E74.11
BillableEssential fructosuria
Essential fructosuria
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Fructokinase deficiency
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- •transitory endocrine and metabolic disorders specific to newbornP70-P74
- •androgen insensitivity syndromeE34.5
- •congenital adrenal hyperplasiaE25.0
- •hemolytic anemias attributable to enzyme disordersD55
- •Marfan syndromeQ87.4
- •5-alpha-reductase deficiencyE29.1
- •diabetes mellitusE08-E13
- •hypoglycemia NOSE16.2
- •increased secretion of glucagonE16.3
- •mucopolysaccharidosisE76.0-E76.3
- •muscle phosphofructokinase deficiencyE74.09
Related Codes(3)
Also Known As / Clinical Terms(59)
SNOMED CT
- Fructosuria24338009
- Disorder of fructose metabolism39452003
- Fructose metabolism disorder39452003
- Benign fructosaemia40278002
- Benign fructosemia40278002
- EF - Essential fructosaemia40278002
- EF - Essential fructosemia40278002
- Essential benign fructosuria40278002
- Essential fructosaemia40278002
- Essential fructosemia40278002
- Essential fructosuria40278002
- Fructokinase deficiency40278002
- Hepatic fructokinase deficiency40278002
- Deficiency of ketohexokinase124299001
- Deficiency of fructokinase124300009
UMLS
- Benign fructosaemiaC0268160
- Benign fructosemiaC0268160
- Deficiency of fructokinaseC0268160
- Deficiency of fructokinase (disorder)C0268160
- Deficiency of ketohexokinaseC0268160
- Deficiency of ketohexokinase (disorder)C0268160
- EF - Essential fructosaemiaC0268160
- EF - Essential fructosemiaC0268160
- Essential benign fructosuriaC0268160
- Essential fructosaemiaC0268160
- Essential fructosemiaC0268160
- Essential fructosuriaC0268160
- FRUCTOSURIA, ESSENTIALC0268160
- Fructokinase deficiencyC0268160
- FructosuriaC0268160
- Fructosuria (disorder)C0268160
- HEPATIC FRUCTOKINASE DEFICIENCYC0268160
- Hepatic fructokinase deficiencyC0268160
- Hepatic fructokinase deficiency (disorder)C0268160
- KETOHEXOKINASE DEFICIENCYC0268160
- Ketohexokinase deficiencyC0268160
- disorder fructosuriaC0268160
- fructosuriaC0268160
Clinical Terms
- Deficiency of ketohexokinase (disorder)
- FRUCTOSURIA, ESSENTIAL
- HEPATIC FRUCTOKINASE DEFICIENCY
- Benign fructosaemia
- Hepatic fructokinase deficiency (disorder)
- Ketohexokinase deficiency
- Benign fructosemia
- Deficiency of fructokinase
- Fructosuria
- Fructosuria (disorder)
- Deficiency of fructokinase (disorder)
- Fructokinase deficiency
- disorder fructosuria
- Disorder of fructose metabolism
- Essential fructosaemia
- Deficiency of ketohexokinase
- Fructose metabolism disorder
- Essential benign fructosuria
- Essential fructosemia
- EF - Essential fructosaemia
- EF - Essential fructosemia
Frequently Asked Questions
What is the ICD-10 code for essential fructosuria?
The ICD-10-CM code for essential fructosuria is E74.11. The full clinical description is "Essential fructosuria". E74.11 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code E74.11 mean?
ICD-10-CM code E74.11 represents “Essential fructosuria”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.
Is E74.11 a billable code?
Yes, E74.11 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E74.11 in?
E74.11 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E74.11?
E74.11 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 8 more.
What SNOMED CT codes does E74.11 map to?
E74.11 maps to 5 SNOMED CT concepts: 40278002, 124300009, 124299001, 39452003, 24338009. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E74.11?
E74.11 is linked to 1 UMLS Concept Unique Identifier: C0268160. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does E74.11 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like essential fructosuria affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of E74.11?
There is no direct ICD-11 mapping available for E74.11 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.