4A01.12
Major histocompatibility complex class II deficiency
Major histocompatibility complex class II deficiency
Classification
ICD-11
Block
4A00-4A0ZParent Code
4A01.1ICD-10 Mapping
1 equivalentWHO Foundation
View on WHOICD-10 Equivalents(1)
ICD-10 Equivalents
View full mappingCorresponding ICD-10-CM codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(6)
SNOMED CT ↗
- Bare lymphocyte syndrome type 2191002000
- Immunodeficiency by defective expression of major histocompatibility complex class II due to regulatory factor X associated protein mutation1351501003
- Immunodeficiency by defective expression of major histocompatibility complex class II due to class II major histocompatibility complex transactivator mutation1351502005
- Immunodeficiency by defective expression of major histocompatibility complex class II due to regulatory factor X associated ankyrin containing protein mutation1351503000
- Immunodeficiency by defective expression of major histocompatibility complex class II due to regulatory factor X5 mutation1351504006
Frequently Asked Questions
What is the ICD-11 code for major histocompatibility complex class ii deficiency?
The ICD-11 code for major histocompatibility complex class ii deficiency is 4A01.12. The full clinical description is "Major histocompatibility complex class II deficiency".
What does ICD-11 code 4A01.12 mean?
ICD-11 code 4A01.12 represents “Major histocompatibility complex class II deficiency”. It is classified under Chapter 4: Diseases of the Immune System.
What chapter is 4A01.12 in?
4A01.12 is in Chapter 4: Diseases of the Immune System (codes 4A00-4B4Z).
What is the ICD-10 equivalent of ICD-11 code 4A01.12?
4A01.12 maps to the ICD-10 code: D81.7 (Major histocompatibility complex class II deficiency). This is an equivalent mapping.
What is the difference between ICD-10 and ICD-11?
ICD-11 is the latest revision of the WHO's International Classification of Diseases, succeeding ICD-10. Key differences include: a fully digital-first design, new chapters for sleep-wake disorders, sexual health, and traditional medicine, improved coding for rare diseases, and better integration with electronic health records through extension codes.
What SNOMED CT codes does 4A01.12 map to?
4A01.12 maps to 5 SNOMED CT concepts: 191002000, 1351502005, 1351503000, 1351501003, 1351504006. SNOMED CT is a clinical terminology used in electronic health records.
What UMLS concepts map to ICD-11 code 4A01.12?
4A01.12 is linked to 1 UMLS Concept Unique Identifier: C2931418. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.