E76.210
BillableMorquio A mucopolysaccharidoses
Morquio A mucopolysaccharidoses
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Classic Morquio syndrome
- Morquio syndrome A
- Mucopolysaccharidosis, type IVA
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Related Codes(2)
Also Known As / Clinical Terms(131)
SNOMED CT
- Atypical chondrodystrophy378007
- Brailsford-Morquio syndrome378007
- Chondro-osteodystrophy378007
- Chondrodystrophia tarda378007
- Familial osseous dystrophy378007
- Familial osteochondrodystrophy378007
- Hereditary enchondral dysostosis378007
- Keratan sulfaturia378007
- Keratan sulphaturia378007
- Morquio disease378007
- Morquio syndrome378007
- Morquio-Brailsford disease378007
- Morquio-Suarez syndrome378007
- Morquio-Ullrich disease378007
- Mucopolysaccharidosis type IV378007
- Mucopolysaccharidosis, MPS-IV378007
- Osteochondrodystrophia deformans378007
- Osteochondrodystrophy378007
- Galactosamine-6-sulfatase deficiency7259005
- Galactosamine-6-sulphatase deficiency7259005
- Galactose-6-sulfatase deficiency7259005
- Galactose-6-sulphatase deficiency7259005
- MPS IV-A-Mucopolysaccharidosis IV-A7259005
- Morquio A syndrome7259005
- Morquio syndrome A7259005
- Morquio's syndrome, classic form7259005
- Mucopolysaccharidosis IV-A7259005
- Mucopolysaccharidosis, MPS-IV-A7259005
- N-acetylgalactosamine-6-sulfatase deficiency7259005
- N-acetylgalactosamine-6-sulphatase deficiency7259005
- Congenital osteodystrophy5731000119108
UMLS
- Classic Morquio syndromeC2874276
- Deficiencies, Galactosamine-6-SulfataseC0086651
- Deficiency of N-acetylgalactosamine-6-sulfataseC0086651
- Deficiency of N-acetylgalactosamine-6-sulfatase (finding)C0086651
- Deficiency of N-acetylgalactosamine-6-sulphataseC0086651
- Deficiency of chondroitinaseC0086651
- Deficiency of chondroitinsulfataseC0086651
- Deficiency of chondroitinsulphataseC0086651
- Deficiency of galactose-6-sulfate sulfataseC0086651
- Deficiency of galactose-6-sulphate sulphataseC0086651
- Deficiency, Galactosamine-6-SulfataseC0086651
- Disease, Morquio AC0086651
- GALACTOSAMINE-6-SULFATASE DEFICIENCYC0086651
- GALNS DEFICIENCYC0086651
- Galactosamine 6 Sulfatase DeficiencyC0086651
- Galactosamine-6-Sulfatase DeficienciesC0086651
- Galactosamine-6-Sulfatase DeficiencyC0086651
- Galactosamine-6-sulfatase deficiencyC0086651
- Galactosamine-6-sulphatase deficiencyC0086651
- Galactose-6-sulfatase deficiencyC0086651
- Galactose-6-sulphatase deficiencyC0086651
- MORQUIO A DISEASEC0086651
- MORQUIO SYNDROME AC0086651
- MPS IV AC0086651
- MPS IV-A-Mucopolysaccharidosis IV-AC0086651
- MPS IVAC0086651
- MPS4AC0086651
- MUCOPOLYSACCHARIDOSIS, TYPE IVAC0086651
- Morquio A DiseaseC0086651
- Morquio A syndromeC0086651
- Morquio Syndrome AC0086651
- Morquio syndrome AC0086651
- Morquio's syndrome, classic formC0086651
- Mucopolysaccharidosis IV-AC0086651
- Mucopolysaccharidosis IV-A (disorder)C0086651
- Mucopolysaccharidosis Type IV AC0086651
- Mucopolysaccharidosis Type IVAC0086651
- Mucopolysaccharidosis, MPS-IV-AC0086651
- Mucopolysaccharidosis, type IVAC0086651
- N-acetylgalactosamine-6-sulfatase deficiencyC0086651
- N-acetylgalactosamine-6-sulphatase deficiencyC0086651
- Syndrome A, MorquioC0086651
- mps ivC0086651
- Morquio A mucopolysaccharidosesC2874277
Clinical Terms
- mps iv
- MPS IV-A-Mucopolysaccharidosis IV-A
- Morquio disease
- Galactose-6-sulphatase deficiency
- N-acetylgalactosamine-6-sulfatase deficiency
- Morquio syndrome A
- Morquio syndrome
- Morquio-Suarez syndrome
- Galactosamine-6-sulphatase deficiency
- Galactosamine-6-sulfatase deficiency
- Osteochondrodystrophy
- Morquio A Disease
- Morquio-Brailsford disease
- Galactosamine-6-Sulfatase Deficiencies
- N-acetylgalactosamine-6-sulphatase deficiency
- Mucopolysaccharidosis IV-A
- Mucopolysaccharidosis, MPS-IV
- Keratan sulfaturia
- Morquio-Ullrich disease
- Deficiencies, Galactosamine-6-Sulfatase
- Atypical chondrodystrophy
- Mucopolysaccharidosis Type IVA
- Brailsford-Morquio syndrome
- Deficiency of galactose-6-sulphate sulphatase
- Familial osteochondrodystrophy
- Mucopolysaccharidosis type IV
- Familial osseous dystrophy
- Chondro-osteodystrophy
- Chondrodystrophia tarda
- Deficiency of N-acetylgalactosamine-6-sulfatase (finding)
- Hereditary enchondral dysostosis
- Mucopolysaccharidosis, MPS-IV-A
- MUCOPOLYSACCHARIDOSIS, TYPE IVA
- Osteochondrodystrophia deformans
- Mucopolysaccharidosis IV-A (disorder)
- Congenital osteodystrophy
- Keratan sulphaturia
- Deficiency of N-acetylgalactosamine-6-sulfatase
- Disease, Morquio A
- Classic Morquio syndrome
- Galactose-6-sulfatase deficiency
- Deficiency of chondroitinase
- Deficiency of galactose-6-sulfate sulfatase
- Syndrome A, Morquio
- MPS4A
- Morquio A syndrome
- GALNS DEFICIENCY
- Mucopolysaccharidosis Type IV A
- Deficiency of chondroitinsulphatase
- Deficiency of N-acetylgalactosamine-6-sulphatase
- Galactosamine 6 Sulfatase Deficiency
- Deficiency of chondroitinsulfatase
- Deficiency, Galactosamine-6-Sulfatase
- MPS IV A
- MPS IVA
- Morquio's syndrome, classic form
Frequently Asked Questions
What is the ICD-10 code for morquio a mucopolysaccharidoses?
The ICD-10-CM code for morquio a mucopolysaccharidoses is E76.210. The full clinical description is "Morquio A mucopolysaccharidoses". E76.210 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code E76.210 mean?
ICD-10-CM code E76.210 represents “Morquio A mucopolysaccharidoses”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.
Is E76.210 a billable code?
Yes, E76.210 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E76.210 in?
E76.210 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E76.210?
E76.210 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 3 more.
What SNOMED CT codes does E76.210 map to?
E76.210 maps to 3 SNOMED CT concepts: 378007, 5731000119108, 7259005. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E76.210?
E76.210 is linked to 3 UMLS Concept Unique Identifiers: C2874276, C0086651, C2874277. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does E76.210 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like morquio a mucopolysaccharidoses affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of E76.210?
There is no direct ICD-11 mapping available for E76.210 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.