D75.0
BillableFamilial erythrocytosis
Familial erythrocytosis
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Benign polycythemia
- Familial polycythemia
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- •autoimmune disease (systemic) NOSM35.9
- •certain conditions originating in the perinatal periodP00-P96
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •human immunodeficiency virus [HIV] diseaseB20
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
- •acute lymphadenitisL04
- •chronic lymphadenitisI88.1
- •enlarged lymph nodesR59
- •hypergammaglobulinemia NOSD89.2
- •lymphadenitis NOSI88.9
- •mesenteric lymphadenitis (acute) (chronic)I88.0
Related Codes(4)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(118)
SNOMED CT
- Familial erythrocytosis17342003
- Familial polycythaemia17342003
- Familial polycythemia17342003
- Hereditary pure erythrocytosis17342003
- Disorder of manganese metabolism63656007
- Primary malignant neoplasm of bone marrow93720005
- Erythrocythaemia109992005
- Erythrocythemia109992005
- Osler-Vaquez syndrome109992005
- PPP - Primary proliferative polycythaemia109992005
- PPP - Primary proliferative polycythemia109992005
- PRV - Polycythaemia rubra vera109992005
- PRV - Polycythemia rubra vera109992005
- Polycythaemia rubra vera109992005
- Polycythaemia vera109992005
- Polycythaemia vera (clinical)109992005
- Polycythemia rubra vera109992005
- Polycythemia vera109992005
- Polycythemia vera (clinical)109992005
- Primary polycythaemia109992005
- Primary proliferative polycythaemia109992005
- Primary proliferative polycythemia109992005
- Vaquez's disease109992005
- Familial erythrocytosis due to diphosphoglycerate mutase deficiency127065001
- Familial polycythaemia vera127066000
- Familial polycythemia vera127066000
- HMDPC - hypermanganesemia with dystonia, polycythaemia and cirrhosis702377007
- HMDPC - hypermanganesemia with dystonia, polycythemia and cirrhosis702377007
- Hypermanganesemia with dystonia, polycythaemia, and cirrhosis702377007
- Hypermanganesemia with dystonia, polycythemia, and cirrhosis702377007
- Familial manganese-induced neurotoxicity768553002
- HMNDYT - hypermanganesemia with dystonia768553002
- Hypermanganesemia with dystonia768553002
- Chuvash erythrocytosis770407006
- Chuvash polycythaemia770407006
- Chuvash polycythemia770407006
- Von Hippel Lindau dependent polycythaemia770407006
- Von Hippel Lindau dependent polycythemia770407006
- Primary familial polycythaemia due to erythropoietin receptor mutation1153349004
- Primary familial polycythemia due to erythropoietin receptor mutation1153349004
UMLS
- Benign familial polycythemiaC0152264
- Congenital erythrocytosisC0152264
- Familial ErythrocytosisC0152264
- Familial PolycythemiaC0152264
- Familial erythrocytosisC0152264
- Familial erythrocytosis (disorder)C0152264
- Familial polycythaemiaC0152264
- Familial polycythemiaC0152264
- Hereditary erythrocytosisC0152264
- Hereditary pure erythrocytosisC0152264
- Primary familial polycythemiaC0152264
- Benign polycythaemiaC0221276
- Benign polycythemiaC0221276
- Relative erythrocytosisC0221276
- Relative polycythaemiaC0221276
- Relative polycythemiaC0221276
- Relative polycythemia (disorder)C0221276
- Spurious polycythaemiaC0221276
- Spurious polycythemiaC0221276
- polycythemia relativeC0221276
- pseudopolycythemiaC0221276
- relative erythrocytosisC0221276
- relative polycythemiaC0221276
- spurious polycythemiaC0221276
Clinical Terms
- Familial erythrocytosis due to diphosphoglycerate mutase deficiency
- Disorder of manganese metabolism
- Von Hippel Lindau dependent polycythemia
- Familial Polycythemia
- spurious polycythemia
- Relative polycythaemia
- Vaquez's disease
- Osler-Vaquez syndrome
- Primary familial polycythemia
- Benign polycythemia
- Erythrocythemia
- Benign polycythaemia
- Polycythemia vera (clinical)
- Primary familial polycythemia due to erythropoietin receptor mutation
- Polycythemia vera
- PRV - Polycythaemia rubra vera
- Familial polycythemia vera
- Hypermanganesemia with dystonia
- Congenital erythrocytosis
- Hereditary pure erythrocytosis
- Relative polycythemia
- Primary malignant neoplasm of bone marrow
- Familial polycythaemia
- Hypermanganesemia with dystonia, polycythemia, and cirrhosis
- PRV - Polycythemia rubra vera
- Benign familial polycythemia
- Relative polycythemia (disorder)
- Spurious polycythaemia
- relative erythrocytosis
- Primary proliferative polycythemia
- pseudopolycythemia
- Familial manganese-induced neurotoxicity
- Primary polycythaemia
- HMNDYT - hypermanganesemia with dystonia
- Chuvash polycythemia
- Von Hippel Lindau dependent polycythaemia
- Hypermanganesemia with dystonia, polycythaemia, and cirrhosis
- Erythrocythaemia
- HMDPC - hypermanganesemia with dystonia, polycythaemia and cirrhosis
- PPP - Primary proliferative polycythemia
- Polycythaemia rubra vera
- Polycythaemia vera
- Familial polycythaemia vera
- Chuvash erythrocytosis
- polycythemia relative
- Polycythaemia vera (clinical)
- HMDPC - hypermanganesemia with dystonia, polycythemia and cirrhosis
- Primary familial polycythaemia due to erythropoietin receptor mutation
- Chuvash polycythaemia
- Polycythemia rubra vera
- Primary proliferative polycythaemia
- Hereditary erythrocytosis
- PPP - Primary proliferative polycythaemia
- Familial erythrocytosis (disorder)
Frequently Asked Questions
What is the ICD-10 code for familial erythrocytosis?
The ICD-10-CM code for familial erythrocytosis is D75.0. The full clinical description is "Familial erythrocytosis". D75.0 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code D75.0 mean?
ICD-10-CM code D75.0 represents “Familial erythrocytosis”. It is classified under Chapter 3: Diseases of the Blood and Blood-Forming Organs and is a billable/specific code that can be used on a claim.
Is D75.0 a billable code?
Yes, D75.0 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is D75.0 in?
D75.0 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).
What codes cannot be used with D75.0?
D75.0 has Excludes1 notes indicating codes that cannot be used together with it, including: hereditary ovalocytosis (D58.1).
What SNOMED CT codes does D75.0 map to?
D75.0 maps to 10 SNOMED CT concepts: 770407006, 63656007, 109992005, 17342003, 127065001, and 5 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for D75.0?
D75.0 is linked to 2 UMLS Concept Unique Identifiers: C0152264, C0221276. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does D75.0 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like familial erythrocytosis affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of D75.0?
D75.0 maps to the ICD-11 code: 3A80.0 (Primary inherited erythrocytosis).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.