5C56.30
Mucopolysaccharidosis type 1
Mucopolysaccharidosis type 1
Classification
ICD-11
Block
5C50-5C5ZParent Code
5C56.3ICD-10 Mapping
1 equivalentWHO Foundation
View on WHOICD-10 Equivalents(1)
ICD-10 Equivalents
View full mappingCorresponding ICD-10-CM codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(1)
Frequently Asked Questions
What is the ICD-11 code for mucopolysaccharidosis type 1?
The ICD-11 code for mucopolysaccharidosis type 1 is 5C56.30. The full clinical description is "Mucopolysaccharidosis type 1".
What does ICD-11 code 5C56.30 mean?
ICD-11 code 5C56.30 represents “Mucopolysaccharidosis type 1”. It is classified under Chapter 5: Endocrine, Nutritional or Metabolic Diseases.
What chapter is 5C56.30 in?
5C56.30 is in Chapter 5: Endocrine, Nutritional or Metabolic Diseases (codes 5A00-5D46).
What is the ICD-10 equivalent of ICD-11 code 5C56.30?
5C56.30 maps to the ICD-10 code: E76.0 (Mucopolysaccharidosis, type I). This is an equivalent mapping.
What is the difference between ICD-10 and ICD-11?
ICD-11 is the latest revision of the WHO's International Classification of Diseases, succeeding ICD-10. Key differences include: a fully digital-first design, new chapters for sleep-wake disorders, sexual health, and traditional medicine, improved coding for rare diseases, and better integration with electronic health records through extension codes.
What UMLS concepts map to ICD-11 code 5C56.30?
5C56.30 is linked to 1 UMLS Concept Unique Identifier: C0023786. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
Automate Medical Coding With AI
Send clinical text to the AutoICD API and get back structured ICD-10 and ICD-11 codes with confidence scores. Integrates into any EHR or billing system in minutes.
Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.