E75.23
BillableKrabbe disease
Krabbe disease
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- •transitory endocrine and metabolic disorders specific to newbornP70-P74
- •androgen insensitivity syndromeE34.5
- •congenital adrenal hyperplasiaE25.0
- •hemolytic anemias attributable to enzyme disordersD55
- •Marfan syndromeQ87.4
- •5-alpha-reductase deficiencyE29.1
- •mucolipidosis, types I-IIIE77.0-E77.1
- •Refsum's diseaseG60.1
- •adrenoleukodystrophy [Addison-Schilder]E71.528
Related Codes(8)
Also Known As / Clinical Terms(205)
SNOMED CT
- Adult type Krabbe disease41142009
- Adult-type Krabbe's disease41142009
- Adult-type globoid cell leukodystrophy41142009
- Galactocerebroside beta-galactosidase deficiency - late onset41142009
- Globoid cell leucodystrophy late onset41142009
- Globoid cell leucodystrophy, late-onset41142009
- Globoid cell leukodystrophy, late-onset41142009
- Late onset Krabbe disease41142009
- Diffuse globoid cell cerebral sclerosis192782005
- GCL - Globoid cell leucodystrophy192782005
- Galactocerebroside beta-galactosidase deficiency192782005
- Galactosylceramide beta-galactosidase deficiency192782005
- Globoid cell leucodystrophy192782005
- Krabbe disease192782005
- Krabbe leucodystrophy192782005
- Krabbe's disease192782005
- Krabbe's leukodystrophy192782005
- Galactocerebroside beta-galactosidase deficiency - early onset238030005
- Infantile Krabbe disease238030005
- Atypical Krabbe disease due to saposin A deficiency1296731001
UMLS
- Cell Leukodystrophies, GloboidC0023521
- Cell Leukodystrophy, GloboidC0023521
- Cell Leukoencephalopathies, GloboidC0023521
- Cell Leukoencephalopathy, GloboidC0023521
- Deficiencies, GALCC0023521
- Deficiencies, GalactocerebrosidaseC0023521
- Deficiencies, Galactosylceramide beta-GalactosidaseC0023521
- Deficiency Disease, GalactosylceramidaseC0023521
- Deficiency Disease, Galactosylceramide-beta-GalactosidaseC0023521
- Deficiency Diseases, GalactosylceramidaseC0023521
- Deficiency Diseases, Galactosylceramide-beta-GalactosidaseC0023521
- Deficiency, GALCC0023521
- Deficiency, GalactocerebrosidaseC0023521
- Deficiency, Galactosylceramide beta-GalactosidaseC0023521
- Diffuse Globoid Body SclerosisC0023521
- Diffuse globoid body sclerosisC0023521
- Diffuse globoid cell cerebral sclerosisC0023521
- Disease, Galactosylceramidase DeficiencyC0023521
- Disease, Galactosylceramide-beta-Galactosidase DeficiencyC0023521
- Diseases, Galactosylceramidase DeficiencyC0023521
- Diseases, Galactosylceramide-beta-Galactosidase DeficiencyC0023521
- GALACTOCEREBROSIDASE DEFICIENCYC0023521
- GALACTOSYLCERAMIDASE DEFIC DISC0023521
- GALACTOSYLCERAMIDE BETA-GALACTOSIDASE DEFICIENCYC0023521
- GALC DEFICIENCYC0023521
- GALC DeficienciesC0023521
- GALC DeficiencyC0023521
- GALC deficiencyC0023521
- GCLC0023521
- GCL - Globoid cell leucodystrophyC0023521
- GLDC0023521
- GLOBOID CELL LEUKODYSTROPHYC0023521
- GLOBOID CELL LEUKOENCEPHALOPATHYC0023521
- Galactocerebrosidase DeficienciesC0023521
- Galactocerebrosidase DeficiencyC0023521
- Galactocerebroside beta-galactosidase deficiencyC0023521
- Galactosylceramidase Deficiency DiseaseC0023521
- Galactosylceramidase Deficiency DiseasesC0023521
- Galactosylceramidase deficiency diseaseC0023521
- Galactosylceramide LipidosisC0023521
- Galactosylceramide beta Galactosidase DeficiencyC0023521
- Galactosylceramide beta Galactosidase Deficiency DiseaseC0023521
- Galactosylceramide beta-Galactosidase DeficienciesC0023521
- Galactosylceramide beta-Galactosidase DeficiencyC0023521
- Galactosylceramide beta-galactosidase deficiencyC0023521
- Galactosylceramide beta-galactosidase deficiency (disorder)C0023521
- Galactosylceramide lipidosisC0023521
- Galactosylceramide-beta-Galactosidase Deficiency DiseaseC0023521
- Galactosylceramide-beta-Galactosidase Deficiency DiseasesC0023521
- Galactosylcerebrosidase DeficiencyC0023521
- Galactosylcerebrosidase deficiencyC0023521
- Galactosylsphingosine LipidosisC0023521
- Galactosylsphingosine lipidosisC0023521
- Globoid Body Sclerosis, DiffuseC0023521
- Globoid Cell LeukodystrophiesC0023521
- Globoid Cell LeukodystrophyC0023521
- Globoid Cell LeukoencephalopathiesC0023521
- Globoid Cell LeukoencephalopathyC0023521
- Globoid LeukodystrophiesC0023521
- Globoid LeukodystrophyC0023521
- Globoid cell leucodystrophyC0023521
- KRABBE DISC0023521
- KRABBE DISEASEC0023521
- KRABBES DISC0023521
- KRBC0023521
- Krabbe DiseaseC0023521
- Krabbe LeukodystrophyC0023521
- Krabbe diseaseC0023521
- Krabbe leucodystrophyC0023521
- Krabbe's DiseaseC0023521
- Krabbe's LeukodystrophyC0023521
- Krabbe's diseaseC0023521
- Krabbe's leukodystrophyC0023521
- Krabbes DiseaseC0023521
- Krabbes LeukodystrophyC0023521
- Leukodystrophies, GloboidC0023521
- Leukodystrophies, Globoid CellC0023521
- Leukodystrophy, GloboidC0023521
- Leukodystrophy, Globoid CellC0023521
- Leukodystrophy, KrabbeC0023521
- Leukodystrophy, Krabbe'sC0023521
- Leukoencephalopathies, Globoid CellC0023521
- Leukoencephalopathy, Globoid CellC0023521
- Psychosine LipidosisC0023521
- Psychosine lipidosisC0023521
- beta galactocerebrosidase deficiencyC0023521
- beta-Galactosidase Deficiencies, GalactosylceramideC0023521
- beta-Galactosidase Deficiency, GalactosylceramideC0023521
- disease krabbeC0023521
- disease krabbesC0023521
- diseases krabbeC0023521
- galactosylceramide lipidosisC0023521
- globoid cell leukodystrophyC0023521
- globoid leukodystrophyC0023521
- krabbe diseaseC0023521
- krabbe leukodystrophyC0023521
- krabbe's diseaseC0023521
- krabbe's leukodystrophyC0023521
- krabbes diseaseC0023521
- leukodystrophy krabbeC0023521
Clinical Terms
- Krabbe Leukodystrophy
- Galactosylceramide beta-galactosidase deficiency (disorder)
- Krabbe's disease
- Galactosylceramidase Deficiency Disease
- globoid cell leukodystrophy
- Globoid Leukodystrophies
- Krabbe's Leukodystrophy
- Diffuse globoid cell cerebral sclerosis
- Leukodystrophy, Globoid
- KRABBES DIS
- Cell Leukoencephalopathies, Globoid
- krabbes disease
- Globoid cell leukodystrophy, late-onset
- Adult type Krabbe disease
- KRABBE DIS
- KRB
- diseases krabbe
- globoid leukodystrophy
- Disease, Galactosylceramidase Deficiency
- Deficiency Disease, Galactosylceramidase
- Late onset Krabbe disease
- disease krabbes
- Diseases, Galactosylceramidase Deficiency
- Galactocerebroside beta-galactosidase deficiency - early onset
- Diffuse Globoid Body Sclerosis
- Leukodystrophy, Krabbe's
- Deficiency Diseases, Galactosylceramide-beta-Galactosidase
- leukodystrophy krabbe
- Galactocerebroside beta-galactosidase deficiency
- Krabbes Leukodystrophy
- Globoid Body Sclerosis, Diffuse
- GALACTOSYLCERAMIDE BETA-GALACTOSIDASE DEFICIENCY
- Leukodystrophies, Globoid Cell
- Psychosine lipidosis
- GLOBOID CELL LEUKOENCEPHALOPATHY
- Leukoencephalopathies, Globoid Cell
- GALACTOSYLCERAMIDASE DEFIC DIS
- Adult-type Krabbe's disease
- Globoid cell leucodystrophy, late-onset
- Cell Leukodystrophy, Globoid
- Galactosylceramide-beta-Galactosidase Deficiency Diseases
- Globoid Cell Leukodystrophies
- Cell Leukodystrophies, Globoid
- Deficiency Disease, Galactosylceramide-beta-Galactosidase
- galactosylceramide lipidosis
- Galactosylceramide beta Galactosidase Deficiency Disease
- Galactosylceramide beta-Galactosidase Deficiencies
- Leukodystrophies, Globoid
- Infantile Krabbe disease
- GALACTOCEREBROSIDASE DEFICIENCY
- Leukodystrophy, Krabbe
- Galactosylsphingosine lipidosis
- Deficiencies, Galactocerebrosidase
- GALC Deficiencies
- Deficiency, Galactosylceramide beta-Galactosidase
- Globoid cell leucodystrophy
- Deficiency, Galactocerebrosidase
- Leukodystrophy, Globoid Cell
- GALC deficiency
- beta galactocerebrosidase deficiency
- GLD
- Galactosylceramidase Deficiency Diseases
- Galactosylceramide beta Galactosidase Deficiency
- GCL
- Deficiency, GALC
- Globoid Cell Leukoencephalopathies
- Leukoencephalopathy, Globoid Cell
- Deficiencies, GALC
- beta-Galactosidase Deficiency, Galactosylceramide
- beta-Galactosidase Deficiencies, Galactosylceramide
- Globoid cell leucodystrophy late onset
- Krabbe leucodystrophy
- GCL - Globoid cell leucodystrophy
- Deficiencies, Galactosylceramide beta-Galactosidase
- Deficiency Diseases, Galactosylceramidase
- Galactosylceramide-beta-Galactosidase Deficiency Disease
- Diseases, Galactosylceramide-beta-Galactosidase Deficiency
- Adult-type globoid cell leukodystrophy
- Disease, Galactosylceramide-beta-Galactosidase Deficiency
- Galactocerebrosidase Deficiencies
- Galactosylcerebrosidase Deficiency
- disease krabbe
- Galactocerebroside beta-galactosidase deficiency - late onset
- Atypical Krabbe disease due to saposin A deficiency
- Cell Leukoencephalopathy, Globoid
Frequently Asked Questions
What is the ICD-10 code for krabbe disease?
The ICD-10-CM code for krabbe disease is E75.23. The full clinical description is "Krabbe disease". E75.23 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code E75.23 mean?
ICD-10-CM code E75.23 represents “Krabbe disease”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.
Is E75.23 a billable code?
Yes, E75.23 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E75.23 in?
E75.23 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E75.23?
E75.23 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 6 more.
What SNOMED CT codes does E75.23 map to?
E75.23 maps to 4 SNOMED CT concepts: 41142009, 1296731001, 192782005, 238030005. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E75.23?
E75.23 is linked to 1 UMLS Concept Unique Identifier: C0023521. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does E75.23 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like krabbe disease affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of E75.23?
There is no direct ICD-11 mapping available for E75.23 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.