy in Friedreich's ataxia195030007
- Cardiomyopathy in myotonic dystrophy195031006
- Congestive obstructive cardiomyopathy233871002
- Congenital woolly hair254231002
- Congenital wooly hair254231002
- Autosomal dominant epidermolysis bullosa simplex398170002
- EBS 1398170002
- CCM - Congestive cardiomyopathy399020009
- COCM - Congestive cardiomyopathy399020009
- Congestive cardiomyopathy399020009
- Congestive dilated cardiomyopathy399020009
- DCM - Dilated cardiomyopathy399020009
- Dilated cardiomyopathy399020009
- Non age related cataract399305009
- Non age-related cataract399305009
- Nonsenile cataract399305009
- Autosomal recessive familial woolly hair403795009
- Autosomal recessive familial wooly hair403795009
- Dilated cardiomyopathy with connective tissue disorder413994008
- Dilated cardiomyopathy due to taurine deficiency413995009
- Dilated cardiomyopathy of ischaemic origin426856002
- Dilated cardiomyopathy of ischemic origin426856002
- Ischaemic congestive cardiomyopathy426856002
- Ischemic congestive cardiomyopathy426856002
- Heart disease caused by ionising radiation430401005
- Heart disease caused by ionizing radiation430401005
- Dilated cardiomyopathy with genetic marker471890009
- Ischaemic congestive cardiomyopathy due to coronary artery disease472100003
- Ischaemic dilated cardiomyopathy due to coronary artery disease472100003
- Ischemic congestive cardiomyopathy due to coronary artery disease472100003
- Ischemic dilated cardiomyopathy due to coronary artery disease472100003
- Cardiovascular abnormality due to infectious myocarditis472811009
- Cardiovascular abnormality due to infective myocarditis472811009
- Secondary nonischemic congestive cardiomyopathy699668009
- DMD-associated dilated cardiomyopathy702424003
- Dilated cardiomyopathy 3B702424003
- Duchenne muscular dystrophy-associated dilated cardiomyopathy702424003
- X-linked dilated cardiomyopathy702424003
- Microcephalus cardiomyopathy syndrome719380003
- Microcephaly cardiomyopathy syndrome719380003
- Winship Viljoen Leary syndrome719380003
- Cardiogenital syndrome719451006
- Dilated cardiomyopathy with hypergonadotropic hypogonadism syndrome719451006
- Malouf syndrome719451006
- Najjar syndrome719451006
- Carvajal syndrome719835006
- Keratoderma with woolly hair type II719835006
- Keratoderma with wooly hair type II719835006
- Woolly hair and palmoplantar keratoderma with dilated cardiomyopathy syndrome719835006
- Wooly hair and palmoplantar keratoderma with dilated cardiomyopathy syndrome719835006
- Cardiomyopathy with cataract and hip spine disease syndrome720609003
- Krasnow Qazi syndrome720609003
- Sensorineural deafness with dilated cardiomyopathy syndrome723993005
- Familial dilated cardiomyopathy with conduction defect due to LMNA mutation766883006
- Familial dilated cardiomyopathy with conduction defect due to lamin A/C mutation766883006
- Cardiomyopathy due to connective tissue disease860837007
- Cardiomyopathy due to storage disease860839005
- Dilated cardiomyopathy due to mitochondrial disease871639003
- Infiltrative cardiomyopathy871646007
- Dilated cardiomyopathy due to carnitine deficiency880014009
- Dilated cardiomyopathy due to lysosomal storage disease880038008
- Dilated cardiomyopathy caused by anthracycline880042006
- Dilated cardiomyopathy caused by anthracycline toxicity880042006
- Dilated cardiomyopathy due to electrolyte imbalance1149109001
- Dilated cardiomyopathy due to parasitic myocarditis1153452008
- Intermediate epidermolysis bullosa simplex with cardiomyopathy1177176009
- EKC (erythrokeratodermia cardiomyopathy) syndrome1179293006
- Erythrokeratodermia cardiomyopathy syndrome1179293006
- Dilated cardiomyopathy due to scleroderma1264404009
- Cardiomyopathy caused by drug16228931000119102
- Cardiomyopathy due to viral infection204981000119101
- Nonischemic congestive cardiomyopathy111000119104
- Toxic cardiomyopathy103331000119103
- Toxic dilated cardiomyopathy165468981000119105
UMLS
- CCM - Congestive cardiomyopathyC0007193
- COCM - Congestive cardiomyopathyC0007193
- Cardiomyopathies, DilatedC0007193
- Cardiomyopathy, DilatedC0007193
- Cardiomyopathy, dilatedC0007193
- Congestive (dilated) cardiomyopathyC0007193
- Congestive cardiomyopathyC0007193
- Congestive cardiomyopathy (disorder)C0007193
- Congestive dilated cardiomyopathyC0007193
- DCMC0007193
- DCM - Dilated cardiomyopathyC0007193
- Dilated CardiomyopathiesC0007193
- Dilated CardiomyopathyC0007193
- Dilated cardiomyopathyC0007193
- Primary dilated cardiomyopathyC0007193
- Primary dilated cardiomyopathy (disorder)C0007193
- Stretched and thinned heart muscleC0007193
- cardiomyopathy congestiveC0007193
- cardiomyopathy dilatedC0007193
- congestive cardiomyopathyC0007193
- dilated cardiomyopathyC0007193
- primary dilated cardiomyopathyC0007193
Clinical Terms
- Congestive dilated cardiomyopathy
- Secondary dilated cardiomyopathy
- Dilated cardiomyopathy due to parasitic myocarditis
- Winship Viljoen Leary syndrome
- Dilated cardiomyopathy 3B
- Intermediate epidermolysis bullosa simplex with cardiomyopathy
- Cardiogenital syndrome
- Toxic dilated cardiomyopathy
- Primary familial cardiomyopathy
- Dilated cardiomyopathy due to muscular dystrophy
- Dilated cardiomyopathy due to phytanic acid storage disease
- Dilated cardiomyopathy due to dermatomyositis
- Mucopolysaccharidosis cardiomyopathy
- Congestive obstructive cardiomyopathy
- Cardiomyopathy due to connective tissue disease
- Dilated cardiomyopathy with hypergonadotropic hypogonadism syndrome
- Congenital wooly hair
- Familial cardiomyopathy
- Dilated cardiomyopathy due to rheumatoid arthritis
- Secondary nonischemic congestive cardiomyopathy
- Dilated cardiomyopathy secondary to phytanic acid storage disease
- Stretched and thinned heart muscle
- COCM - Congestive cardiomyopathy
- Drug-induced cardiomyopathy
- Dilated cardiomyopathy due to protozoan myocarditis
- Autosomal dominant epidermolysis bullosa simplex
- Dilated cardiomyopathy secondary to viral myocarditis
- Infiltrative dilated cardiomyopathy
- Ischaemic dilated cardiomyopathy due to coronary artery disease
- Cardiomyopathy, dilated
- Infiltrative cardiomyopathy
- Dilated cardiomyopathy secondary to drug
- Najjar syndrome
- Dilated cardiomyopathy due to bacterial myocarditis
- Wooly hair and palmoplantar keratoderma with dilated cardiomyopathy syndrome
- Dilated cardiomyopathy secondary to myotonic dystrophy
- Dilated cardiomyopathy due to electrolyte imbalance
- Drug-induced specific heart muscle disorder
- Primary idiopathic dilated cardiomyopathy
- Keratoderma with wooly hair type II
- Non age related cataract
- Congestive cardiomyopathy
- Dilated cardiomyopathy due to fungal myocarditis
- Autosomal recessive familial woolly hair
- Primary dilated cardiomyopathy
- Cardiovascular abnormality due to infective myocarditis
- Dilated cardiomyopathy caused by anthracycline
- Microcephaly cardiomyopathy syndrome
- Dilated cardiomyopathy due to infection
- Woolly hair and palmoplantar keratoderma with dilated cardiomyopathy syndrome
- Heart disease caused by ionising radiation
- Sensorineural deafness with dilated cardiomyopathy syndrome
- Dilated cardiomyopathy secondary to Refsum disease
- Dilated cardiomyopathy due to mucopolysaccharidosis
- Primary dilated cardiomyopathy (disorder)
- Cardiomyopathies, Dilated
- Dilated cardiomyopathy due to myotonic dystrophy
- Familial dilated cardiomyopathy with conduction defect due to LMNA mutation
- Ischemic congestive cardiomyopathy due to coronary artery disease
- Dilated cardiomyopathy due to hemochromatosis
- Autosomal recessive familial wooly hair
- Cardiomyopathy due to viral infection
- Cardiomyopathy in Friedreich ataxia
- Nonischemic congestive cardiomyopathy
- Congenital woolly hair
- cardiomyopathy dilated
- Dilated cardiomyopathy due to protozoal myocarditis
- Ischaemic congestive cardiomyopathy
- Dilated cardiomyopathy due to viral myocarditis
- Dilated cardiomyopathy due to malignancy
- Cardiomyopathy caused by drug
- Dilated cardiomyopathy due to carnitine deficiency
- Dilated cardiomyopathy due to neuromuscular disorder
- Dilated cardiomyopathy due to metabolic disorder
- Dilated cardiomyopathy due to granuloma
- Krasnow Qazi syndrome
- Primary familial dilated cardiomyopathy
- DMD-associated dilated cardiomyopathy
- Dilated cardiomyopathy due to nutritional deficiency
- Heart disease caused by ionizing radiation
- Dilated cardiomyopathy due to lysosomal storage disease
- Dilated Cardiomyopathies
- Nonsenile cataract
- Cardiomyopathy with cataract and hip spine disease syndrome
- Dilated cardiomyopathy due to haemochromatosis
- cardiomyopathy congestive
- Dilated cardiomyopathy due to Friedreich's ataxia
- Duchenne muscular dystrophy-associated dilated cardiomyopathy
- Dilated cardiomyopathy secondary to Refsum's disease
- Dilated cardiomyopathy with genetic marker
- Cardiomyopathy due to mucopolysaccharidosis
- Dilated cardiomyopathy secondary to hemochromatosis
- Dilated cardiomyopathy caused by radiation
- Dilated cardiomyopathy secondary to bacterial myocarditis
- Cardiomyopathy due to storage disease
- Dilated cardiomyopathy caused by anthracycline toxicity
- Congestive cardiomyopathy (disorder)
- Dilated cardiomyopathy secondary to muscular dystrophy
- Dilated cardiomyopathy due to infectious disease
- DCM - Dilated cardiomyopathy
- Cardiovascular abnormality due to infectious myocarditis
- Metabolic cardiomyopathy
- Cardiomyopathy in myotonic dystrophy
- Dilated cardiomyopathy due to sarcoidosis
- Familial dilated cardiomyopathy
- Malouf syndrome
- Carvajal syndrome
- Dilated cardiomyopathy due to Friedreich ataxia
- Dilated cardiomyopathy secondary to glycogen storage disease
- X-linked dilated cardiomyopathy
- EBS 1
- Dilated cardiomyopathy due to systemic sclerosis
- Dilated cardiomyopathy due to mitochondrial disease
- Dilated cardiomyopathy with connective tissue disorder
- Dilated cardiomyopathy due to infiltration
- Ischaemic congestive cardiomyopathy due to coronary artery disease
- Dilated cardiomyopathy due to scleroderma
- Familial dilated cardiomyopathy with conduction defect due to lamin A/C mutation
- Dilated cardiomyopathy due to polyarteritis nodosa
- Dilated cardiomyopathy secondary to fungal myocarditis
- Dilated cardiomyopathy due to amyloidosis
- Microcephalus cardiomyopathy syndrome
- Nutritional cardiomyopathy
- Ischemic congestive cardiomyopathy
- Dilated cardiomyopathy secondary to metabolic disorder
- Dilated cardiomyopathy of ischemic origin
- Dilated cardiomyopathy due to familial storage disease
- Dilated cardiomyopathy caused by drug
- EKC (erythrokeratodermia cardiomyopathy) syndrome
- Toxic cardiomyopathy
- Congestive (dilated) cardiomyopathy
- Erythrokeratodermia cardiomyopathy syndrome
- Dilated cardiomyopathy due to taurine deficiency
- Dilated cardiomyopathy secondary to haemochromatosis
- CCM - Congestive cardiomyopathy
- Dilated cardiomyopathy of ischaemic origin
- Dilated cardiomyopathy due to glycogen storage disease
- Keratoderma with woolly hair type II
- DCM
- Dilated cardiomyopathy secondary to amyloidosis
- Non age-related cataract
- Ischemic dilated cardiomyopathy due to coronary artery disease
- Cardiomyopathy in Friedreich's ataxia
- Dilated cardiomyopathy secondary to protozoal myocarditis
Frequently Asked Questions
What is the ICD-10 code for dilated cardiomyopathy?
The ICD-10-CM code for dilated cardiomyopathy is I42.0. The full clinical description is "Dilated cardiomyopathy". I42.0 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code I42.0 mean?
ICD-10-CM code I42.0 represents “Dilated cardiomyopathy”. It is classified under Chapter 9: Diseases of the Circulatory System and is a billable/specific code that can be used on a claim.
Is I42.0 a billable code?
Yes, I42.0 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is I42.0 in?
I42.0 is in Chapter 9: Diseases of the Circulatory System (codes I00-I99).
What SNOMED CT codes does I42.0 map to?
I42.0 maps to 73 SNOMED CT concepts: 398170002, 403795009, 399020009, 719451006, 16228931000119102, and 68 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for I42.0?
I42.0 is linked to 1 UMLS Concept Unique Identifier: C0007193. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does I42.0 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like dilated cardiomyopathy affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of I42.0?
I42.0 maps to the ICD-11 code: BC43.0Z (Dilated cardiomyopathy, unspecified).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.