E77.0
BillableDefects in post-translational mod of lysosomal enzymes
Defects in post-translational modification of lysosomal enzymes
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Mucolipidosis II [I-cell disease]
- Mucolipidosis III [pseudo-Hurler polydystrophy]
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Related Codes(3)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(31)
SNOMED CT
- Mucolipidosis III65764006
- Pseudo-Hurler disease65764006
- Pseudo-Hurler polydystrophy65764006
- Pseudo-Hurler's disease65764006
- I-cell - Inclusion cell disease70199000
- I-cell disease70199000
- Mucolipidosis II70199000
- Mucolipidosis type II70199000
- N-acetylglucosamine-1-phosphotransferase deficiency70199000
- Mucolipidosis70528007
- Defect in post-translational modification of lysosomal enzymes190948002
UMLS
- Defect in post-translational modification of lysosomal enzymesC0342845
- Defect in post-translational modification of lysosomal enzymes (disorder)C0342845
- Defects in post-translational mod of lysosomal enzymesC0342845
- Defects in post-translational modification of lysosomal enzymesC0342845
- Mucolipidosis II [I-cell disease]C2874285
- Mucolipidosis III [pseudo-Hurler polydystrophy]C2874286
Clinical Terms
- Mucolipidosis
- I-cell disease
- Pseudo-Hurler's disease
- Pseudo-Hurler polydystrophy
- Mucolipidosis III [pseudo-Hurler polydystrophy]
- Mucolipidosis II
- N-acetylglucosamine-1-phosphotransferase deficiency
- Defect in post-translational modification of lysosomal enzymes
- Mucolipidosis II [I-cell disease]
- Mucolipidosis III
- I-cell - Inclusion cell disease
- Defect in post-translational modification of lysosomal enzymes (disorder)
- Pseudo-Hurler disease
- Mucolipidosis type II
Frequently Asked Questions
What is the ICD-10 code for defects in post-translational mod of lysosomal enzymes?
The ICD-10-CM code for defects in post-translational mod of lysosomal enzymes is E77.0. The full clinical description is "Defects in post-translational modification of lysosomal enzymes". E77.0 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code E77.0 mean?
ICD-10-CM code E77.0 represents “Defects in post-translational modification of lysosomal enzymes”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.
Is E77.0 a billable code?
Yes, E77.0 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E77.0 in?
E77.0 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E77.0?
E77.0 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 3 more.
What SNOMED CT codes does E77.0 map to?
E77.0 maps to 4 SNOMED CT concepts: 190948002, 70199000, 70528007, 65764006. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E77.0?
E77.0 is linked to 3 UMLS Concept Unique Identifiers: C0342845, C2874285, C2874286. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does E77.0 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like defects in post-translational mod of lysosomal enzymes affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of E77.0?
E77.0 maps to the ICD-11 code: 5C56.Z (Lysosomal diseases, unspecified).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.