E75.25
BillableMetachromatic leukodystrophy
Metachromatic leukodystrophy
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)
- androgen insensitivity syndrome (E34.5-)
- congenital adrenal hyperplasia (E25.0)
- hemolytic anemias attributable to enzyme disorders (D55.-)
- Marfan syndrome (Q87.4-)
- 5-alpha-reductase deficiency (E29.1)
- mucolipidosis, types I-III (E77.0-E77.1)
- Refsum's disease (G60.1)
- adrenoleukodystrophy [Addison-Schilder] (E71.528)
Excludes 2
Conditions not included here, but the patient may have both
- Ehlers-Danlos syndromes (Q79.6-)
Also Known As / Clinical Terms
SNOMED CT
- Adult metachromatic leucodystrophy24326000
- Adult metachromatic leukodystrophy24326000
- Metachromatic leucodystrophy, adult type24326000
- Metachromatic leukodystrophy, adult type24326000
- Metachromatic leucodystrophy, congenital type40802007
- Metachromatic leukodystrophy, congenital type40802007
- Juvenile metachromatic leucodystrophy44359008
- Metachromatic leucodystrophy, juvenile type44359008
- Metachromatic leukodystrophy, juvenile type44359008
- Scholz cerebral sclerosis44359008
- Scholz-Bielschowsky-Henneberg diffuse cerebral sclerosis44359008
- Greenfield disease47683004
- Late infantile metachromatic leucodystrophy47683004
- Metachromatic leucodystrophy, late infantile type47683004
- Metachromatic leukodystrophy, late infantile type47683004
- SAPI - Sphingolipid activator protein I deficiency68390005
- Saposin B deficiency68390005
- Sphingolipid activator protein 1 deficiency68390005
- Metachromatic leucodystrophy without arylsulphatase deficiency83832001
- Metachromatic leukodystrophy without arylsulfatase deficiency83832001
- ARSA - Arylsulfatase A deficiency238031009
- ARSA - Arylsulphatase A deficiency238031009
- Arylsulfatase A deficiency238031009
- Arylsulphatase A deficiency238031009
- Cerebroside sulfatase deficiency238031009
- Cerebroside sulphatase deficiency238031009
- Severe deficiency of arylsulfatase238031009
- Severe deficiency of arylsulphatase238031009
- Metachromatic leucodystrophy due to deficiency of cerebroside sulphatase activator297278001
- Metachromatic leukodystrophy due to deficiency of cerebroside sulfatase activator297278001
- Familial progressive cerebral sclerosis396338004
- MLD - Metachromatic leucodystrophy396338004
- Metachromatic leucodystrophy396338004
- Metachromatic leukodystrophy396338004
- Metachromatic leukoencephaly396338004
- Sulfatide lipidosis396338004
- Sulphatide lipidosis396338004
- van Bogaert-Nijssen disease396338004
- PMLD - Pelizaeus Merzbacher like disease717042001
- Pelizaeus Merzbacher like disease717042001
- Dystonia due to metachromatic leucodystrophy1260391004
- Dystonia due to metachromatic leukodystrophy1260391004
UMLS
- ARYLSULFATASE A DEFIC DISC0023522
- Arylsulfatase A Deficiency DiseaseC0023522
- CEREBRAL SCLEROSIS, DIFFUSE, METACHROMATIC FORMC0023522
- CEREBROSIDE SULFATASE DEFICIENCYC0023522
- CEREBROSIDE SULPHATASE DEFIC DISC0023522
- Cerebral sclerosis, Diffuse, Metachromatic FormC0023522
- Cerebral sclerosis, diffuse, metachromatic formC0023522
- Cerebroside Sulphatase Deficiency DiseaseC0023522
- Cerebroside sulphatase deficiency diseaseC0023522
- Familial progressive cerebral sclerosisC0023522
- Leukodystrophies, MetachromaticC0023522
- Leukodystrophy, MetachromaticC0023522
- Leukoencephalopathies, MetachromaticC0023522
- Leukoencephalopathy, MetachromaticC0023522
- Lipidosis, SulfatideC0023522
- METACHROMATIC LEUKODYSTROPHYC0023522
- METACHROMATIC LEUKOENCEPHALOPATHYC0023522
- MLDC0023522
- MLD - Metachromatic leucodystrophyC0023522
- Metachromatic LeukodystrophiesC0023522
- Metachromatic LeukodystrophyC0023522
- Metachromatic LeukoencephalopathiesC0023522
- Metachromatic LeukoencephalopathyC0023522
- Metachromatic leucodystrophyC0023522
- Metachromatic leucodystrophy (disorder)C0023522
- Metachromatic leukodystrophyC0023522
- Metachromatic leukoencephalopathyC0023522
- Metachromatic leukoencephalyC0023522
- SULFATIDE LIPIDOSISC0023522
- Scholz cerebral sclerosisC0023522
- Scholz-Bielschowsky-Henneberg diffuse cerebral sclerosisC0023522
- Sulfatide LipidosisC0023522
- Sulfatide lipidosisC0023522
- Sulphatide lipidosisC0023522
- leukodystrophy metachromaticC0023522
- metachromatic leucodystrophyC0023522
- metachromatic leukodystrophyC0023522
- metachromatic leukoencephalopathyC0023522
- metachromatic leukoencephalyC0023522
- mldC0023522
- sulfatide lipoidosisC0023522
- van Bogaert-Nijssen diseaseC0023522
Frequently Asked Questions
What is the ICD-10 code for metachromatic leukodystrophy?
The ICD-10-CM code for metachromatic leukodystrophy is E75.25. The full clinical description is "Metachromatic leukodystrophy". E75.25 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code E75.25 mean?
ICD-10-CM code E75.25 represents "Metachromatic leukodystrophy". It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.
Is E75.25 a billable code?
Yes, E75.25 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E75.25 in?
E75.25 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E75.25?
E75.25 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 6 more.
What SNOMED CT codes does E75.25 map to?
E75.25 maps to 11 SNOMED CT concepts: 238031009, 24326000, 1260391004, 396338004, 47683004, and 6 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E75.25?
E75.25 is linked to 1 UMLS Concept Unique Identifier: C0023522. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.