I27.21
BillableSecondary pulmonary arterial hypertension
Secondary pulmonary arterial hypertension
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- (Associated) (drug-induced) (toxin-induced) pulmonary arterial hypertension NOS
- (Associated) (drug-induced) (toxin-induced) (secondary) group 1 pulmonary hypertension
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- •certain conditions originating in the perinatal periodP04-P96
- •certain infectious and parasitic diseasesA00-B99
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations, and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
- •systemic connective tissue disordersM30-M36
- •transient cerebral ischemic attacks and related syndromesG45
Code Also
A second code may be required; sequencing depends on circumstances
- associated underlying condition
- associated conditions if applicable, or adverse effects of drugs or toxins, such as:
- •adverse effect of appetite depressantsX5)T50.5
- •congenital heart diseaseQ20-Q28
- •human immunodeficiency virus [HIV] diseaseB20
- •polymyositisM33.2
- •portal hypertensionK76.6
- •rheumatoid arthritisM05
- •schistosomiasisB65
- •Sjögren syndromeM35.0
- •systemic sclerosisM34
Related Codes(5)
Also Known As / Clinical Terms(52)
SNOMED CT
- Secondary pulmonary hypertension88223008
- Solitary pulmonary hypertension233941006
- Small vessel pulmonary hypertension233942004
- Drug-induced pulmonary hypertension233945002
- Pulmonary arterial hypertension caused by drug233945002
- Pulmonary arterial hypertension induced by drug233945002
- Pulmonary hypertension caused by drug233945002
- Pulmonary arterial hypertension caused by toxin697901009
- Pulmonary arterial hypertension induced by toxin697901009
- Associated pulmonary arterial hypertension697902002
- Pulmonary arterial hypertension associated with connective tissue disease697903007
- Pulmonary arterial hypertension associated with HIV infection697904001
- Pulmonary arterial hypertension associated with human immunodeficiency virus infection697904001
- Pulmonary arterial hypertension associated with congenital heart disease697905000
- Pulmonary arterial hypertension associated with congenital systemic-to-pulmonary shunt697906004
- Pulmonary arterial hypertension associated with schistosomiasis697907008
- Pulmonary arterial hypertension associated with chronic haemolytic anaemia697908003
- Pulmonary arterial hypertension associated with chronic hemolytic anemia697908003
- Pulmonary hypertension due to pulmonary capillary haemangiomatosis879814007
- Pulmonary hypertension due to pulmonary capillary hemangiomatosis879814007
- Pulmonary hypertension due to pulmonary veno-occlusive disease879815008
- Pulmonary hypertension due to familial pulmonary capillary haemangiomatosis879816009
- Pulmonary hypertension due to familial pulmonary capillary hemangiomatosis879816009
UMLS
Clinical Terms
- Small vessel pulmonary hypertension
- Pulmonary arterial hypertension associated with connective tissue disease
- Pulmonary arterial hypertension associated with congenital heart disease
- (Associated) (drug-induced) (toxin-induced) pulmonary arterial hypertension NOS
- Pulmonary arterial hypertension associated with congenital systemic-to-pulmonary shunt
- Associated pulmonary arterial hypertension
- Pulmonary hypertension due to familial pulmonary capillary haemangiomatosis
- Pulmonary arterial hypertension caused by drug
- Pulmonary arterial hypertension associated with HIV infection
- Pulmonary hypertension caused by drug
- Pulmonary arterial hypertension associated with chronic haemolytic anaemia
- Pulmonary arterial hypertension associated with schistosomiasis
- Pulmonary arterial hypertension caused by toxin
- Pulmonary arterial hypertension induced by toxin
- Pulmonary hypertension due to pulmonary capillary haemangiomatosis
- Pulmonary hypertension due to pulmonary veno-occlusive disease
- Solitary pulmonary hypertension
- Pulmonary hypertension due to pulmonary capillary hemangiomatosis
- Pulmonary arterial hypertension associated with human immunodeficiency virus infection
- Pulmonary arterial hypertension induced by drug
- Pulmonary hypertension due to familial pulmonary capillary hemangiomatosis
- Secondary pulmonary hypertension
- (Associated) (drug-induced) (toxin-induced) (secondary) group 1 pulmonary hypertension
- Pulmonary arterial hypertension associated with chronic hemolytic anemia
- Drug-induced pulmonary hypertension
Frequently Asked Questions
What is the ICD-10 code for secondary pulmonary arterial hypertension?
The ICD-10-CM code for secondary pulmonary arterial hypertension is I27.21. The full clinical description is "Secondary pulmonary arterial hypertension". I27.21 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code I27.21 mean?
ICD-10-CM code I27.21 represents “Secondary pulmonary arterial hypertension”. It is classified under Chapter 9: Diseases of the Circulatory System and is a billable/specific code that can be used on a claim.
Is I27.21 a billable code?
Yes, I27.21 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is I27.21 in?
I27.21 is in Chapter 9: Diseases of the Circulatory System (codes I00-I99).
What codes cannot be used with I27.21?
I27.21 has Excludes1 notes indicating codes that cannot be used together with it, including: Eisenmenger's syndrome (I27.83).
What SNOMED CT codes does I27.21 map to?
I27.21 maps to 15 SNOMED CT concepts: 697902002, 233945002, 697904001, 697908003, 697905000, and 10 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for I27.21?
I27.21 is linked to 3 UMLS Concept Unique Identifiers: C4509210, C4509209, C3665995. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does I27.21 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like secondary pulmonary arterial hypertension affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of I27.21?
There is no direct ICD-11 mapping available for I27.21 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.