Q74.3
BillableArthrogryposis multiplex congenita
Arthrogryposis multiplex congenita
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(5)
Q74.0Oth congen malform of upper limb(s), inc shoulder girdle
Q74.1Congenital malformation of knee
Q74.2Oth congen malform of lower limb(s), including pelvic girdle
Q74.8Other specified congenital malformations of limb(s)
Q74.9Unspecified congenital malformation of limb(s)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(333)
SNOMED CT
- Inherited disorder of bilirubin metabolism5655007
- Congenital hypoplasia of breast8915006
- Hypoplasia of breast8915006
- Hypoplastic breast8915006
- Congenital webbing of neck11731003
- Neck webbing11731003
- Webbed neck11731003
- Distal arthrogryposis24269006
- Distal arthrogryposis syndrome24269006
- Inherited arthrogryposis28204005
- Akinesia33994004
- HRF - Hepatorenal failure51292008
- Hepatorenal failure51292008
- Hepatorenal syndrome51292008
- Minicore disease55133004
- Multi-core congenital myopathy55133004
- Multi-core disease55133004
- Multi-minicore disease55133004
- Multicore disease55133004
- Multiminicore disease55133004
- Familial arthrogryposis - cholestatic hepatorenal syndrome62216007
- Familial arthrogryposis-cholestatic hepatorenal syndrome62216007
- Lethal familial cholestatic AND pigmentary liver disease62216007
- Anterior horn cell disease85672005
- Arthrogryposis111246005
- AMC - arthrogryposis multiplex congenita205402004
- Arthrogryposis multiplex congenita205402004
- Multiple congenital arthrogryposis205402004
- Congenital muscular dystrophy with arthrogryposis multiplex congenita240061000
- Hypoplasia of nipple268290005
- Rudimentary nipple268290005
- Congenital arthrogryposis caused by teratogen370473000
- MH - malignant hyperpyrexia405501007
- MHS - malignant hyperthermia susceptibility405501007
- Malignant hyperthermia405501007
- Hyperpyrexia409702008
- Arthrogryposis-like syndrome702447002
- Kuskokwim syndrome702447002
- Distal arthrogryposis type 2B715216008
- Freeman-Sheldon syndrome variant715216008
- Sheldon-Hall syndrome715216008
- Arthrogryposis with oculomotor limitation and electroretinal anomaly715217004
- Distal arthrogryposis type 5715217004
- Distal arthrogryposis with ophthalmoplegia715217004
- Oculomelic amyoplasia715217004
- Digitotalar dysmorphism715314008
- Distal arthrogryposis type 1715314008
- Neurogenic arthrogryposis multiplex congenita715316005
- Herva disease715418007
- Lethal congenital contracture syndrome type 1715418007
- Multiple contracture syndrome Finnish type715418007
- Lethal congenital contracture syndrome type 2715419004
- Multiple contracture syndrome Israeli-Bedouin type715419004
- Lethal congenital contracture syndrome type 3715420005
- Lethal arthrogryposis co-occurrent with anterior horn cell disease715565004
- Lethal arthrogryposis with anterior horn cell disease715565004
- Vuopala disease715565004
- Arthrogryposis with severe scoliosis715575001
- Distal arthrogryposis type 4715575001
- Camptodactyly with joint contracture and facial skeletal defect syndrome715986009
- Rozin Hertz Goodman syndrome715986009
- Rozin camptodactyly syndrome715986009
- Holoprosencephaly sequence with hypokinesia and congenital joint contracture syndrome716169009
- Morse Rawnsley Sargent syndrome716169009
- Froster Iskenius Waterson syndrome719398004
- Malignant hyperthermia with arthrogryposis and torticollis syndrome719398004
- Infantile-onset X-linked spinal muscular atrophy719836007
- Spinal muscular atrophy with arthrogryposis719836007
- X-linked distal arthrogryposis multiplex congenita719836007
- X-linked spinal muscular atrophy type 2719836007
- Adducted thumbs and arthrogryposis syndrome Christian type720463009
- ARC (arthrogryposis, renal dysfunction, cholestasis) syndrome720513002
- Arthrogryposis with renal dysfunction and cholestasis syndrome720513002
- Arthrogryposis multiplex congenita and whistling face syndrome720514008
- Illum syndrome720514008
- Arthrogryposis-like hand anomaly and sensorineural deafness syndrome720515009
- Distal arthrogryposis type 6720515009
- Arthrogryposis hyperkeratosis syndrome lethal form726620005
- Johnston Aarons Schelley syndrome726620005
- Autism spectrum disorder, epilepsy, arthrogryposis syndrome733623005
- SLC35A3-CDG - solute carrier family 35 member A3 congenital disorder of glycosylation733623005
- Fetal akinesia, cerebral and retinal haemorrhage syndrome763346009
- Fetal akinesia, cerebral and retinal hemorrhage syndrome763346009
- Foetal akinesia, cerebral and retinal haemorrhage syndrome763346009
- Lethal congenital contracture syndrome type 5763346009
- Autosomal recessive myogenic arthrogryposis multiplex congenita764812008
- SYNE1 (spectrin repeat containing nuclear envelope protein 1) related arthrogryposis multiplex congenita764812008
- SYNE1-related arthrogryposis multiplex congenita764812008
- Hypomyelination neuropathy arthrogryposis syndrome766931003
- DA5D - distal arthrogryposis type 5D773396009
- Distal arthrogryposis type 5 without ophthalmoparesis773396009
- Distal arthrogryposis type 5 without ophthalmoplegia773396009
- Distal arthrogryposis type 5D773396009
- Contractures, webbed neck, micrognathia, hypoplastic nipples syndrome773626008
- Dinno syndrome773626008
- Joint contracture, webbed neck, micrognathia, hypoplastic nipple syndrome773626008
- Pelvic dysplasia, arthrogryposis of lower limbs syndrome783140003
- Ray Peterson Scott syndrome783140003
- Arthrogryposis and ectodermal dysplasia syndrome786039009
- Arthrogryposis, ectodermal dysplasia, other anomalies syndrome786039009
- Stoll Alembik Finck syndrome786039009
- Camptodactyly, cleft palate, clubfoot syndrome897570002
- Distal arthrogryposis type 3897570002
- Distal arthrogryposis type IIA897570002
- Gordon syndrome897570002
- Congenital flexion contracture of foot joint1004071000
- X-linked distal hereditary motor neuropathy1156840002
- Congenital plantar flexion contracture1208482007
- DA10 - distal arthrogryposis type 101208482007
- Distal arthrogryposis type 101208482007
- MYBPC1-related autosomal recessive non-lethal arthrogryposis multiplex congenita syndrome1251451005
- Myosin binding protein C1-related autosomal recessive non-lethal arthrogryposis multiplex congenita syndrome1251451005
- Antenatal multi-minicore disease with arthrogryposis multiplex congenita1259119003
UMLS
- AMC - arthrogryposis multiplex congenitaC5779613
- AMYOPLASIA CONGENC5779613
- ARTHROMYODYSPLASIA CONGENC5779613
- Amyoplasia CongenitaC5779613
- ArthrogryposesC5779613
- Arthrogryposes, Congenital MultipleC5779613
- ArthrogryposisC5779613
- Arthrogryposis Multiplex CongenitaC5779613
- Arthrogryposis Multiplex Congenita (AMC)C5779613
- Arthrogryposis Multiplex CongenitasC5779613
- Arthrogryposis Multiplex Congenitas (AMC)C5779613
- Arthrogryposis multiplexC5779613
- Arthrogryposis multiplex congenitaC5779613
- Arthrogryposis multiplex congenita (AMC)C5779613
- Arthrogryposis multiplex congenita (disorder)C5779613
- Arthrogryposis, Congenital MultipleC5779613
- Arthrogryposis, congenitalC5779613
- Arthromyodysplasia, CongenitalC5779613
- Arthromyodysplasias, CongenitalC5779613
- CONGEN ARTHROMYODYSPLASIAC5779613
- Congenita, Arthrogryposis MultiplexC5779613
- Congenita, Arthrogryposis Multiplex (AMC)C5779613
- Congenital ArthromyodysplasiaC5779613
- Congenital ArthromyodysplasiasC5779613
- Congenital Multiple ArthrogryposesC5779613
- Congenital Multiple ArthrogryposisC5779613
- Congenital contractures, multipleC5779613
- Congenital multiplex arthrogryposisC5779613
- Congenitas, Arthrogryposis MultiplexC5779613
- Congenitas, Arthrogryposis Multiplex (AMC)C5779613
- Fibrous Ankylosis of Multiple JointsC5779613
- Guerin Stern SyndromeC5779613
- Guerin Stern syndromeC5779613
- Guerin-Stern SyndromeC5779613
- Guérin Stern SyndromeC5779613
- Guérin-Stern SyndromeC5779613
- Multiple Arthrogryposes, CongenitalC5779613
- Multiple Arthrogryposis, CongenitalC5779613
- Multiple congenital arthrogryposisC5779613
- Multiple congenital contracturesC5779613
- Multiplex Congenita, ArthrogryposisC5779613
- Multiplex Congenita, Arthrogryposis (AMC)C5779613
- Multiplex Congenitas, ArthrogryposisC5779613
- Multiplex Congenitas, Arthrogryposis (AMC)C5779613
- Myodystrophia Fetalis DeformansC5779613
- Otto SyndromeC5779613
- Rocher Sheldon SyndromeC5779613
- Rocher-Sheldon SyndromeC5779613
- Rossi SyndromeC5779613
- Syndrome, Guerin-SternC5779613
- Syndrome, Guérin-SternC5779613
- Syndrome, OttoC5779613
- Syndrome, Rocher-SheldonC5779613
- Syndrome, RossiC5779613
- arthrogryposesC5779613
- arthrogryposisC5779613
- multiple congenital contractureC5779613
- myodystrophia fetalis deformansC5779613
- syndrome ottoC5779613
Clinical Terms
- Oculomelic amyoplasia
- Arthrogryposis hyperkeratosis syndrome lethal form
- Multiplex Congenitas, Arthrogryposis (AMC)
- Congenital muscular dystrophy with arthrogryposis multiplex congenita
- Multiple Arthrogryposis, Congenital
- Lethal congenital contracture syndrome type 3
- Inherited disorder of bilirubin metabolism
- Antenatal multi-minicore disease with arthrogryposis multiplex congenita
- Minicore disease
- Pelvic dysplasia, arthrogryposis of lower limbs syndrome
- X-linked distal arthrogryposis multiplex congenita
- Arthrogryposis with renal dysfunction and cholestasis syndrome
- Johnston Aarons Schelley syndrome
- Distal arthrogryposis type 6
- MH - malignant hyperpyrexia
- Malignant hyperthermia
- Adducted thumbs and arthrogryposis syndrome Christian type
- Arthrogryposes
- Hyperpyrexia
- AMC - arthrogryposis multiplex congenita
- Arthrogryposis multiplex congenita (disorder)
- AMYOPLASIA CONGEN
- SYNE1-related arthrogryposis multiplex congenita
- Arthrogryposis, ectodermal dysplasia, other anomalies syndrome
- Familial arthrogryposis-cholestatic hepatorenal syndrome
- Congenita, Arthrogryposis Multiplex
- Distal arthrogryposis type 10
- Fetal akinesia, cerebral and retinal hemorrhage syndrome
- Akinesia
- MYBPC1-related autosomal recessive non-lethal arthrogryposis multiplex congenita syndrome
- Multi-core disease
- Multiplex Congenita, Arthrogryposis (AMC)
- Rozin camptodactyly syndrome
- Autism spectrum disorder, epilepsy, arthrogryposis syndrome
- Lethal arthrogryposis co-occurrent with anterior horn cell disease
- Distal arthrogryposis type 5 without ophthalmoparesis
- Dinno syndrome
- Guérin Stern Syndrome
- Freeman-Sheldon syndrome variant
- Congenital webbing of neck
- Infantile-onset X-linked spinal muscular atrophy
- Neck webbing
- Congenital multiplex arthrogryposis
- Autosomal recessive myogenic arthrogryposis multiplex congenita
- Distal arthrogryposis
- Hypomyelination neuropathy arthrogryposis syndrome
- Camptodactyly with joint contracture and facial skeletal defect syndrome
- Congenital flexion contracture of foot joint
- Arthrogryposis Multiplex Congenitas
- Myosin binding protein C1-related autosomal recessive non-lethal arthrogryposis multiplex congenita syndrome
- Multi-minicore disease
- Congenitas, Arthrogryposis Multiplex
- Multiminicore disease
- Arthrogryposis with severe scoliosis
- Congenital Multiple Arthrogryposis
- Distal arthrogryposis syndrome
- Congenital plantar flexion contracture
- Hypoplasia of nipple
- Arthrogryposis
- Ray Peterson Scott syndrome
- Arthrogryposis, congenital
- Holoprosencephaly sequence with hypokinesia and congenital joint contracture syndrome
- Anterior horn cell disease
- Camptodactyly, cleft palate, clubfoot syndrome
- Multiplex Congenitas, Arthrogryposis
- Multiple contracture syndrome Finnish type
- Congenital Arthromyodysplasia
- Herva disease
- multiple congenital contracture
- Hypoplasia of breast
- Rozin Hertz Goodman syndrome
- Arthrogryposis Multiplex Congenita (AMC)
- Congenital Multiple Arthrogryposes
- Multiple Arthrogryposes, Congenital
- Congenitas, Arthrogryposis Multiplex (AMC)
- SYNE1 (spectrin repeat containing nuclear envelope protein 1) related arthrogryposis multiplex congenita
- Multiple contracture syndrome Israeli-Bedouin type
- Hepatorenal failure
- Foetal akinesia, cerebral and retinal haemorrhage syndrome
- Distal arthrogryposis type 5
- Hypoplastic breast
- Rossi Syndrome
- Lethal congenital contracture syndrome type 2
- Distal arthrogryposis type 3
- Neurogenic arthrogryposis multiplex congenita
- Malignant hyperthermia with arthrogryposis and torticollis syndrome
- Lethal congenital contracture syndrome type 1
- HRF - Hepatorenal failure
- myodystrophia fetalis deformans
- Kuskokwim syndrome
- DA5D - distal arthrogryposis type 5D
- Digitotalar dysmorphism
- Arthrogryposis with oculomotor limitation and electroretinal anomaly
- Arthrogryposis and ectodermal dysplasia syndrome
- Gordon syndrome
- Spinal muscular atrophy with arthrogryposis
- Distal arthrogryposis type 5D
- Syndrome, Rossi
- Multiplex Congenita, Arthrogryposis
- Syndrome, Rocher-Sheldon
- ARTHROMYODYSPLASIA CONGEN
- Arthrogryposis-like syndrome
- Syndrome, Guerin-Stern
- Rudimentary nipple
- Multiple congenital arthrogryposis
- Familial arthrogryposis - cholestatic hepatorenal syndrome
- Lethal familial cholestatic AND pigmentary liver disease
- Congenital Arthromyodysplasias
- MHS - malignant hyperthermia susceptibility
- Fetal akinesia, cerebral and retinal haemorrhage syndrome
- Joint contracture, webbed neck, micrognathia, hypoplastic nipple syndrome
- Arthrogryposis multiplex
- Guerin Stern Syndrome
- Syndrome, Otto
- syndrome otto
- Congenita, Arthrogryposis Multiplex (AMC)
- Froster Iskenius Waterson syndrome
- Congenital arthrogryposis caused by teratogen
- Vuopala disease
- Distal arthrogryposis type 4
- Guerin-Stern Syndrome
- X-linked spinal muscular atrophy type 2
- Arthrogryposis Multiplex Congenitas (AMC)
- Distal arthrogryposis type 2B
- Syndrome, Guérin-Stern
- Arthromyodysplasias, Congenital
- Arthrogryposis, Congenital Multiple
- Stoll Alembik Finck syndrome
- CONGEN ARTHROMYODYSPLASIA
- Webbed neck
- Guérin-Stern Syndrome
- Lethal arthrogryposis with anterior horn cell disease
- Amyoplasia Congenita
- Sheldon-Hall syndrome
- Contractures, webbed neck, micrognathia, hypoplastic nipples syndrome
- Distal arthrogryposis type IIA
- X-linked distal hereditary motor neuropathy
- Distal arthrogryposis type 1
- Arthrogryposes, Congenital Multiple
- Fibrous Ankylosis of Multiple Joints
- ARC (arthrogryposis, renal dysfunction, cholestasis) syndrome
- Inherited arthrogryposis
- Morse Rawnsley Sargent syndrome
- Distal arthrogryposis type 5 without ophthalmoplegia
- Arthrogryposis multiplex congenita and whistling face syndrome
- SLC35A3-CDG - solute carrier family 35 member A3 congenital disorder of glycosylation
- Arthrogryposis-like hand anomaly and sensorineural deafness syndrome
- Distal arthrogryposis with ophthalmoplegia
- Rocher-Sheldon Syndrome
- Otto Syndrome
- Congenital contractures, multiple
- Multicore disease
- Arthromyodysplasia, Congenital
- Rocher Sheldon Syndrome
- Illum syndrome
- Multi-core congenital myopathy
- Lethal congenital contracture syndrome type 5
- DA10 - distal arthrogryposis type 10
- Hepatorenal syndrome
- Congenital hypoplasia of breast
- Multiple congenital contractures
Frequently Asked Questions
What is the ICD-10 code for arthrogryposis multiplex congenita?
The ICD-10-CM code for arthrogryposis multiplex congenita is Q74.3. The full clinical description is "Arthrogryposis multiplex congenita". Q74.3 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q74.3 mean?
ICD-10-CM code Q74.3 represents “Arthrogryposis multiplex congenita”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q74.3 a billable code?
Yes, Q74.3 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q74.3 in?
Q74.3 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What codes cannot be used with Q74.3?
Q74.3 has Excludes1 notes indicating codes that cannot be used together with it, including: polydactyly (Q69.-); reduction defect of limb (Q71-Q73); syndactyly (Q70.-).
What SNOMED CT codes does Q74.3 map to?
Q74.3 maps to 50 SNOMED CT concepts: 205402004, 720513002, 720463009, 33994004, 1259119003, and 45 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q74.3?
Q74.3 is linked to 1 UMLS Concept Unique Identifier: C5779613. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q74.3 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like arthrogryposis multiplex congenita affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q74.3?
Q74.3 maps to the ICD-11 code: LD26.41 (Arthrogryposis multiplex congenita).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.