E75.2
Non-billableOther sphingolipidosis
Other sphingolipidosis
This is a header/category code. For billing purposes, use a more specific child code from the list below.
Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)
- androgen insensitivity syndrome (E34.5-)
- congenital adrenal hyperplasia (E25.0)
- hemolytic anemias attributable to enzyme disorders (D55.-)
- Marfan syndrome (Q87.4-)
- 5-alpha-reductase deficiency (E29.1)
- mucolipidosis, types I-III (E77.0-E77.1)
- Refsum's disease (G60.1)
- adrenoleukodystrophy [Addison-Schilder] (E71.528)
Excludes 2
Conditions not included here, but the patient may have both
- Ehlers-Danlos syndromes (Q79.6-)
Child Codes (9)
E75.21Fabry (-Anderson) disease
E75.22Gaucher disease
E75.23Krabbe disease
E75.24Niemann-Pick disease
E75.25Metachromatic leukodystrophy
E75.26Sulfatase deficiency
E75.27Pelizaeus-Merzbacher disease
E75.28Canavan disease
E75.29Other sphingolipidosis
Also Known As / Clinical Terms
Frequently Asked Questions
What is ICD-10 code E75.2?
ICD-10-CM code E75.2 represents "Other sphingolipidosis". It is a non-billable header code — use a more specific child code for billing purposes.
Is E75.2 a billable code?
No, E75.2 is a non-billable header code. You need to use one of its more specific child codes for billing. There are 9 child codes under E75.2.
What chapter is E75.2 in?
E75.2 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E75.2?
E75.2 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 6 more.
What are the subcategories under E75.2?
E75.2 has 9 child codes, including: E75.21 (Fabry (-Anderson) disease), E75.22 (Gaucher disease), E75.23 (Krabbe disease), E75.24 (Niemann-Pick disease), and 5 more.
What are the UMLS CUIs for E75.2?
E75.2 is linked to 1 UMLS Concept Unique Identifier: C0348489. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.