Q01
Non-billableEncephalocele
Encephalocele
This is a header/category code. For billing purposes, use a more specific child code from the list below.
Coding Notes
Includes
Conditions included under this code
- Arnold-Chiari syndrome, type III
- encephalocystocele
- encephalomyelocele
- hydroencephalocele
- hydromeningocele, cranial
- meningocele, cerebral
- meningoencephalocele
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
Child Codes (5)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(35)
UMLS
- Arnold-Chiari syndrome, type IIIC4290271
- Bifid skullC4551722
- Cranium BifidumC4551722
- Cranium bifidumC4551722
- EncephaloceleC4551722
- Encephalocele (disorder)C4551722
- Encephalocele, unspecifiedC4551722
- Cerebral meningoceleC0009694
- Congenital cerebral meningoceleC0009694
- Congenital cerebral meningocele (disorder)C0009694
- Congenital cranial meningoceleC0009694
- Cranial MeningoceleC0009694
- Cranial hydromeningoceleC0009694
- Cranial meningoceleC0009694
- congenital cerebral meningoceleC0009694
- cranial meningoceleC0009694
- meningocele cerebralC0009694
- meningocele, cerebralC0009694
- EncephalocystoceleC0266455
- Encephalocystocele (disorder)C0266455
- HydrencephaloceleC0266455
- HydrocephaloceleC0266455
- HydroencephaloceleC0266455
- encephalocystoceleC0266455
- hydroencephaloceleC0266455
- EncephalomeningoceleC0266456
- HydrencephalomeningoceleC0266456
- MeningoencephaloceleC0266456
- Meningoencephalocele (disorder)C0266456
- encephalomeningoceleC0266456
- meningoencephaloceleC0266456
- EncephalomyeloceleC0266454
- Encephalomyelocele (disorder)C0266454
- encephalomyeloceleC0266454
- hydromeningocele, cranialC0266459
Frequently Asked Questions
What is the ICD-10 code for encephalocele?
The ICD-10-CM code for encephalocele is Q01. The full clinical description is "Encephalocele". Q01 is a non-billable header code. Use a more specific child code for billing purposes.
What does ICD-10 code Q01 mean?
ICD-10-CM code Q01 represents “Encephalocele”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a non-billable header code. Use a more specific child code for billing purposes.
Is Q01 a billable code?
No, Q01 is a non-billable header code. You need to use one of its more specific child codes for billing. There are 5 child codes under Q01.
What chapter is Q01 in?
Q01 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What codes cannot be used with Q01?
Q01 has Excludes1 notes indicating codes that cannot be used together with it, including: Meckel-Gruber syndrome (Q61.9).
What are the subcategories under Q01?
Q01 has 5 child codes, including: Q01.0 (Frontal encephalocele), Q01.1 (Nasofrontal encephalocele), Q01.2 (Occipital encephalocele), Q01.8 (Encephalocele of other sites), and 1 more.
What are the UMLS CUIs for Q01?
Q01 is linked to 7 UMLS Concept Unique Identifiers: C4290271, C4551722, C0009694, C0266455, C0266456, and 2 more. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q01 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like encephalocele affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q01?
Q01 maps to the ICD-11 code: LA01 (Cephalocele).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.