E75.244
BillableNiemann-Pick disease type A/B
Niemann-Pick disease type A/B
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Acid sphingomyelinase deficiency type A/B (ASMD type A/B)
- Chronic neurovisceral acid sphingomyelinase deficiency
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)
- androgen insensitivity syndrome (E34.5-)
- congenital adrenal hyperplasia (E25.0)
- hemolytic anemias attributable to enzyme disorders (D55.-)
- Marfan syndrome (Q87.4-)
- 5-alpha-reductase deficiency (E29.1)
- mucolipidosis, types I-III (E77.0-E77.1)
- Refsum's disease (G60.1)
- adrenoleukodystrophy [Addison-Schilder] (E71.528)
Excludes 2
Conditions not included here, but the patient may have both
- Ehlers-Danlos syndromes (Q79.6-)
Also Known As / Clinical Terms
SNOMED CT
- Lipoidosis11455007
- Neuronal cholesterol lipidosis58459009
- Niemann-Pick disease58459009
- Sphingomyelin lipidosis58459009
- Sphingomyelin/cholesterol lipidosis58459009
- Sphingomyelinase deficiency58459009
- Chronic neurovisceral ASMD (acid sphingomyelinase deficiency)1362021005
- Chronic neurovisceral acid sphingomyelinase deficiency1362021005
- NPD-A/B - Niemann Pick disease type A/B1362021005
- Niemann Pick disease type A/B1362021005
UMLS
- Acid sphingomyelinase deficiency type A/B (ASMD type A/B)C5539332
- Chronic neurovisceral ASMD (acid sphingomyelinase deficiency)C5539139
- Chronic neurovisceral acid sphingomyelinase deficiencyC5539139
- Chronic neurovisceral acid sphingomyelinase deficiency (disorder)C5539139
- NPD-A/B - Niemann Pick disease type A/BC5539139
- Niemann Pick disease type A/BC5539139
- Niemann-Pick disease type A/BC5539139
Frequently Asked Questions
What is the ICD-10 code for niemann-pick disease type a/b?
The ICD-10-CM code for niemann-pick disease type a/b is E75.244. The full clinical description is "Niemann-Pick disease type A/B". E75.244 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code E75.244 mean?
ICD-10-CM code E75.244 represents "Niemann-Pick disease type A/B". It is classified under Chapter 4: Endocrine, Nutritional and Metabolic Diseases and is a billable/specific code that can be used on a claim.
Is E75.244 a billable code?
Yes, E75.244 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is E75.244 in?
E75.244 is in Chapter 4: Endocrine, Nutritional and Metabolic Diseases (codes E00-E89).
What codes cannot be used with E75.244?
E75.244 has Excludes1 notes indicating codes that cannot be used together with it, including: transitory endocrine and metabolic disorders specific to newborn (P70-P74); androgen insensitivity syndrome (E34.5-); congenital adrenal hyperplasia (E25.0); and 6 more.
What SNOMED CT codes does E75.244 map to?
E75.244 maps to 3 SNOMED CT concepts: 1362021005, 11455007, 58459009. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for E75.244?
E75.244 is linked to 2 UMLS Concept Unique Identifiers: C5539332, C5539139. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.