4A01.10
Severe combined immunodeficiencies
Severe combined immunodeficiencies
Classification
ICD-11
Block
4A00-4A0ZParent Code
4A01.1ICD-10 Mapping
5 equivalentsWHO Foundation
View on WHOICD-10 Equivalents(5)
ICD-10 Equivalents
View full mappingCorresponding ICD-10-CM codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(15)
SNOMED CT ↗
- Combined immunodeficiency associated with maturation pathway defect3439009
- SCID (severe combined immunodeficiency) due to absent IL-2 (interleukin-2) production45390000
- SCID (severe combined immunodeficiency) due to absent T cell receptor49555001
- Severe combined immunodeficiency with reticular dysgenesis190996002
- Hereditary eosinophilia191358004
- Disorder of eosinophil417967008
- Omenn syndrome722067005
- Combined immunodeficiency due to partial RAG1 deficiency725290000
- SCID (severe combined immunodeficiency) due to complete RAG1/2 deficiency765188009
- Autosomal dominant T-B- SCID (severe combined immunodeficiency) due to activated RAC2 defect1351235001
UMLS ↗
- Severe combined immunodeficiency [SCID] with reticular dysgenesisC0494256
- Severe combined immunodeficiency [SCID] with low T- and B-cell numbersC0451693
- Severe combined immunodef w low or normal B-cell numbersC0451694
- ADA - Adenosine aminohydrolase deficiencyC0268124
- Immunodeficiency with short-limbed statureC0265299
Frequently Asked Questions
What is the ICD-11 code for severe combined immunodeficiencies?
The ICD-11 code for severe combined immunodeficiencies is 4A01.10. The full clinical description is "Severe combined immunodeficiencies".
What does ICD-11 code 4A01.10 mean?
ICD-11 code 4A01.10 represents “Severe combined immunodeficiencies”. It is classified under Chapter 4: Diseases of the Immune System.
What chapter is 4A01.10 in?
4A01.10 is in Chapter 4: Diseases of the Immune System (codes 4A00-4B4Z).
What is the ICD-10 equivalent of ICD-11 code 4A01.10?
4A01.10 maps to 5 ICD-10 codes: D81.0 (Severe combined immunodeficiency with reticular dysgenesis), D81.1 (Severe combined immunodeficiency w low T- and B-cell numbers), D81.2 (Severe combined immunodef w low or normal B-cell numbers), and 2 more. ICD-10 and ICD-11 do not always have one-to-one mappings — check the mapping type (equivalent, approximate, narrower, or broader) for each result.
What is the difference between ICD-10 and ICD-11?
ICD-11 is the latest revision of the WHO's International Classification of Diseases, succeeding ICD-10. Key differences include: a fully digital-first design, new chapters for sleep-wake disorders, sexual health, and traditional medicine, improved coding for rare diseases, and better integration with electronic health records through extension codes.
What SNOMED CT codes does 4A01.10 map to?
4A01.10 maps to 10 SNOMED CT concepts: 3439009, 190996002, 1351235001, 725290000, 417967008, and 5 more. SNOMED CT is a clinical terminology used in electronic health records.
What UMLS concepts map to ICD-11 code 4A01.10?
4A01.10 is linked to 5 UMLS Concept Unique Identifiers: C0494256, C0451693, C0451694, C0268124, C0265299. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.