E71.39
BillableOther disorders of fatty-acid metabolism
Other disorders of fatty-acid metabolism
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- •transitory endocrine and metabolic disorders specific to newbornP70-P74
- •androgen insensitivity syndromeE34.5
- •congenital adrenal hyperplasiaE25.0
- •hemolytic anemias attributable to enzyme disordersD55
- •Marfan syndromeQ87.4
- •5-alpha-reductase deficiencyE29.1
- •peroxisomal disordersE71.5
- •Refsum's diseaseG60.1
- •Schilder's diseaseG37.0
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(3)
Also Known As / Clinical Terms(101)
SNOMED CT
- Acetyl-CoA carboxylase deficiency4920001
- Deficiency of acetyl-CoA carboxylase4920001
- Deficiency of acetyl-coenzyme A carboxylase4920001
- Deficiency of acetoacetyl-CoA reductase124123000
- Deficiency of acetoacetyl-coenzyme A reductase124123000
- Deficiency of 2-hydroxyglutarate dehydrogenase124149005
- Deficiency of dehydrogenase124226002
- Deficiency of carnitine acetyltransferase124257002
- Deficiency of coenzyme-A transferase124404001
- Beta-hydroxyisobutyryl-coenzyme A deacylase deficiency124427009
- Deficiency of 3-hydroxyisobutyryl CoA hydrolase124427009
- Deficiency of 3-hydroxyisobutyryl coenzyme A hydrolase124427009
- Deficiency of malonyl-CoA decarboxylase124594007
- Deficiency of malonyl-coenzyme A decarboxylase124594007
- Malonyl-CoA decarboxylase deficiency124594007
- Deficiency of 3-hydroxybutyryl-CoA epimerase124660002
- Deficiency of 3-hydroxybutyryl-coenzyme A epimerase124660002
- Deficiency of 1 biotinyl-CoA synthetase124698002
- Deficiency of acetate thiokinase124698002
- Deficiency of acetate-CoA ligase124698002
- Deficiency of acetate-coenzyme A ligase124698002
- Deficiency of acetyl activating enzyme124698002
- Deficiency of acetyl-CoA synthetase124698002
- Deficiency of acyl-CoA synthetase124699005
- Deficiency of fatty acid thiokinase (long chain)124699005
- Deficiency of long-chain-fatty-acid-CoA ligase124699005
- Deficiency of glutarate-CoA ligase124702003
- Deficiency of glutaryl-CoA synthetase124702003
- Carnitine acylcarnitine translocase deficiency238003000
- Deficiency of acetyl-CoA deacylase360709003
- Deficiency of acetyl-coenzyme A deacylase360709003
- Deficiency of acetyl-CoA acylase360721004
- Deficiency of acetyl-coenzyme A acylase360721004
- Deficiency of acetyl-CoA hydrolase360733009
- Deficiency of long-chain fatty-acyl-CoA hydrolase360757009
- Deficiency of long-chain fatty-acyl-coenzyme A hydrolase360757009
- Deficiency of palmitoyl-CoA hydrolase360757009
- Deficiency of palmitoyl-coenzyme A hydrolase360757009
- MLYCD-gene related malonic aciduria361203007
- Malonic aciduria361203007
- Long-chain fatty acid transport deficiency426387005
- Deficiency of 2,4-dienoyl-CoA reductase444944006
- Deficiency of 2,4-dienoyl-coenzyme A reductase444944006
- 3-hydroxy-3-methylglutaryl-CoA synthase deficiency725286002
- 3-hydroxy-3-methylglutaryl-coenzyme A synthase deficiency725286002
- Deficiency of 3-hydroxy-3-methylglutaryl-coenzyme A synthase725286002
- HMG-coenzyme A synthase deficiency725286002
- LCHADD - long chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency726021008
- Long chain 3-hydroxyacyl-CoA dehydrogenase deficiency726021008
- Long chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency726021008
Clinical Terms
- LCHADD - long chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency
- Deficiency of acetoacetyl-CoA reductase
- Deficiency of coenzyme-A transferase
- Deficiency of acyl-CoA synthetase
- Deficiency of long-chain fatty-acyl-CoA hydrolase
- Deficiency of acetyl-CoA hydrolase
- Deficiency of 3-hydroxyisobutyryl CoA hydrolase
- Deficiency of 2,4-dienoyl-CoA reductase
- Malonyl-CoA decarboxylase deficiency
- Acetyl-CoA carboxylase deficiency
- Long chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency
- Deficiency of acetyl-CoA deacylase
- Deficiency of acetyl-CoA acylase
- Deficiency of acetyl-CoA synthetase
- Deficiency of 3-hydroxybutyryl-CoA epimerase
- Deficiency of long-chain fatty-acyl-coenzyme A hydrolase
- Deficiency of long-chain-fatty-acid-CoA ligase
- Long-chain fatty acid transport deficiency
- Deficiency of acetate-CoA ligase
- Deficiency of acetoacetyl-coenzyme A reductase
- Deficiency of acetyl activating enzyme
- Malonic aciduria
- Deficiency of acetate thiokinase
- Deficiency of acetyl-coenzyme A carboxylase
- Deficiency of 3-hydroxy-3-methylglutaryl-coenzyme A synthase
- Deficiency of glutarate-CoA ligase
- 3-hydroxy-3-methylglutaryl-coenzyme A synthase deficiency
- Deficiency of 1 biotinyl-CoA synthetase
- MLYCD-gene related malonic aciduria
- 3-hydroxy-3-methylglutaryl-CoA synthase deficiency
- Deficiency of 3-hydroxyisobutyryl coenzyme A hydrolase
- Deficiency of palmitoyl-CoA hydrolase
- Deficiency of acetyl-CoA carboxylase
- Deficiency of 2-hydroxyglutarate dehydrogenase
- Deficiency of fatty acid thiokinase (long chain)
- HMG-coenzyme A synthase deficiency
- Deficiency of acetyl-coenzyme A acylase
- Deficiency of acetyl-coenzyme A deacylase
- Deficiency of 2,4-dienoyl-coenzyme A reductase
- Beta-hydroxyisobutyryl-coenzyme A deacylase deficiency
- Deficiency of acetate-coenzyme A ligase
- Deficiency of dehydrogenase
- Carnitine acylcarnitine translocase deficiency
- Deficiency of 3-hydroxybutyryl-coenzyme A epimerase
- Deficiency of carnitine acetyltransferase
- Deficiency of malonyl-coenzyme A decarboxylase
- Deficiency of palmitoyl-coenzyme A hydrolase
- Deficiency of glutaryl-CoA synthetase
- Long chain 3-hydroxyacyl-CoA dehydrogenase deficiency
- Deficiency of malonyl-CoA decarboxylase
Frequently Asked Questions
What is the ICD-10 code for other disorders of fatty-acid metabolism?
The ICD-10-CM code for other disorders of fatty-acid metabolism is E71.39. The full clinical description is "Other disorders of fatty-acid metabolism". E71.39 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code E71.39 mean?
ICD-10-CM code E71.39 represents “Other disorders of fatty-acid metabolism”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.
Is E71.39 a billable code?
Yes, E71.39 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E71.39 in?
E71.39 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E71.39?
E71.39 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 6 more.
What SNOMED CT codes does E71.39 map to?
E71.39 maps to 22 SNOMED CT concepts: 725286002, 4920001, 124427009, 238003000, 124698002, and 17 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E71.39?
E71.39 is linked to 1 UMLS Concept Unique Identifier: C2874245. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does E71.39 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like other disorders of fatty-acid metabolism affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of E71.39?
There is no direct ICD-11 mapping available for E71.39 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.