E80.5
BillableCrigler-Najjar syndrome
Crigler-Najjar syndrome
Coding Notes
Includes
Conditions included under this code
- defects of catalase and peroxidase
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Related Codes(7)
E80.0Hereditary erythropoietic porphyria
E80.1Porphyria cutanea tarda
E80.2Other and unspecified porphyria
E80.3Defects of catalase and peroxidase
E80.4Gilbert syndrome
E80.6Other disorders of bilirubin metabolism
E80.7Disorder of bilirubin metabolism, unspecified
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(64)
SNOMED CT
- Inherited disorder of bilirubin metabolism5655007
- Bilirubin UDP glucuronyl transferase deficiency8933000
- Bilirubin glucuronosyltransferase deficiency8933000
- Crigler-Najjar syndrome type I8933000
- Crigler-Najjar syndrome, type I8933000
- Crigler-Najjar type 18933000
- Deficiency of glucuronosyltransferase8933000
- Glucuronyltransferase deficiency8933000
- UDP glucuronyl transferase deficiency8933000
- Crigler-Najjar syndrome28259009
- Arias syndrome68067009
- Crigler-Najjar syndrome type II68067009
- Crigler-Najjar syndrome, type II68067009
- Crigler-Najjar type 268067009
- Neonatal jaundice due to Crigler-Najjar syndrome206454000
UMLS
- CRIGLER-NAJJAR SYNDROMEC5551003
- Crigler Najar SyndromeC5551003
- Crigler Najjar SyndromeC5551003
- Crigler Najjar SyndromesC5551003
- Crigler Najjar syndromeC5551003
- Crigler-Najar SyndromeC5551003
- Crigler-Najjar SyndromeC5551003
- Crigler-Najjar syndromeC5551003
- Crigler-Najjar syndrome (disorder)C5551003
- Familial Nonhemolytic Unconjugated HyperbilirubinemiaC5551003
- Familial nonhemolytic unconjugated hyperbilirubinemiaC5551003
- Hereditary Unconjugated HyperbilirubinemiaC5551003
- Hereditary Unconjugated HyperbilirubinemiasC5551003
- Hereditary unconjugated hyperbilirubinemiaC5551003
- Hyperbilirubinemia, Hereditary UnconjugatedC5551003
- Najjar Syndrome, CriglerC5551003
- Syndrome, Crigler NajjarC5551003
- Unconjugated Hyperbilirubinemia, HereditaryC5551003
- crigler najjar syndromeC5551003
- crigler najjar syndromesC5551003
- crigler-najjar diseaseC5551003
- crigler-najjar syndromeC5551003
Clinical Terms
- Hereditary Unconjugated Hyperbilirubinemia
- Crigler Najar Syndrome
- Bilirubin UDP glucuronyl transferase deficiency
- Deficiency of glucuronosyltransferase
- Inherited disorder of bilirubin metabolism
- Crigler-Najjar syndrome, type I
- Familial Nonhemolytic Unconjugated Hyperbilirubinemia
- Neonatal jaundice due to Crigler-Najjar syndrome
- crigler najjar syndrome
- Hyperbilirubinemia, Hereditary Unconjugated
- UDP glucuronyl transferase deficiency
- Bilirubin glucuronosyltransferase deficiency
- Crigler-Najjar type 1
- Crigler-Najjar syndrome type I
- Crigler-Najjar syndrome, type II
- Crigler-Najar Syndrome
- Arias syndrome
- crigler-najjar disease
- Najjar Syndrome, Crigler
- Crigler-Najjar syndrome type II
- crigler najjar syndromes
- Syndrome, Crigler Najjar
- Glucuronyltransferase deficiency
- Crigler-Najjar syndrome (disorder)
- Hereditary Unconjugated Hyperbilirubinemias
- Unconjugated Hyperbilirubinemia, Hereditary
- Crigler-Najjar type 2
Frequently Asked Questions
What is the ICD-10 code for crigler-najjar syndrome?
The ICD-10-CM code for crigler-najjar syndrome is E80.5. The full clinical description is "Crigler-Najjar syndrome". E80.5 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code E80.5 mean?
ICD-10-CM code E80.5 represents “Crigler-Najjar syndrome”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.
Is E80.5 a billable code?
Yes, E80.5 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E80.5 in?
E80.5 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E80.5?
E80.5 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 3 more.
What SNOMED CT codes does E80.5 map to?
E80.5 maps to 5 SNOMED CT concepts: 68067009, 8933000, 28259009, 5655007, 206454000. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E80.5?
E80.5 is linked to 1 UMLS Concept Unique Identifier: C5551003. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does E80.5 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like crigler-najjar syndrome affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of E80.5?
E80.5 maps to the ICD-11 code: 5C58.00 (Crigler-Najjar syndrome).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.