AutoICD API

E71.121

Billable

Propionic acidemia

Propionic acidemia

Status

Billable / Specific

Block

E70-E88

Parent Code

E71.12

Coding Notes

Excludes 1

Codes that cannot be used together with this code (mutual exclusion)

Excludes 2

Conditions not included here, but the patient may have both

Related Codes(2)
E71.120

Methylmalonic acidemia

BillableE71.128

Other disorders of propionate metabolism

Billable
Also Known As / Clinical Terms(122)

SNOMED CT

UMLS

Clinical Terms

  • Propionyl-CoA carboxylase deficiency pccBC complementation group
  • Acidemia, Propionic
  • Deficiency, PCC
  • propionic acidaemia
  • propionyl coA carboxylase deficiency
  • Propionic aciduria
  • Deficiencies, Propionyl-CoA Carboxylase
  • GLYCINEMIA, KETOTIC
  • Ketotic hyperglycinaemia
  • Propionyl-CoA carboxylase deficiency
  • Propionyl-coenzyme A carboxylase deficiency pccBC complementation group
  • Hyperglycinemias, Ketotic
  • Propionic, Acidemia
  • PCCB-gene related propionyl-coenzyme A carboxylase deficiency pccBC complementation group
  • Ketotic Hyperglycinemia
  • Carboxylase Deficiencies, Propionyl-CoA
  • Acidemia Propionics
  • Propionyl-CoA Carboxylase Deficiencies
  • PCC deficiency
  • PCCA-gene related propionyl-coenzyme A carboxylase deficiency pccA complementation group
  • HYPERGLYCINEMIA WITH KETOACIDOSIS AND LEUKOPENIA
  • PCC Deficiencies
  • Propionicacidemias
  • Propionicacidemia
  • ketotic glycinemia
  • Deficiency, Propionyl-CoA Carboxylase
  • Propionyl-coenzyme A carboxylase deficiency pccA complementation group
  • Deficiency of propionyl-CoA carboxylase
  • Ketotic glycinaemia
  • Carboxylase Deficiency, Propionyl-CoA
  • Propionyl-CoA carboxylase deficiency pccA complementation group
  • Propionic acidemia (disorder)
  • Propionic acidemia, type II
  • Propionic acidaemia, type I
  • Hyperglycinaemia with ketosis and leucopenia
  • PROP
  • Propionic acidemia, type I
  • Hyperglycinemia, Ketotic
  • Deficiency of propionyl-coenzyme A carboxylase
  • Hyperglycinemia with ketosis and leukopenia
  • Glycinemias, Ketotic
  • Ketotic Glycinemias
  • Propionic acidaemia, type II
  • Ketotic Hyperglycinemias
  • Propionic Acidemias
  • Acidemia Propionic
  • PCC - Propionyl-CoA carboxylase deficiency
Frequently Asked Questions
What is the ICD-10 code for propionic acidemia?

The ICD-10-CM code for propionic acidemia is E71.121. The full clinical description is "Propionic acidemia". E71.121 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code E71.121 mean?

ICD-10-CM code E71.121 represents “Propionic acidemia”. It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.

Is E71.121 a billable code?

Yes, E71.121 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is E71.121 in?

E71.121 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).

What codes cannot be used with E71.121?

E71.121 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 3 more.

What SNOMED CT codes does E71.121 map to?

E71.121 maps to 6 SNOMED CT concepts: 124718009, 69080001, 303094000, 303095004, 399087009, and 1 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for E71.121?

E71.121 is linked to 1 UMLS Concept Unique Identifier: C0268579. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does E71.121 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like propionic acidemia affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of E71.121?

There is no direct ICD-11 mapping available for E71.121 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.

Automate ICD-10 Coding With AI

Send clinical text to the AutoICD API and get back structured ICD-10 codes with confidence scores. Integrates into any EHR or billing system in minutes.

Try FreeView API Docs

Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.