I27.0
BillablePrimary pulmonary hypertension
Primary pulmonary hypertension
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Heritable pulmonary arterial hypertension
- Idiopathic pulmonary arterial hypertension
- Primary group 1 pulmonary hypertension
- Primary pulmonary arterial hypertension
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- •certain conditions originating in the perinatal periodP04-P96
- •certain infectious and parasitic diseasesA00-B99
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations, and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
- •systemic connective tissue disordersM30-M36
- •transient cerebral ischemic attacks and related syndromesG45
Related Codes(4)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(98)
SNOMED CT
- Idiopathic pulmonary arteriosclerosis49778009
- Ayerza syndrome78862003
- Ayerza's syndrome78862003
- Cardiopathia nigra78862003
- Cor pulmonale83291003
- Pulmonary heart disease83291003
- Right heart failure due to pulmonary hypertension83291003
- Sporadic primary pulmonary hypertension233943009
- Familial primary pulmonary hypertension233944003
- Finding of pulmonary arterial pressure301141002
- Observation of pulmonary arterial pressure301141002
- Heritable pulmonary arterial hypertension697897003
- Idiopathic pulmonary arterial hypertension697898008
- Heritable pulmonary arterial hypertension due to BMPR2 mutation697899000
- Heritable pulmonary arterial hypertension due to bone morphogenetic protein receptor type II mutation697899000
- Heritable pulmonary arterial hypertension due to ACVRL1 or endoglin mutation697900005
- Heritable pulmonary arterial hypertension due to ALK1 or endoglin mutation697900005
- Heritable pulmonary arterial hypertension due to activin A receptor type II-like kinase 1 or endoglin mutation697900005
- Pulmonary arterial pressure above reference range863928009
- Pulmonary arterial pressure increased863928009
- Right ventricular failure due to disorder of pulmonary circulation1208848007
- Right ventricular failure due to pulmonary vascular disease1208848007
UMLS
- FPPHC0340543
- Familial Primary Pulmonary HypertensionC0340543
- Familial primary pulmonary hypertensionC0340543
- Familial primary pulmonary hypertension (disorder)C0340543
- Familial pulmonary arterial hypertensionC0340543
- HPAHC0340543
- Heritable Pulmonary Arterial HypertensionC0340543
- Heritable pulmonary arterial hypertensionC0340543
- Heritable pulmonary arterial hypertension (disorder)C0340543
- Hypertension, Idiopathic PulmonaryC3203102
- Hypertension, Primary PulmonaryC3203102
- IPAHC3203102
- Idiopathic Pulmonary Arterial HypertensionC3203102
- Idiopathic Pulmonary HypertensionC3203102
- Idiopathic pulmonary arterial hypertensionC3203102
- Idiopathic pulmonary arterial hypertension (disorder)C3203102
- PAHC3203102
- PHTC3203102
- PULMONARY ARTERIAL HYPERTENSIONC3203102
- Primary pulmonary arterial hypertensionC3203102
- Pulmonary Hypertension, IdiopathicC3203102
- Pulmonary Hypertension, PrimaryC3203102
- Idiopathic pulmonary hypertensionC0152171
- PPHC0152171
- PPHTC0152171
- Primary Pulmonary HypertensionC0152171
- Primary pulmonary hypertensionC0152171
- Pulmonary hypertension primaryC0152171
- hypertension primary pulmonaryC0152171
- primary pulmonary hypertensionC0152171
- pulmonary primary hypertensionC0152171
- Primary group 1 pulmonary hypertensionC4509206
Clinical Terms
- Heritable pulmonary arterial hypertension due to ALK1 or endoglin mutation
- Familial primary pulmonary hypertension
- Idiopathic Pulmonary Arterial Hypertension
- PPH
- Right ventricular failure due to disorder of pulmonary circulation
- Heritable pulmonary arterial hypertension due to activin A receptor type II-like kinase 1 or endoglin mutation
- FPPH
- Idiopathic Pulmonary Hypertension
- Pulmonary arterial pressure above reference range
- PHT
- HPAH
- Pulmonary Hypertension, Primary
- Observation of pulmonary arterial pressure
- Primary pulmonary arterial hypertension
- Pulmonary Hypertension, Idiopathic
- pulmonary primary hypertension
- Hypertension, Idiopathic Pulmonary
- Heritable pulmonary arterial hypertension due to BMPR2 mutation
- PAH
- Primary group 1 pulmonary hypertension
- Heritable pulmonary arterial hypertension (disorder)
- hypertension primary pulmonary
- Heritable pulmonary arterial hypertension due to bone morphogenetic protein receptor type II mutation
- Pulmonary heart disease
- Right ventricular failure due to pulmonary vascular disease
- Familial pulmonary arterial hypertension
- Idiopathic pulmonary arterial hypertension (disorder)
- Ayerza's syndrome
- Familial primary pulmonary hypertension (disorder)
- Idiopathic pulmonary arteriosclerosis
- Finding of pulmonary arterial pressure
- Pulmonary hypertension primary
- Heritable pulmonary arterial hypertension due to ACVRL1 or endoglin mutation
- Pulmonary arterial pressure increased
- Sporadic primary pulmonary hypertension
- Ayerza syndrome
- Hypertension, Primary Pulmonary
- Cor pulmonale
- IPAH
- Heritable pulmonary arterial hypertension
- Cardiopathia nigra
- PPHT
- Right heart failure due to pulmonary hypertension
- PULMONARY ARTERIAL HYPERTENSION
Frequently Asked Questions
What is the ICD-10 code for primary pulmonary hypertension?
The ICD-10-CM code for primary pulmonary hypertension is I27.0. The full clinical description is "Primary pulmonary hypertension". I27.0 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code I27.0 mean?
ICD-10-CM code I27.0 represents “Primary pulmonary hypertension”. It is classified under Chapter 9: Diseases of the Circulatory System and is a billable/specific code that can be used on a claim.
Is I27.0 a billable code?
Yes, I27.0 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is I27.0 in?
I27.0 is in Chapter 9: Diseases of the Circulatory System (codes I00-I99).
What codes cannot be used with I27.0?
I27.0 has Excludes1 notes indicating codes that cannot be used together with it, including: persistent pulmonary hypertension of newborn (P29.30); pulmonary hypertension NOS (I27.20); secondary pulmonary arterial hypertension (I27.21); and 1 more.
What SNOMED CT codes does I27.0 map to?
I27.0 maps to 12 SNOMED CT concepts: 78862003, 83291003, 233944003, 301141002, 697897003, and 7 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for I27.0?
I27.0 is linked to 4 UMLS Concept Unique Identifiers: C0340543, C3203102, C0152171, C4509206. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does I27.0 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like primary pulmonary hypertension affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of I27.0?
I27.0 maps to the ICD-11 code: BB01.Z (Pulmonary hypertension, unspecified).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.