AutoICD API

E80.21

Billable

Acute intermittent (hepatic) porphyria

Acute intermittent (hepatic) porphyria

Status

Billable / Specific

Block

E70-E88

Parent Code

E80.2

Coding Notes

Includes

Conditions included under this code

  • defects of catalase and peroxidase

Excludes 2

Conditions not included here, but the patient may have both

Related Codes(2)
Also Known As / Clinical Terms(25)

Clinical Terms

  • Pyrroloporphyria
  • PBGD - Porphobilinogen deaminase deficiency
  • Intermittent acute porphyria syndrome
  • Acute intermittent porphyria
  • PBGD deficiency
  • Swedish porphyria
  • Homozygous acute intermittent porphyria
  • Uroporphyrinogen 1 synthase deficiency
  • Intermittent acute porphyria
  • Porphobilinogen deaminase deficiency
  • AIP - Acute intermittent porphyria
  • Acute porphyria
Frequently Asked Questions
What is the ICD-10 code for acute intermittent (hepatic) porphyria?

The ICD-10-CM code for acute intermittent (hepatic) porphyria is E80.21. The full clinical description is "Acute intermittent (hepatic) porphyria". E80.21 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code E80.21 mean?

ICD-10-CM code E80.21 represents “Acute intermittent (hepatic) porphyria”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.

Is E80.21 a billable code?

Yes, E80.21 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is E80.21 in?

E80.21 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).

What codes cannot be used with E80.21?

E80.21 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 3 more.

What SNOMED CT codes does E80.21 map to?

E80.21 maps to 3 SNOMED CT concepts: 234422006, 238054000, 276263005. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for E80.21?

E80.21 is linked to 1 UMLS Concept Unique Identifier: C2874295. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does E80.21 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like acute intermittent (hepatic) porphyria affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of E80.21?

There is no direct ICD-11 mapping available for E80.21 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.