D59.5
BillableParoxysmal nocturnal hemoglobinuria [Marchiafava-Micheli]
Paroxysmal nocturnal hemoglobinuria [Marchiafava-Micheli]
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- •autoimmune disease (systemic) NOSM35.9
- •certain conditions originating in the perinatal periodP00-P96
- •complications of pregnancy, childbirth and the puerperiumO9A)O00
- •congenital malformations, deformations and chromosomal abnormalitiesQ00-Q99
- •endocrine, nutritional and metabolic diseasesE00-E88
- •human immunodeficiency virus [HIV] diseaseB20
- •injury, poisoning and certain other consequences of external causesS00-T88
- •neoplasmsC00-D49
- •symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classifiedR00-R94
Related Codes(8)
D59.0Drug-induced autoimmune hemolytic anemia
D59.1Other autoimmune hemolytic anemias
D59.2Drug-induced nonautoimmune hemolytic anemia
D59.3Hemolytic-uremic syndrome
D59.4Other nonautoimmune hemolytic anemias
D59.6Hemoglobinuria due to hemolysis from other external causes
D59.8Other acquired hemolytic anemias
D59.9Acquired hemolytic anemia, unspecified
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(65)
SNOMED CT
- Marchiafava-Micheli syndrome1963002
- PNH - paroxysmal nocturnal haemoglobinuria1963002
- PNH - paroxysmal nocturnal hemoglobinuria1963002
- Paroxysmal nocturnal haemoglobinuria1963002
- Paroxysmal nocturnal hemoglobinuria1963002
- Thrombophilia due to paroxysmal nocturnal haemoglobinuria441990004
- Thrombophilia due to paroxysmal nocturnal haemoglobinuria (PNH)441990004
- Thrombophilia due to paroxysmal nocturnal hemoglobinuria441990004
- Thrombophilia due to paroxysmal nocturnal hemoglobinuria (PNH)441990004
- Occlusion of cutaneous microvasculature caused by platelet plug724856009
- Occlusion of microvasculature of skin caused by platelet plug724856009
- Occlusion of microvasculature of skin due to paroxysmal nocturnal haemoglobinuria-associated platelet plugs1251387004
- Occlusion of microvasculature of skin due to paroxysmal nocturnal hemoglobinuria-associated platelet plugs1251387004
- Occlusion of microvasculature of skin due to platelet thrombus associated with paroxysmal nocturnal haemoglobinuria1251387004
- Occlusion of microvasculature of skin due to platelet thrombus associated with paroxysmal nocturnal hemoglobinuria1251387004
UMLS
- Hemoglobinuria, Nocturnal ParoxysmalC0024790
- Hemoglobinuria, Paroxysmal NocturnalC0024790
- Marchiafava Micheli SyndromeC0024790
- Marchiafava Micheli diseaseC0024790
- Marchiafava-Micheli SyndromeC0024790
- Marchiafava-Micheli syndromeC0024790
- Nocturnal Paroxysmal HemoglobinuriaC0024790
- PAROXYSMAL NOCTURNAL HEMOGLOBINURIAC0024790
- PNHC0024790
- PNH - paroxysmal nocturnal haemoglobinuriaC0024790
- PNH - paroxysmal nocturnal hemoglobinuriaC0024790
- Paroxysmal HemoglobinuriaC0024790
- Paroxysmal Hemoglobinuria, NocturnalC0024790
- Paroxysmal Nocturnal HemoglobinuriaC0024790
- Paroxysmal nocturnal haemoglobinuriaC0024790
- Paroxysmal nocturnal hemoglobinuriaC0024790
- Paroxysmal nocturnal hemoglobinuria (PNH)C0024790
- Paroxysmal nocturnal hemoglobinuria (disorder)C0024790
- Paroxysmal nocturnal hemoglobinuria [Marchiafava-Micheli]C0024790
- Syndrome, Marchiafava-MicheliC0024790
- marchiafava-micheli syndromeC0024790
- paroxysmal nocturnal hemoglobinuriaC0024790
- paroxysmal nocturnal hemoglobinuria (PNH)C0024790
- pnhC0024790
Clinical Terms
- paroxysmal nocturnal hemoglobinuria
- Thrombophilia due to paroxysmal nocturnal hemoglobinuria (PNH)
- PNH - paroxysmal nocturnal haemoglobinuria
- Nocturnal Paroxysmal Hemoglobinuria
- Occlusion of microvasculature of skin due to paroxysmal nocturnal haemoglobinuria-associated platelet plugs
- Thrombophilia due to paroxysmal nocturnal haemoglobinuria (PNH)
- paroxysmal nocturnal hemoglobinuria (PNH)
- Occlusion of microvasculature of skin caused by platelet plug
- Marchiafava Micheli disease
- PNH
- marchiafava-micheli syndrome
- Syndrome, Marchiafava-Micheli
- Occlusion of cutaneous microvasculature caused by platelet plug
- PNH - paroxysmal nocturnal hemoglobinuria
- Paroxysmal Hemoglobinuria
- Paroxysmal nocturnal haemoglobinuria
- Hemoglobinuria, Paroxysmal Nocturnal
- Paroxysmal nocturnal hemoglobinuria (disorder)
- Occlusion of microvasculature of skin due to platelet thrombus associated with paroxysmal nocturnal haemoglobinuria
- Occlusion of microvasculature of skin due to paroxysmal nocturnal hemoglobinuria-associated platelet plugs
- Hemoglobinuria, Nocturnal Paroxysmal
- Thrombophilia due to paroxysmal nocturnal haemoglobinuria
- Paroxysmal Hemoglobinuria, Nocturnal
- Marchiafava Micheli Syndrome
- Thrombophilia due to paroxysmal nocturnal hemoglobinuria
- Occlusion of microvasculature of skin due to platelet thrombus associated with paroxysmal nocturnal hemoglobinuria
Frequently Asked Questions
What is the ICD-10 code for paroxysmal nocturnal hemoglobinuria [marchiafava-micheli]?
The ICD-10-CM code for paroxysmal nocturnal hemoglobinuria [marchiafava-micheli] is D59.5. The full clinical description is "Paroxysmal nocturnal hemoglobinuria [Marchiafava-Micheli]". D59.5 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code D59.5 mean?
ICD-10-CM code D59.5 represents “Paroxysmal nocturnal hemoglobinuria [Marchiafava-Micheli]”. It is classified under Chapter 3: Diseases of the Blood and Blood-Forming Organs and is a billable/specific code that can be used on a claim.
Is D59.5 a billable code?
Yes, D59.5 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is D59.5 in?
D59.5 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).
What codes cannot be used with D59.5?
D59.5 has Excludes1 notes indicating codes that cannot be used together with it, including: hemoglobinuria NOS (R82.3).
What SNOMED CT codes does D59.5 map to?
D59.5 maps to 4 SNOMED CT concepts: 1963002, 724856009, 1251387004, 441990004. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for D59.5?
D59.5 is linked to 1 UMLS Concept Unique Identifier: C0024790. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does D59.5 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like paroxysmal nocturnal hemoglobinuria [marchiafava-micheli] affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of D59.5?
D59.5 maps to the ICD-11 code: 3A21.0 (Paroxysmal nocturnal haemoglobinuria).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.