D83.9
BillableCommon variable immunodeficiency, unspecified
Common variable immunodeficiency, unspecified
Coding Notes
Includes
Conditions included under this code
- defects in the complement system
- immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
- sarcoidosis
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- •autoimmune disease (systemic) NOSM35.9
- •certain conditions originating in the perinatal periodP00-P96
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •human immunodeficiency virus [HIV] diseaseB20
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
Related Codes(4)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(77)
SNOMED CT
- Common variable agammaglobulinaemia23238000
- Common variable agammaglobulinemia23238000
- Late onset immunoglobulin deficiency23238000
- CVID - common variable immunodeficiency191010004
- Common variable immunodeficiency191010004
- Idiopathic immunoglobulin deficiency191010004
- Primary antibody deficiency191010004
- Primary hypogammaglobulinaemia191010004
- Primary hypogammaglobulinemia191010004
- DAVID (deficiency in anterior pituitary function, variable immunodeficiency) syndrome773664005
- Deficiency in anterior pituitary function, variable immunodeficiency syndrome773664005
UMLS
- Acquired AgammaglobulinemiaC0009447
- COMMON VARIABLE IMMUNODEFICC0009447
- CVIDC0009447
- CVID - common variable immunodeficiencyC0009447
- Common Variable HypogammaglobulinemiaC0009447
- Common Variable HypogammaglobulinemiasC0009447
- Common Variable Immune DeficiencyC0009447
- Common Variable ImmunodeficienciesC0009447
- Common Variable ImmunodeficiencyC0009447
- Common variable hypogammaglobulinemiaC0009447
- Common variable immune deficiencyC0009447
- Common variable immunodeficiencyC0009447
- Common variable immunodeficiency (CVID)C0009447
- Common variable immunodeficiency (disorder)C0009447
- Common variable immunodeficiency, unspecifiedC0009447
- Hypogammaglobulinemia, Common VariableC0009447
- Hypogammaglobulinemias, Common VariableC0009447
- IMMUNODEFIC COMMON VARIABLEC0009447
- IMMUNODEFICIENCY, COMMON VARIABLEC0009447
- Idiopathic immunoglobulin deficiencyC0009447
- Immunodeficiencies, Common VariableC0009447
- Immunodeficiency common variableC0009447
- Immunodeficiency, Common VariableC0009447
- Immunodeficiency, common variableC0009447
- Primary acquired hypogammaglobulinaemiaC0009447
- Primary acquired hypogammaglobulinemiaC0009447
- Primary antibody deficiencyC0009447
- Primary hypogammaglobulinaemiaC0009447
- Primary hypogammaglobulinemiaC0009447
- Secondary HypogammaglobulinemiaC0009447
- Variable Hypogammaglobulinemia, CommonC0009447
- Variable Hypogammaglobulinemias, CommonC0009447
- common immunodeficiency variableC0009447
- common variable immunodeficiencyC0009447
- cvidC0009447
Clinical Terms
- COMMON VARIABLE IMMUNODEFIC
- Primary hypogammaglobulinaemia
- Common variable immunodeficiency (disorder)
- Common Variable Immunodeficiencies
- IMMUNODEFICIENCY, COMMON VARIABLE
- Immunodeficiencies, Common Variable
- CVID
- Primary acquired hypogammaglobulinaemia
- Secondary Hypogammaglobulinemia
- Variable Hypogammaglobulinemias, Common
- Common variable agammaglobulinemia
- Common Variable Hypogammaglobulinemia
- Primary acquired hypogammaglobulinemia
- IMMUNODEFIC COMMON VARIABLE
- common immunodeficiency variable
- Hypogammaglobulinemia, Common Variable
- Common variable immune deficiency
- Hypogammaglobulinemias, Common Variable
- Common Variable Hypogammaglobulinemias
- Common variable immunodeficiency (CVID)
- Immunodeficiency common variable
- Common variable agammaglobulinaemia
- Primary hypogammaglobulinemia
- CVID - common variable immunodeficiency
- Late onset immunoglobulin deficiency
- DAVID (deficiency in anterior pituitary function, variable immunodeficiency) syndrome
- Idiopathic immunoglobulin deficiency
- Acquired Agammaglobulinemia
- Variable Hypogammaglobulinemia, Common
- Deficiency in anterior pituitary function, variable immunodeficiency syndrome
- Primary antibody deficiency
Frequently Asked Questions
What is the ICD-10 code for common variable immunodeficiency, unspecified?
The ICD-10-CM code for common variable immunodeficiency, unspecified is D83.9. The full clinical description is "Common variable immunodeficiency, unspecified". D83.9 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code D83.9 mean?
ICD-10-CM code D83.9 represents “Common variable immunodeficiency, unspecified”. It is classified under Chapter 3: Diseases of the Blood and Blood-Forming Organs and is a billable/specific code that can be used on a claim.
Is D83.9 a billable code?
Yes, D83.9 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is D83.9 in?
D83.9 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).
What codes cannot be used with D83.9?
D83.9 has Excludes1 notes indicating codes that cannot be used together with it, including: autoimmune disease (systemic) NOS (M35.9); functional disorders of polymorphonuclear neutrophils (D71); human immunodeficiency virus [HIV] disease (B20).
What SNOMED CT codes does D83.9 map to?
D83.9 maps to 3 SNOMED CT concepts: 191010004, 23238000, 773664005. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for D83.9?
D83.9 is linked to 1 UMLS Concept Unique Identifier: C0009447. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does D83.9 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like common variable immunodeficiency, unspecified affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of D83.9?
D83.9 maps to the ICD-11 code: 4A01.0Y (Other specified immunodeficiencies with predominantly antibody defects).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.