4A01.22
Immune dysregulation syndromes presenting primarily with lymphoproliferation
Immune dysregulation syndromes presenting primarily with lymphoproliferation
Classification
ICD-11
Block
4A00-4A0ZParent Code
4A01.2ICD-10 Mapping
1 equivalentWHO Foundation
View on WHOICD-10 Equivalents(1)
ICD-10 Equivalents
View full mappingCorresponding ICD-10-CM codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(7)
SNOMED CT ↗
- Duncan's syndrome77121009
- Immunodeficiency following hereditary defective response to Epstein-Barr virus191008001
- X-linked immunodeficiency with magnesium defect, Epstein-Barr virus infection and neoplasia711481001
- SH2D1A/SLAM-associated protein deficiency1162828001
- X-linked lymphoproliferative disease due to XIAP deficiency1162830004
Frequently Asked Questions
What is the ICD-11 code for immune dysregulation syndromes presenting primarily with lymphoproliferation?
The ICD-11 code for immune dysregulation syndromes presenting primarily with lymphoproliferation is 4A01.22. The full clinical description is "Immune dysregulation syndromes presenting primarily with lymphoproliferation".
What does ICD-11 code 4A01.22 mean?
ICD-11 code 4A01.22 represents “Immune dysregulation syndromes presenting primarily with lymphoproliferation”. It is classified under Chapter 4: Diseases of the Immune System.
What chapter is 4A01.22 in?
4A01.22 is in Chapter 4: Diseases of the Immune System (codes 4A00-4B4Z).
What is the ICD-10 equivalent of ICD-11 code 4A01.22?
4A01.22 maps to the ICD-10 code: D82.3 (Immunodef fol heredit defctv response to Epstein-Barr virus). This is an equivalent mapping.
What is the difference between ICD-10 and ICD-11?
ICD-11 is the latest revision of the WHO's International Classification of Diseases, succeeding ICD-10. Key differences include: a fully digital-first design, new chapters for sleep-wake disorders, sexual health, and traditional medicine, improved coding for rare diseases, and better integration with electronic health records through extension codes.
What SNOMED CT codes does 4A01.22 map to?
4A01.22 maps to 5 SNOMED CT concepts: 77121009, 191008001, 1162828001, 711481001, 1162830004. SNOMED CT is a clinical terminology used in electronic health records.
What UMLS concepts map to ICD-11 code 4A01.22?
4A01.22 is linked to 2 UMLS Concept Unique Identifiers: C0549463, C0451697. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
Automate Medical Coding With AI
Send clinical text to the AutoICD API and get back structured ICD-10 and ICD-11 codes with confidence scores. Integrates into any EHR or billing system in minutes.
Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.