AutoICD API

D74.0

Billable

Congenital methemoglobinemia

Congenital methemoglobinemia

Status

Billable / Specific

Block

D70-D77

Parent Code

D74

ICD-11 Mapping

1 equivalent

Coding Notes

Inclusion Terms

Alternative clinical terms for this condition

  • Congenital NADH-methemoglobin reductase deficiency
  • Hemoglobin-M [Hb-M] disease
  • Methemoglobinemia, hereditary

Excludes 2

Conditions not included here, but the patient may have both

Related Codes(2)
D74.8

Other methemoglobinemias

BillableD74.9

Methemoglobinemia, unspecified

Billable
ICD-11 Equivalents(1)

ICD-11 Equivalents

View full mapping

Corresponding ICD-11 codes from the WHO crosswalk mapping

3A9ZAnaemias or other erythrocyte disorders, unspecifiedequivalentPrimary
Also Known As / Clinical Terms(133)

SNOMED CT

UMLS

Clinical Terms

  • Hereditary M hemoglobinopathy
  • Hereditary methemoglobinemia due to globin chain mutation (disorder)
  • Deficiency of cytochrome-b<sub>5</sub> reductase (disorder)
  • Hemoglobin M disease
  • NADH-dependent methemoglobin reductase deficiency
  • Autosomal recessive congenital methemoglobinemia type I
  • Hereditary methemoglobinaemia
  • Deficiency of cytochrome-b5 reductase (disorder)
  • NADH-methaemoglobin reductase deficiency
  • Autosomal recessive congenital methemoglobinemia type II
  • NADH-methemoglobin reductase deficiency
  • Hereditary methemoglobinuria
  • Methemoglobinemia, hereditary
  • Congenital methemoglobinemia with abnormal methemoglobins
  • Congenital NADH-methemoglobin reductase deficiency
  • Autosomal recessive congenital methaemoglobinaemia type I
  • Hereditary methemoglobinemia due to globin chain mutation
  • Autosomal recessive congenital methemoglobinemia
  • Hereditary methemoglobinemia
  • NADH methemoglobin reductase deficiency
  • Hereditary methaemoglobinuria
  • Autosomal recessive congenital methaemoglobinaemia
  • Congenital NADH-methaemoglobin reductase deficiency
  • Deficiency of cytochrome-b5 reductase
  • NADH diaphorase deficiency
  • Chronic familial methaemoglobin reductase deficiency
  • Congenital methaemoglobinaemia
  • Autosomal recessive congenital methaemoglobinaemia type II
  • Methemoglobinemia due to deficiency of methemoglobin reductase
  • Congenital methemoglobinemia (disorder)
  • Deficiency of cytochrome-b>5< reductase (disorder)
  • Congenital methemoglobinaema with defective methemoglobin-reducing system
  • Congenital methemoglobinemia due to NADH-cytochrome b5 reductase 3 deficiency
  • Hereditary M haemoglobinopathy
  • NADH-CYB5R deficiency
  • Deficiency of cytochrome-b<sub>5</sub> reductase
  • Congenital methaemoglobinaemia due to NADH-cytochrome b5 reductase 3 deficiency
  • NADH cytochrome B5 reductase deficiency
  • Diaphorase deficiency
  • Haemoglobin M disease
  • Hereditary methemoglobinaemia due to globin chain mutation
  • DIHYDROLIPOAMIDE DEHYDROGENASE DEFICIENCY
  • Congenital methaemoglobinaemia with abnormal methaemoglobins
  • Hemoglobin-M [Hb-M] disease
  • Autosomal recessive congenital methemoglobinemia (disorder)
  • Chronic familial methemoglobin reductase deficiency
  • Nadh-Cytochrome B5 Reductase Deficiency
  • Cytochrome b5 reductase deficiency
  • Methemoglobinemia, Congenital, Autosomal Recessive
  • Congenital methaemoglobinaema with defective methaemoglobin-reducing system
  • Deficiency of cytochrome-b>5< reductase
Frequently Asked Questions
What is the ICD-10 code for congenital methemoglobinemia?

The ICD-10-CM code for congenital methemoglobinemia is D74.0. The full clinical description is "Congenital methemoglobinemia". D74.0 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code D74.0 mean?

ICD-10-CM code D74.0 represents “Congenital methemoglobinemia”. It is classified under Chapter 3: Diseases of the Blood and Blood-Forming Organs and is a billable/specific code that can be used on a claim.

Is D74.0 a billable code?

Yes, D74.0 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is D74.0 in?

D74.0 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).

What SNOMED CT codes does D74.0 map to?

D74.0 maps to 7 SNOMED CT concepts: 767497003, 767499000, 767498008, 234395000, 267550008, and 2 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for D74.0?

D74.0 is linked to 4 UMLS Concept Unique Identifiers: C0268193, C0272087, C3665425, C2873821. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does D74.0 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like congenital methemoglobinemia affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of D74.0?

D74.0 maps to the ICD-11 code: 3A9Z (Anaemias or other erythrocyte disorders, unspecified).

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.