H49.40
BillableProgressive external ophthalmoplegia, unspecified eye
Progressive external ophthalmoplegia, unspecified eye
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- Kearns-Sayre syndrome (H49.81-)
Excludes 2
Conditions not included here, but the patient may have both
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
- diabetes mellitus related eye conditions (E09.3-, E10.3-, E11.3-, E13.3-)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury (trauma) of eye and orbit (S05.-)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
- syphilis related eye disorders (A50.01, A50.3-, A51.43, A52.71)
- nystagmus and other irregular eye movements (H55)
- internal ophthalmoplegia (H52.51-)
- internuclear ophthalmoplegia (H51.2-)
- progressive supranuclear ophthalmoplegia (G23.1)
Also Known As / Clinical Terms
SNOMED CT
- CPEO - chronic progressive external ophthalmoplegia46252003
- Chronic progressive external ophthalmoplegia46252003
- Chronic progressive ophthalmoplegia46252003
- Graefe's disease46252003
- PEO - Progressive external ophthalmoplegia46252003
- Progressive external ophthalmoplegia46252003
- Ophthalmoplegia plus syndrome77835008
- Painful ophthalmoplegia95794005
- Tolosa-Hunt syndrome95794005
- Oculomotor nerve finding106153001
- Third cranial nerve finding106153001
- Adult-onset CPEO (chronic progressive external ophthalmoplegia) with mitochondrial myopathy725464001
- Adult-onset chronic progressive external ophthalmoplegia with mitochondrial myopathy725464001
- Mitochondrial DNA (deoxyribonucleic acid) maintenance syndrome due to MGME1 (mitochondrial genome maintenance exonuclease 1) deficiency764733009
- PEO (progressive external ophthalmoplegia) myopathy emaciation syndrome764733009
- Progressive external ophthalmoplegia, myopathy, emaciation syndrome764733009
- Autosomal dominant progressive external ophthalmoplegia827115000
- adPEO - autosomal dominant progressive external ophthalmoplegia827115000
- Autosomal recessive progressive external ophthalmoplegia827117008
- arPEO- autosomal recessive progressive external ophthalmoplegia827117008
- Autosomal dominant progressive external ophthalmoplegia type 51156853004
- Autosomal dominant progressive external ophthalmoplegia type 31156855006
- Autosomal dominant progressive external ophthalmoplegia type 41156856007
- Autosomal dominant progressive external ophthalmoplegia type 11156857003
- Autosomal dominant progressive external ophthalmoplegia type 21156858008
Frequently Asked Questions
What is the ICD-10 code for progressive external ophthalmoplegia, unspecified eye?
The ICD-10-CM code for progressive external ophthalmoplegia, unspecified eye is H49.40. The full clinical description is "Progressive external ophthalmoplegia, unspecified eye". H49.40 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code H49.40 mean?
ICD-10-CM code H49.40 represents "Progressive external ophthalmoplegia, unspecified eye". It is classified under Chapter 7: Diseases of the Eye and Adnexa and is a billable/specific code that can be used on a claim.
Is H49.40 a billable code?
Yes, H49.40 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is H49.40 in?
H49.40 is in Chapter 7: Diseases of the Eye and Adnexa (codes H00-H59).
What codes cannot be used with H49.40?
H49.40 has Excludes1 notes indicating codes that cannot be used together with it, including: Kearns-Sayre syndrome (H49.81-).
What SNOMED CT codes does H49.40 map to?
H49.40 maps to 13 SNOMED CT concepts: 725464001, 827115000, 1156857003, 1156858008, 1156855006, and 8 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for H49.40?
H49.40 is linked to 1 UMLS Concept Unique Identifier: C2881296. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.