E77.0
BillableDefects in post-translational mod of lysosomal enzymes
Defects in post-translational modification of lysosomal enzymes
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Mucolipidosis II [I-cell disease]
- Mucolipidosis III [pseudo-Hurler polydystrophy]
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- Ehlers-Danlos syndromes (Q79.6-)
Also Known As / Clinical Terms
SNOMED CT
- Mucolipidosis III65764006
- Pseudo-Hurler disease65764006
- Pseudo-Hurler polydystrophy65764006
- Pseudo-Hurler's disease65764006
- I-cell - Inclusion cell disease70199000
- I-cell disease70199000
- Mucolipidosis II70199000
- Mucolipidosis type II70199000
- N-acetylglucosamine-1-phosphotransferase deficiency70199000
- Mucolipidosis70528007
- Defect in post-translational modification of lysosomal enzymes190948002
UMLS
- Defect in post-translational modification of lysosomal enzymesC0342845
- Defect in post-translational modification of lysosomal enzymes (disorder)C0342845
- Defects in post-translational mod of lysosomal enzymesC0342845
- Defects in post-translational modification of lysosomal enzymesC0342845
- Mucolipidosis II [I-cell disease]C2874285
- Mucolipidosis III [pseudo-Hurler polydystrophy]C2874286
Frequently Asked Questions
What is ICD-10 code E77.0?
ICD-10-CM code E77.0 represents "Defects in post-translational modification of lysosomal enzymes". It is a billable/specific code that can be used on a claim.
Is E77.0 a billable code?
Yes, E77.0 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E77.0 in?
E77.0 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E77.0?
E77.0 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 3 more.
What SNOMED CT codes does E77.0 map to?
E77.0 maps to 4 SNOMED CT concepts: 190948002, 70199000, 70528007, 65764006. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E77.0?
E77.0 is linked to 3 UMLS Concept Unique Identifiers: C0342845, C2874285, C2874286. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
Automate ICD-10 Coding With AI
Send clinical text to the AutoICD API and get back structured ICD-10 codes with confidence scores. Integrates into any EHR or billing system in minutes.
Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.