G31.89

Billable

Other specified degenerative diseases of nervous system

Status

Billable / Specific

Chapter

6: Diseases of the Nervous System

Block

G30-G32

Parent Code

G31.8

Coding Notes

Excludes 2

Conditions not included here, but the patient may have both

Use Additional Code

Additional codes that should follow this code

Related Codes(7)

G31.80

Leukodystrophy, unspecified

Billable G31.81

Alpers disease

Billable G31.82

Leigh's disease

Billable G31.83

Neurocognitive disorder with Lewy bodies

Billable G31.84

Mild cognitive impairment of uncertain or unknown etiology

Billable G31.85

Corticobasal degeneration

Billable G31.86

Alexander disease

Billable

Also Known As / Clinical Terms(396)

SNOMED CT

UMLS

Clinical Terms

Axonal neuropathy
Infantile spasms, psychomotor retardation, progressive brain atrophy, basal ganglia disease syndrome
Olivopontocerebellar atrophy co-occurrent with sensorineural hearing loss
Alpha synuclein pathology
Chorea due to Huntington disease-like 2
Corticostriatal-spinal degeneration
Global brain atrophy
OPCA - Olivopontocerebellar atrophy
Spinocerebellar degeneration and corneal dystrophy syndrome
Dejerine-Thomas syndrome
Seitelberger's disease
TUBB4A (tubulin beta 4A class IVa) related leukodystrophy
Chorea with dentatorubropallidoluysian degeneration
Keratosis follicularis, dwarfism, cerebral atrophy syndrome
TUBB4A-related leukodystrophy
Neurodegeneration due to 3-hydroxyisobutyryl-CoA hydrolase deficiency
DYT29 - dystonia 29
Mitochondrial enoyl coenzyme A reductase protein-associated neurodegeneration syndrome
Corneal cerebellar syndrome
Infantile cerebral and cerebellar atrophy with postnatal progressive microcephaly
3-methylglutaconic aciduria type IV with sensorineural deafness, encephalopathy and Leigh-like syndrome
Dentatorubropallidoluysian atrophy
CoPAN - coenzyme A synthase protein associated neurodegeneration
Olivopontocerebellar atrophy
PARK9 - Parkinson disease 9
Alpha synucleinopathy
Chorea due to chronic hepatocerebral degeneration
Apolipoprotein A-I binding protein deficiency
Proliferating cell nuclear antigen-related progressive neurodegenerative photosensitivity syndrome
Type 1 diabetes mellitus, central and peripheral neurodegeneration syndrome
ANOAC (axonal neuropathy, optic atrophy, cognitive deficit) syndrome
MEPAN syndrome
TUBB4A-related hypomyelinating leukodystrophy
3-methylglutaconic aciduria with deafness, encephalopathy, Leigh-like syndrome
NAD(P)HX dehydratase deficiency
Second cranial nerve finding
Diffuse atrophy of cerebrum
Autoimmune degeneration of cerebellum
Cerebellar ataxia associated with another disorder
H-ABC - hypomyelination, atrophy of basal ganglia and cerebellum
Olivocerebellar atrophy
Chorea due to Huntington disease-like 3
Seitelberger disease
Argyrophilic grain disease
Diffuse atrophy of cerebellum
C9ORF72-related Huntington disease phenocopy
Hereditary cerebellar atrophy
HPDL-related Leigh-like encephalopathy
Neuroaxonal dystrophy
Chronic hepatocerebral degeneration
Diffuse atrophy of cerebral structure
Coenzyme A synthase protein associated neurodegeneration
Childhood-onset generalized dystonia, optic atrophy syndrome
3-methylglutaconic aciduria with hearing loss, encephalopathy, Leigh-like syndrome
Atrophy of cerebellar vermis
Kufor Rakeb syndrome
Chloride voltage-gated channel 6-related childhood-onset progressive neurodegeneration, peripheral neuropathy syndrome
Huntington disease-like syndrome disorder
CARKD deficiency
Late cortical cerebellar atrophy
Valine metabolic defect
Hypomyelination with atrophy of basal ganglia and cerebellum syndrome
Progressive neuronal degeneration without liver cirrhosis
Thomas' syndrome
Early-onset neurodegeneration, choreoathetoid movement, microcytic anaemia due to IREB2 mutation
Late infantile and juvenile neuroaxonal dystrophy
INAD - Infantile neuroaxonal dystrophy
Hereditary acantholytic dermatosis
Static encephalopathy of childhood with neurodegeneration in adulthood
Synucleinopathy
Cystic degeneration of brain
Corticostriatal spinal degeneration
X-linked neurodegenerative syndrome Hamel type
Beta-propeller protein-associated neurodegeneration
CLCN6-related childhood-onset progressive neurodegeneration, peripheral neuropathy syndrome
Huntington disease-like 3
Juvenile cerebellar degeneration AND myoclonus
PEHOL (progressive encephalopathy with oedema, hypsarrhythmia, and optic atrophy-like) syndrome
MEGDEL syndrome
Chorea due to hereditary ataxia
Inborn error of amino acid metabolism
Autosomal recessive cerebral atrophy
Huntington disease phenocopy syndrome
Hypomyelinating leukodystrophy with atrophy of basal ganglia and cerebellum
Progressive chorea
Congenital cerebellar cortical atrophy
Huntington disease-like syndrome due to chromosome 9 open reading frame 72 expansions
Early-onset neurodegeneration, choreoathetoid movement, microcytic anemia due to IREB2 mutation
Autosomal recessive childhood-onset dystonia DYT29 type
NDCAMA - neurodegeneration, choreoathetoid movement, microcytic anemia
X-linked neurodegenerative syndrome Bertini type
Autosomal dominant striatal neurodegeneration
Acquired atrophy of cerebellum
Chorea co-occurrent and due to dentatorubropallidoluysian degeneration
Cerebellar deficiency syndrome
Severe neurodegenerative syndrome due to BSCL2 deficiency
PCCA - progressive cerebello-cerebral atrophy
Neurodevelopmental delay, seizures, ophthalmic anomalies, osteopenia, cerebellar atrophy syndrome
Infantile neurodegeneration, progressive spasticity, intellectual disability, white matter lesions syndrome
Progressive encephalopathy with edema, hypsarrhythmia, and optic atrophy-like syndrome
Spastic paraplegia 35
Spastic amaurotic axonal idiocy
Progressive encephalopathy with oedema, hypsarrhythmia, and optic atrophy-like syndrome
Myoclonic epilepsy with choreoathetosis
Chorea co-occurrent and due to Huntington disease-like condition
USP18 deficiency
Neurodegeneration with brain iron accumulation 4
Chorea due to Huntington disease-like 1
HDL1 - Huntington disease-like 1
Tubulin beta 4A class IVa related leukodystrophy
Dentatorubral-pallidoluysian atrophy
Hypomyelinating leucodystrophy with atrophy of basal ganglia and cerebellum
HPDL-related infantile neurodegeneration, progressive spasticity, intellectual disability, white matter lesions syndrome
PEHOL (progressive encephalopathy with edema, hypsarrhythmia, and optic atrophy-like) syndrome
3-Methylglutaconic aciduria type 4
Hereditary degenerative disease of central nervous system
Arteriopathic granular atrophy of cerebral cortex
Early-onset prion disease with prominent psychiatric features
Degeneration of pineal gland
Fatal post-viral neurodegenerative disorder
Huntington disease-like syndrome
Neurodegeneration due to 3-hydroxyisobutyryl coenzyme A hydrolase deficiency
Childhood-onset generalised dystonia, optic atrophy syndrome
Childhood-onset motor and cognitive regression syndrome with extrapyramidal movement disorder
Severe neurodegenerative syndrome with lipodystrophy
Pineal gland degeneration
Diffuse cerebral and cerebellar atrophy, intractable seizures, progressive microcephaly syndrome
Early-onset neurodegeneration, choreoathetoid movement, microcytic anaemia due to iron responsive element binding protein 2 gene mutation
Progressive cerebello-cerebral atrophy
Fatty acid hydroxylase associated neurodegeneration
Atrophy of corticospinal tract
Olivopontocerebellar atrophy and deafness
Progressive neuronal degeneration of childhood
Chorea due to heredodegenerative disorder
Autoimmune cerebellar degeneration
Generalised dystonia
Mitochondrial protein associated neurodegeneration
GPAA1-related biosynthesis defect
Early-onset progressive encephalopathy, hearing loss, pons hypoplasia, brain atrophy syndrome
Congenital microcephaly, severe encephalopathy, progressive cerebral atrophy syndrome
NDCAMA - neurodegeneration, choreoathetoid movement, microcytic anaemia
Severe neurodegenerative syndrome due to BSCL2, seipin lipid droplet biogenesis associated deficiency
Hyperaminoaciduria
PCNA-related progressive neurodegenerative photosensitivity syndrome
Acquired cerebellar atrophy
Neurodegeneration with brain iron accumulation due to COASY mutation
Acute cerebellar syndrome
Juvenile-onset diabetes mellitus, central and peripheral neurodegeneration syndrome
Protein kinase cAMP-dependent type I regulatory subunit beta-related neurodegenerative dementia with intermediate filaments
Huntington disease-like 1
HIBCH-gene related deficiency of 3-hydroxyisobutyryl coenzyme A hydrolase
Dentatorubral-pallidoluysian atrophy (DRPLA)
Methacrylic aciduria
Generalized dystonia
Mitochondrial membrane protein associated neurodegeneration
Choreoathetosis
Diffuse atrophy of cerebellar structure
Disorder of valine metabolism
Infantile neuroaxonal dystrophy
Chorea with Huntington disease-like condition
Der Kaloustian Jarudi Khoury syndrome
Axonal neuropathy, optic atrophy, cognitive deficit syndrome
Lawrence-Cavanagh type
Early-onset progressive neurodegeneration, blindness, ataxia, spasticity syndrome
Huntington disease-like syndrome due to C9ORF72 expansions
NAD(P)HX epimerase deficiency
Early-onset neurodegeneration, choreoathetoid movement, microcytic anemia due to iron responsive element binding protein 2 gene mutation
Combined cerebellar and peripheral ataxia, deafness, diabetes mellitus syndrome
HPDL (4-hydroxyphenylpyruvate dioxygenase like) related infantile neurodegeneration, progressive spasticity, intellectual disability, white matter lesions syndrome
Neurodegeneration with brain iron accumulation type 5
ADSD - autosomal dominant striatal neurodegeneration
Combined cerebellar and peripheral ataxia, hearing loss, diabetes mellitus syndrome
PEHO-like syndrome
BPAN - beta-propeller protein-associated neurodegeneration
Parkinson disease 9
Naito-Oyanagi disease
Infantile-onset axonal motor and sensory neuropathy, optic atrophy, neurodegenerative syndrome
Marie-Foix-Alajouanine syndrome
Sporadic cerebellar degeneration
Cerebellar syndrome
Glycosylphosphatidylinositol anchor attachment 1-related biosynthesis defect
Olivopontocerebellar degeneration
Pineal degeneration
Dentatorubropallidoluysian degeneration
Dysmyelinating leukodystrophy and spastic paraparesis
Early-onset progressive diffuse brain atrophy, microcephaly, muscle weakness, optic atrophy syndrome
Haw river syndrome
COASY protein-associated neurodegeneration
Optic nerve finding
Cerebral degeneration in childhood
Déjérine-Thomas syndrome
Atrophy of pyramidal tract
Ubiquitin specific peptidase 18 deficiency
Asparagine synthetase deficiency
DRPLA - Dentatorubropallidoluysian atrophy
PRKAR1B-related neurodegenerative dementia with intermediate filaments
Global developmental delay, visual anomalies, progressive cerebellar atrophy, truncal hypotonia syndrome

Frequently Asked Questions

What is the ICD-10 code for other specified degenerative diseases of nervous system?

The ICD-10-CM code for other specified degenerative diseases of nervous system is G31.89. The full clinical description is "Other specified degenerative diseases of nervous system". G31.89 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code G31.89 mean?

ICD-10-CM code G31.89 represents “Other specified degenerative diseases of nervous system”. It is classified under Chapter 6: Diseases of the Nervous System and is a billable/specific code that can be used on a claim.

Is G31.89 a billable code?

Yes, G31.89 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is G31.89 in?

G31.89 is in Chapter 6: Diseases of the Nervous System (codes G00-G99).

Are additional codes required with G31.89?

Yes, when using G31.89, also report: code, if applicable, for codes G31.0-G31.83, G31.85-G31.9, to identify:; dementia with anxiety (F02.84, F02.A4, F02.B4, F02.C4); dementia with behavioral disturbance (F02.81-, F02.A1-, F02.B1-, F02.C1-); dementia with mood disturbance (F02.83, F02.A3, F02.B3, F02.C3); dementia with psychotic disturbance (F02.82, F02.A2, F02.B2, F02.C2); dementia without behavioral disturbance (F02.80, F02.A0, F02.B0, F02.C0); mild neurocognitive disorder due to known physiological condition (F06.7-).

What SNOMED CT codes does G31.89 map to?

G31.89 maps to 94 SNOMED CT concepts: 297233004, 711409002, 725392005, 1260129000, 800703961000119100, and 89 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for G31.89?

G31.89 is linked to 1 UMLS Concept Unique Identifier: C0477365. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does G31.89 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like other specified degenerative diseases of nervous system affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of G31.89?

There is no direct ICD-11 mapping available for G31.89 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.