E84.9
BillableCystic fibrosis, unspecified
Cystic fibrosis, unspecified
Coding Notes
Includes
Conditions included under this code
- mucoviscidosis
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Code Also
A second code may be required; sequencing depends on circumstances
Related Codes(3)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(87)
SNOMED CT
- Diabetes mellitus associated with genetic syndrome5969009
- Genetic syndromes of diabetes mellitus5969009
- Diabetes mellitus associated with pancreatic disease51002006
- Pancreatogenic type 3c diabetes mellitus51002006
- Secondary pancreatic diabetes mellitus51002006
- Cystic fibrosis with no meconium ileus81423003
- Cystic fibrosis without meconium ileus81423003
- CF - Cystic fibrosis190905008
- Cystic fibrosis190905008
- Fibrocystic disease190905008
- Mucoviscidosis190905008
- Cystic fibrosis of pancreas235978006
- Fibrocystic disease of pancreas235978006
- Fibrocystic disease of the pancreas235978006
- Mucoviscidosis of pancreas235978006
- Hamartoma of pilosebaceous apparatus400120004
- Diabetes mellitus due to cystic fibrosis427089005
- Follicular hamartoma with alopecia and cystic fibrosis syndrome716088000
- Classical cystic fibrosis762269004
- Atypical cystic fibrosis762270003
- Subclinical cystic fibrosis762271004
- Cystic fibrosis due to heterozygous deltaF508 mutation1296527009
- DeltaF508 heterozygous cystic fibrosis1296527009
- DeltaF508 heterozygous mucoviscidosis1296527009
- Cystic fibrosis due to homozygous deltaF508 mutation1296528004
- DeltaF508 homozygous cystic fibrosis1296528004
- DeltaF508 homozygous mucoviscidosis1296528004
- Early neonatal jaundice due to mucoviscidosis1335876002
UMLS
- CF - Cystic fibrosisC0010674
- CYSTIC FIBROSISC0010674
- Cystic FibrosisC0010674
- Cystic fibrosisC0010674
- Cystic fibrosis (disorder)C0010674
- Cystic fibrosis NOSC0010674
- Cystic fibrosis, unspecifiedC0010674
- Fibrocystic diseaseC0010674
- Fibrosis, CysticC0010674
- MUCOVISCIDOSISC0010674
- MucoviscidosisC0010674
- cystic disorder fibrosisC0010674
- cystic fibrosisC0010674
- cystic fibrosis (CF)C0010674
- cystic fibrosis pancreasC0010674
- disease fibrocysticC0010674
- disease fibrocystic pancreasC0010674
- diseases fibrocysticC0010674
- fibrocystic diseaseC0010674
- fibrocystic disease of pancreasC0010674
- mucoviscidosisC0010674
- pancreas cystic fibrosisC0010674
Clinical Terms
- Follicular hamartoma with alopecia and cystic fibrosis syndrome
- Cystic fibrosis without meconium ileus
- cystic fibrosis pancreas
- Genetic syndromes of diabetes mellitus
- cystic disorder fibrosis
- Cystic fibrosis NOS
- Cystic fibrosis due to homozygous deltaF508 mutation
- Diabetes mellitus due to cystic fibrosis
- mucoviscidosis
- Atypical cystic fibrosis
- Classical cystic fibrosis
- Cystic fibrosis with no meconium ileus
- disease fibrocystic pancreas
- Pancreatogenic type 3c diabetes mellitus
- Fibrocystic disease of pancreas
- cystic fibrosis (CF)
- Cystic fibrosis of pancreas
- Cystic fibrosis (disorder)
- Fibrocystic disease
- CF - Cystic fibrosis
- disease fibrocystic
- Fibrocystic disease of the pancreas
- Secondary pancreatic diabetes mellitus
- DeltaF508 homozygous cystic fibrosis
- Fibrosis, Cystic
- Subclinical cystic fibrosis
- DeltaF508 heterozygous cystic fibrosis
- Hamartoma of pilosebaceous apparatus
- Diabetes mellitus associated with pancreatic disease
- pancreas cystic fibrosis
- DeltaF508 heterozygous mucoviscidosis
- Mucoviscidosis of pancreas
- Early neonatal jaundice due to mucoviscidosis
- DeltaF508 homozygous mucoviscidosis
- Cystic fibrosis due to heterozygous deltaF508 mutation
- diseases fibrocystic
- Diabetes mellitus associated with genetic syndrome
Frequently Asked Questions
What is the ICD-10 code for cystic fibrosis, unspecified?
The ICD-10-CM code for cystic fibrosis, unspecified is E84.9. The full clinical description is "Cystic fibrosis, unspecified". E84.9 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code E84.9 mean?
ICD-10-CM code E84.9 represents “Cystic fibrosis, unspecified”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.
Is E84.9 a billable code?
Yes, E84.9 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E84.9 in?
E84.9 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E84.9?
E84.9 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 3 more.
What SNOMED CT codes does E84.9 map to?
E84.9 maps to 14 SNOMED CT concepts: 762270003, 190905008, 762269004, 1296527009, 1296528004, and 9 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E84.9?
E84.9 is linked to 1 UMLS Concept Unique Identifier: C0010674. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does E84.9 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like cystic fibrosis, unspecified affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of E84.9?
E84.9 maps to the ICD-11 code: CA25.Z (Cystic fibrosis, unspecified).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.