G71.038
BillableOther limb girdle muscular dystrophy
Other limb girdle muscular dystrophy
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- LGMD R9 FKRP-related
- •LGMD collagen 6-relatedR22
- Limb girdle muscular dystrophy due to fukutin related protein dysfunction
- Limb girdle muscular dystrophy type 2I
- Other autosomal recessive limb girdle muscular dystrophy
Excludes 2
Conditions not included here, but the patient may have both
- •certain conditions originating in the perinatal periodP04-P96
- •certain infectious and parasitic diseasesA00-B99
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations, and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
- •arthrogryposis multiplex congenitaQ74.3
- •metabolic disordersE70-E88
- •myositisM60
Related Codes(6)
G71.031Autosomal dominant limb girdle muscular dystrophy
G71.032Autosom recess limb girdle musc dyst d/t calpain-3 dysfnct
G71.033Limb girdle muscular dystrophy due to dysferlin dysfunction
G71.034Limb girdle musc dyst due to sarcoglycan dysfunction
G71.035Limb girdle musc dyst due to anoctamin-5 dysfunction
G71.039Limb girdle muscular dystrophy, unspecified
Also Known As / Clinical Terms(135)
SNOMED CT
- Limb-girdle muscular dystrophy240046001
- Muscular dystrophy with predominantly proximal limb girdle distribution240046001
- X-linked muscular dystrophy with limb girdle distribution240047005
- X-linked limb girdle muscular dystrophy with normal dystrophin240051007
- Autosomal recessive muscular dystrophy with limb girdle distribution240054004
- X-linked muscular dystrophy not predominantly limb girdle240071003
- Alpha-sarcoglycanopathy LGMD2D (limb girdle muscular dystrophy type 2D)715340002
- Autosomal recessive limb girdle muscular dystrophy type 2D715340002
- Autosomal recessive limb girdle muscular dystrophy type 2A715341003
- Calpain-3 deficiency limb girdle muscular dystrophy type 2A715341003
- Leyden-Möbius muscular dystrophy715341003
- Primary calpainopathy715341003
- Autosomal recessive limb girdle muscular dystrophy type 2C718176005
- Limb girdle muscular dystrophy due to gamma-sarcoglycan deficiency718176005
- Autosomal recessive limb girdle muscular dystrophy type 2F718177001
- Limb girdle muscular dystrophy due to delta-sarcoglycan deficiency718177001
- Autosomal recessive limb girdle muscular dystrophy type 2B718179003
- Limb girdle muscular dystrophy due to dysferlin deficiency718179003
- Autosomal recessive limb girdle muscular dystrophy type 2I718180000
- Limb girdle muscular dystrophy due to deficiency of fukutin related protein718180000
- Autosomal recessive limb girdle muscular dystrophy type 2E718850008
- Limb girdle muscular dystrophy due to beta-sarcoglycan deficiency718850008
- Autosomal recessive limb girdle muscular dystrophy type 2G720522001
- Limb girdle muscular dystrophy due to telethonin deficiency720522001
- Autosomal recessive limb girdle muscular dystrophy type 2K720523006
- Limb girdle muscular dystrophy with intellectual disability syndrome720523006
- Autosomal recessive limb girdle muscular dystrophy type 2J725042001
- Limb-girdle muscular dystrophy 2J titin gene mutation725042001
- Autosomal recessive limb girdle muscular dystrophy type 2O725043006
- Limb-girdle muscular dystrophy 2O POMGNT1 (protein o-mannose beta-1,2-n-acetylglucosaminyltransferase) gene mutation725043006
- Limb-girdle muscular dystrophy 2O POMGNT1 gene mutation725043006
- Autosomal recessive limb girdle muscular dystrophy type 2Y725907002
- Autosomal recessive muscular dystrophy due to LAP1B (lamin-associated protein 1B) deficiency725907002
- Autosomal recessive muscular dystrophy due to Torsin-1A-interacting protein 1 deficiency725907002
- Muscular dystrophy with progressive weakness, distal contracture and rigid spine725907002
- Autosomal recessive limb girdle muscular dystrophy type 2P726614009
- Autosomal recessive limb girdle muscular dystrophy type 2Q726615005
- Autosomal recessive limb girdle muscular dystrophy type 2L726616006
- Autosomal recessive limb girdle muscular dystrophy type 2N726617002
- Autosomal recessive limb girdle muscular dystrophy type 2M726618007
- Autosomal recessive limb girdle muscular dystrophy type 2S732929002
- Autosomal recessive limb girdle muscular dystrophy type 2T732930007
- Autosomal recessive limb girdle muscular dystrophy due to ISPD deficiency783554002
- Autosomal recessive limb girdle muscular dystrophy type 2U783554002
- LGMD2U - autosomal recessive limb girdle muscular dystrophy type 2U783554002
- Autosomal recessive limb girdle muscular dystrophy, cardiac arrhythmia syndrome1179295004
- BVES (blood vessel epicardial substance) related limb girdle muscular dystrophy1179295004
- BVES-related limb girdle muscular dystrophy1179295004
- Blood vessel epicardial substance related limb girdle muscular dystrophy1179295004
- Limb girdle muscular dystrophy 2X1179295004
- Autosomal recessive limb girdle muscular dystrophy type 2W1179297007
- LIM zinc finger domain containing 2-related limb girdle muscular dystrophy1179297007
- LIMS2-related limb girdle muscular dystrophy1179297007
- Limb girdle muscular dystrophy type 2W1179297007
- Childhood-onset progressive contractures, limb girdle weakness, muscle dystrophy syndrome1187251009
- Limb girdle muscular dystrophy due to POMK deficiency1234819007
- Limb girdle muscular dystrophy due to protein O-mannose kinase deficiency1234819007
- Laminin alpha-2 related limb girdle muscular dystrophy R231279883006
- Laminin subunit alpha 2-related LGMD (limb girdle muscular dystrophy) R231279883006
- Laminin subunit alpha 2-related late-onset muscular dystrophy1279883006
- Laminin subunit alpha 2-related limb girdle muscular dystrophy R231279883006
- Limb girdle muscular dystrophy type R241279884000
- POMGNT2-related limb girdle muscular dystrophy R241279884000
- POMGNT2-related muscular dystrophy1279884000
- Protein O-mannose beta-1,4-n-acetylglucosaminyltransferase 2-related limb girdle muscular dystrophy R241279884000
UMLS
Clinical Terms
- Limb girdle muscular dystrophy due to delta-sarcoglycan deficiency
- LGMD2U - autosomal recessive limb girdle muscular dystrophy type 2U
- Autosomal recessive limb girdle muscular dystrophy type 2S
- Limb-girdle muscular dystrophy
- Autosomal recessive limb girdle muscular dystrophy type 2N
- Limb girdle muscular dystrophy due to POMK deficiency
- Muscular dystrophy with progressive weakness, distal contracture and rigid spine
- Autosomal recessive limb girdle muscular dystrophy type 2D
- Autosomal recessive limb girdle muscular dystrophy type 2T
- Muscular dystrophy with predominantly proximal limb girdle distribution
- Autosomal recessive limb girdle muscular dystrophy type 2G
- LIM zinc finger domain containing 2-related limb girdle muscular dystrophy
- Autosomal recessive limb girdle muscular dystrophy type 2F
- Childhood-onset progressive contractures, limb girdle weakness, muscle dystrophy syndrome
- Autosomal recessive limb girdle muscular dystrophy type 2J
- X-linked muscular dystrophy with limb girdle distribution
- Limb girdle muscular dystrophy due to dysferlin deficiency
- BVES-related limb girdle muscular dystrophy
- Alpha-sarcoglycanopathy LGMD2D (limb girdle muscular dystrophy type 2D)
- Limb girdle muscular dystrophy due to telethonin deficiency
- POMGNT2-related muscular dystrophy
- Autosomal recessive limb girdle muscular dystrophy type 2Q
- Limb girdle muscular dystrophy due to gamma-sarcoglycan deficiency
- Autosomal recessive limb girdle muscular dystrophy, cardiac arrhythmia syndrome
- Primary calpainopathy
- Autosomal recessive limb girdle muscular dystrophy type 2A
- Autosomal recessive limb girdle muscular dystrophy due to ISPD deficiency
- Autosomal recessive limb girdle muscular dystrophy type 2U
- Leyden-Möbius muscular dystrophy
- Laminin subunit alpha 2-related LGMD (limb girdle muscular dystrophy) R23
- Limb girdle muscular dystrophy type R24
- Limb-girdle muscular dystrophy 2J titin gene mutation
- X-linked limb girdle muscular dystrophy with normal dystrophin
- X-linked muscular dystrophy not predominantly limb girdle
- Autosomal recessive limb girdle muscular dystrophy type 2E
- Autosomal recessive limb girdle muscular dystrophy type 2W
- Limb girdle muscular dystrophy due to beta-sarcoglycan deficiency
- Autosomal recessive limb girdle muscular dystrophy type 2Y
- Autosomal recessive muscular dystrophy with limb girdle distribution
- Autosomal recessive limb girdle muscular dystrophy type 2P
- Autosomal recessive limb girdle muscular dystrophy type 2B
- Laminin alpha-2 related limb girdle muscular dystrophy R23
- Limb girdle muscular dystrophy due to deficiency of fukutin related protein
- Calpain-3 deficiency limb girdle muscular dystrophy type 2A
- Autosomal recessive limb girdle muscular dystrophy type 2M
- Autosomal recessive limb girdle muscular dystrophy type 2O
- Protein O-mannose beta-1,4-n-acetylglucosaminyltransferase 2-related limb girdle muscular dystrophy R24
- POMGNT2-related limb girdle muscular dystrophy R24
- Autosomal recessive limb girdle muscular dystrophy type 2C
- LIMS2-related limb girdle muscular dystrophy
- Limb girdle muscular dystrophy 2X
- Laminin subunit alpha 2-related limb girdle muscular dystrophy R23
- Autosomal recessive limb girdle muscular dystrophy type 2I
- Limb girdle muscular dystrophy type 2W
- Autosomal recessive limb girdle muscular dystrophy type 2K
- Other autosomal recessive limb girdle muscular dystrophy
- LGMD R22 collagen 6-related
- Limb girdle muscular dystrophy due to protein O-mannose kinase deficiency
- Autosomal recessive muscular dystrophy due to LAP1B (lamin-associated protein 1B) deficiency
- Laminin subunit alpha 2-related late-onset muscular dystrophy
- Limb-girdle muscular dystrophy 2O POMGNT1 gene mutation
- Autosomal recessive muscular dystrophy due to Torsin-1A-interacting protein 1 deficiency
- Limb girdle muscular dystrophy with intellectual disability syndrome
- BVES (blood vessel epicardial substance) related limb girdle muscular dystrophy
- Limb-girdle muscular dystrophy 2O POMGNT1 (protein o-mannose beta-1,2-n-acetylglucosaminyltransferase) gene mutation
- Autosomal recessive limb girdle muscular dystrophy type 2L
- Blood vessel epicardial substance related limb girdle muscular dystrophy
Frequently Asked Questions
What is the ICD-10 code for other limb girdle muscular dystrophy?
The ICD-10-CM code for other limb girdle muscular dystrophy is G71.038. The full clinical description is "Other limb girdle muscular dystrophy". G71.038 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code G71.038 mean?
ICD-10-CM code G71.038 represents “Other limb girdle muscular dystrophy”. It is classified under Chapter 6: Diseases of the Nervous System and is a billable/specific code that can be used on a claim.
Is G71.038 a billable code?
Yes, G71.038 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is G71.038 in?
G71.038 is in Chapter 6: Diseases of the Nervous System (codes G00-G99).
What SNOMED CT codes does G71.038 map to?
G71.038 maps to 31 SNOMED CT concepts: 715340002, 783554002, 715341003, 718179003, 718176005, and 26 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for G71.038?
G71.038 is linked to 3 UMLS Concept Unique Identifiers: C5676463, C5676465, C0410161. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does G71.038 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like other limb girdle muscular dystrophy affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of G71.038?
There is no direct ICD-11 mapping available for G71.038 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.