AutoICD API

D58.0

Billable

Hereditary spherocytosis

Hereditary spherocytosis

Status

Billable / Specific

Block

D55-D59

Parent Code

D58

ICD-11 Mapping

1 equivalent

Coding Notes

Inclusion Terms

Alternative clinical terms for this condition

  • Acholuric (familial) jaundice
  • Congenital (spherocytic) hemolytic icterus
  • Minkowski-Chauffard syndrome

Excludes 1

Codes that cannot be used together with this code (mutual exclusion)

Excludes 2

Conditions not included here, but the patient may have both

Related Codes(4)
D58.1

Hereditary elliptocytosis

BillableD58.2

Other hemoglobinopathies

BillableD58.8

Other specified hereditary hemolytic anemias

BillableD58.9

Hereditary hemolytic anemia, unspecified

Billable
ICD-11 Equivalents(1)

ICD-11 Equivalents

View full mapping

Corresponding ICD-11 codes from the WHO crosswalk mapping

3A10.YOther specified hereditary haemolytic anaemiaequivalentPrimary
Also Known As / Clinical Terms(74)

SNOMED CT

UMLS

Clinical Terms

  • HS - Hereditary spherocytosis
  • Spherocytoses, Hereditary
  • Mild hereditary spherocytosis due to spectrin deficiency
  • Severe hereditary spherocytosis due to combined deficiency of spectrin AND ankyrin
  • Congenital spherocytic haemolytic anaemia
  • Minkowski Chauffard syndrome
  • spherocytic hemolytic anemia
  • Anemia spherocytic
  • spherocytic anemia
  • Hereditary Spherocytoses
  • Minkowski-Chauffard syndrome
  • Spherocytic anaemia
  • Minkowsky-Chauffard syndrome
  • Congenital spherocytosis
  • Anaemia spherocytic
  • Acholuric (familial) jaundice
  • Congenital (spherocytic) hemolytic icterus
  • Familial spherocytosis
  • Hereditary spherocytosis due to spectrin deficiency
  • Severe hereditary spherocytosis due to spectrin deficiency
  • Familial acholuric jaundice
  • Spherocytosis, Hereditary
  • Mild hereditary spherocytosis due to combined deficiency of spectrin AND ankyrin
  • Congenital spherocytic hemolytic anemia
  • Hereditary spherocytosis due to beta spectrin defect
  • Spherocytosis
  • Hereditary spherocytosis (disorder)
  • spherocytosis hereditary
  • Hereditary spherocytosis due to combined deficiency of spectrin AND ankyrin
  • Hereditary spherocytosis due to deficiency of protein 4.2
Frequently Asked Questions
What is the ICD-10 code for hereditary spherocytosis?

The ICD-10-CM code for hereditary spherocytosis is D58.0. The full clinical description is "Hereditary spherocytosis". D58.0 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code D58.0 mean?

ICD-10-CM code D58.0 represents “Hereditary spherocytosis”. It is classified under Chapter 3: Diseases of the Blood and Blood-Forming Organs and is a billable/specific code that can be used on a claim.

Is D58.0 a billable code?

Yes, D58.0 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is D58.0 in?

D58.0 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).

What codes cannot be used with D58.0?

D58.0 has Excludes1 notes indicating codes that cannot be used together with it, including: hemolytic anemia of the newborn (P55.-).

What SNOMED CT codes does D58.0 map to?

D58.0 maps to 10 SNOMED CT concepts: 55995005, 69981004, 47516005, 33905008, 25266006, and 5 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for D58.0?

D58.0 is linked to 2 UMLS Concept Unique Identifiers: C0037889, C2873774. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does D58.0 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like hereditary spherocytosis affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of D58.0?

D58.0 maps to the ICD-11 code: 3A10.Y (Other specified hereditary haemolytic anaemia).

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.