E79.81
BillableAicardi-Goutieres syndrome
Aicardi-Goutieres syndrome
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- •transitory endocrine and metabolic disorders specific to newbornP70-P74
- •androgen insensitivity syndromeE34.5
- •congenital adrenal hyperplasiaE25.0
- •hemolytic anemias attributable to enzyme disordersD55
- •Marfan syndromeQ87.4
- •5-alpha-reductase deficiencyE29.1
- •Ataxia-telangiectasiaQ87.19
- •Bloom's syndromeQ82.8
- •Cockayne's syndromeQ87.19
- •calculus of kidneyN20.0
- •combined immunodeficiency disordersD81
- •Fanconi's anemiaD61.09
- •gout (M1A.-,M10
- •orotaciduric anemiaD53.0
- •progeriaE34.8
- •Werner's syndromeE34.8
- •xeroderma pigmentosumQ82.1
Related Codes(2)
Also Known As / Clinical Terms(28)
UMLS
- AGSC0393591
- Aicardi Goutieres syndromeC0393591
- Aicardi Goutieres syndrome (disorder)C0393591
- Aicardi-Goutieres SyndromeC0393591
- Aicardi-Goutieres syndromeC0393591
- Aicardi-Goutières syndromeC0393591
- Aicardi-Goutières syndromeC0393591
- CREE ENCEPHALITISC0393591
- Cree EncephalitisC0393591
- Cree encephalitisC0393591
- ENCEPHALOPATHY, FAMILIAL INFANTILE, WITH INTRACRANIAL CALCIFICATION AND CHRONIC CEREBROSPINAL FLUID LYMPHOCYTOSISC0393591
- Encephalopathy with Basal Ganglia CalcificationC0393591
- Encephalopathy with basal ganglia calcificationC0393591
- Familial Infantile Encephalopathy with Intracranial Calcification and Chronic Cerebrospinal Fluid LymphocytosisC0393591
- Familial infantile encephalopathy with intracranial calcification and chronic cerebrospinal fluid lymphocytosisC0393591
- PSEUDOTOXOPLASMOSIS SYNDROMEC0393591
- Pseudotoxoplasmosis syndromeC0393591
- aicardi goutieres syndromeC0393591
Clinical Terms
- PSEUDOTOXOPLASMOSIS SYNDROME
- Familial infantile encephalopathy with intracranial calcification and chronic cerebrospinal fluid lymphocytosis
- Cree Encephalitis
- Aicardi Goutieres syndrome
- Aicardi-Goutières syndrome
- Aicardi-Goutières syndrome
- AGS
- ENCEPHALOPATHY, FAMILIAL INFANTILE, WITH INTRACRANIAL CALCIFICATION AND CHRONIC CEREBROSPINAL FLUID LYMPHOCYTOSIS
- Encephalopathy with Basal Ganglia Calcification
- Aicardi Goutieres syndrome (disorder)
Frequently Asked Questions
What is the ICD-10 code for aicardi-goutieres syndrome?
The ICD-10-CM code for aicardi-goutieres syndrome is E79.81. The full clinical description is "Aicardi-Goutieres syndrome". E79.81 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code E79.81 mean?
ICD-10-CM code E79.81 represents “Aicardi-Goutieres syndrome”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.
Is E79.81 a billable code?
Yes, E79.81 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E79.81 in?
E79.81 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E79.81?
E79.81 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 14 more.
What are the UMLS CUIs for E79.81?
E79.81 is linked to 1 UMLS Concept Unique Identifier: C0393591. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does E79.81 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like aicardi-goutieres syndrome affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of E79.81?
There is no direct ICD-11 mapping available for E79.81 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.