D82.3
BillableImmunodef fol heredit defctv response to Epstein-Barr virus
Immunodeficiency following hereditary defective response to Epstein-Barr virus
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- X-linked lymphoproliferative disease
Includes
Conditions included under this code
- defects in the complement system
- immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
- sarcoidosis
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- autoimmune disease (systemic) NOS (M35.9)
- certain conditions originating in the perinatal period (P00-P96)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- human immunodeficiency virus [HIV] disease (B20)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Also Known As / Clinical Terms
SNOMED CT
- Duncan's syndrome77121009
- Familial fatal Epstein-Barr infection77121009
- Purtilo syndrome77121009
- Severe susceptibility to Epstein-Barr infection77121009
- X-linked lymphoproliferative syndrome77121009
- XLPS - X-linked lymphoproliferative syndrome77121009
- Immunodeficiency following hereditary defective response to Epstein-Barr virus191008001
- X-linked immunodeficiency with magnesium defect, Epstein-Barr virus infection and neoplasia711481001
- SH2D1A/SLAM-associated protein deficiency1162828001
- X-linked lymphoproliferative disease due to SH2D1A deficiency1162828001
- X-linked lymphoproliferative syndrome type 11162828001
- X-linked lymphoproliferative disease due to XIAP deficiency1162830004
- X-linked lymphoproliferative syndrome type 21162830004
- XIAP deficiency syndrome1162830004
UMLS
- Disease, DuncanC0549463
- Disease, X-Linked LymphoproliferativeC0549463
- Diseases, X-Linked LymphoproliferativeC0549463
- Disorder, X-Linked LymphoproliferativeC0549463
- Disorders, X-Linked LymphoproliferativeC0549463
- Duncan DiseaseC0549463
- Duncan diseaseC0549463
- Duncan syndromeC0549463
- Duncan's SyndromeC0549463
- Duncan's syndromeC0549463
- Epstein Barr Virus Induced Lymphoproliferative Disease In MalesC0549463
- Epstein Barr Virus Infection, Familial FatalC0549463
- Epstein-Barr Virus Infection, Familial FatalC0549463
- Epstein-Barr Virus-Induced Lymphoproliferative Disease In MalesC0549463
- Epstein-Barr virus-induced lymphoproliferative disease in malesC0549463
- Familial Fatal Epstein Barr InfectionC0549463
- Familial Fatal Epstein-Barr InfectionC0549463
- Familial fatal Epstein-Barr infectionC0549463
- Immunodeficiency 5C0549463
- Immunodeficiency 5sC0549463
- Immunodeficiency, X Linked Progressive Combined VariableC0549463
- Immunodeficiency, X-Linked Progressive Combined VariableC0549463
- Lymphoproliferative Disease, X LinkedC0549463
- Lymphoproliferative Disease, X-LinkedC0549463
- Lymphoproliferative Diseases, X-LinkedC0549463
- Lymphoproliferative Disorder, X-LinkedC0549463
- Lymphoproliferative Disorders, X-LinkedC0549463
- Lymphoproliferative Syndrome, X-LinkedC0549463
- Lymphoproliferative Syndrome, X-Linked, 1C0549463
- Lymphoproliferative Syndromes, X-LinkedC0549463
- Purtilo SyndromeC0549463
- Purtilo SyndromesC0549463
- Purtilo syndromeC0549463
- Severe susceptibility to EBV infectionC0549463
- Severe susceptibility to Epstein-Barr infectionC0549463
- Severe susceptibility to infectious mononucleosisC0549463
- Syndrome, PurtiloC0549463
- Syndrome, X-Linked LymphoproliferativeC0549463
- Syndromes, PurtiloC0549463
- Syndromes, X-Linked LymphoproliferativeC0549463
- X LINKED LYMPHOPROLIFERATIVE DISC0549463
- X Linked Lymphoproliferative DiseaseC0549463
- X Linked Lymphoproliferative DisorderC0549463
- X Linked Lymphoproliferative SyndromeC0549463
- X-Linked Lymphoproliferative DiseaseC0549463
- X-Linked Lymphoproliferative DiseasesC0549463
- X-Linked Lymphoproliferative DisorderC0549463
- X-Linked Lymphoproliferative DisordersC0549463
- X-Linked Lymphoproliferative SyndromeC0549463
- X-Linked Lymphoproliferative SyndromesC0549463
- X-linked lymphoproliferative diseaseC0549463
- X-linked lymphoproliferative syndromeC0549463
- X-linked lymphoproliferative syndrome (disorder)C0549463
- XLPC0549463
- XLPS - X-linked lymphoproliferative syndromeC0549463
- duncan syndromeC0549463
- duncan's syndromeC0549463
- duncans syndromeC0549463
- Immunodef fol heredit defctv response to Epstein-Barr virusC0451697
- Immunodeficiency following hereditary defective response to Epstein-Barr virusC0451697
- Immunodeficiency following hereditary defective response to Epstein-Barr virus (disorder)C0451697
Frequently Asked Questions
What is ICD-10 code D82.3?
ICD-10-CM code D82.3 represents "Immunodeficiency following hereditary defective response to Epstein-Barr virus". It is a billable/specific code that can be used on a claim.
Is D82.3 a billable code?
Yes, D82.3 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is D82.3 in?
D82.3 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).
What codes cannot be used with D82.3?
D82.3 has Excludes1 notes indicating codes that cannot be used together with it, including: autoimmune disease (systemic) NOS (M35.9); functional disorders of polymorphonuclear neutrophils (D71); human immunodeficiency virus [HIV] disease (B20); and 1 more.
What SNOMED CT codes does D82.3 map to?
D82.3 maps to 5 SNOMED CT concepts: 77121009, 191008001, 1162828001, 711481001, 1162830004. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for D82.3?
D82.3 is linked to 2 UMLS Concept Unique Identifiers: C0549463, C0451697. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.