D81.818
BillableOther biotin-dependent carboxylase deficiency
Other biotin-dependent carboxylase deficiency
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Holocarboxylase synthetase deficiency
- Other multiple carboxylase deficiency
Includes
Conditions included under this code
- defects in the complement system
- immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
- sarcoidosis
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
- autoimmune disease (systemic) NOS (M35.9)
- certain conditions originating in the perinatal period (P00-P96)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- human immunodeficiency virus [HIV] disease (B20)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Also Known As / Clinical Terms
SNOMED CT
UMLS
- Biotin-(propionyl-CoA-carboxylase) ligase deficiencyC0268581
- Biotin-(propionyl-coenzyme A-carboxylase) ligase deficiencyC0268581
- CARBOXYLASE DEFIC MULTIPLE NEONATAL FORMC0268581
- Carboxylase Deficiency, Multiple, Neonatal FormC0268581
- DEFIC HOLOCARBOXYLASE SYNTHETASEC0268581
- DEFIC MULTIPLE CARBOXYLASE NEONATAL FORMC0268581
- Deficiencies, HLCSC0268581
- Deficiencies, Holocarboxylase SynthetaseC0268581
- Deficiency, HLCSC0268581
- Deficiency, Holocarboxylase SynthetaseC0268581
- Deficiency, Multiple Carboxylase, Neonatal FormC0268581
- Early Onset Biotin Responsive Multiple Carboxylase DeficiencyC0268581
- Early Onset Combined Carboxylase DeficiencyC0268581
- Early-Onset Biotin-Responsive Multiple Carboxylase DeficiencyC0268581
- Early-Onset Combined Carboxylase DeficiencyC0268581
- Early-onset biotin-responsive multiple carboxylase deficiencyC0268581
- Early-onset combined carboxylase deficiencyC0268581
- Early-onset multiple carboxylase deficiencyC0268581
- HLCS DEFICIENCYC0268581
- HLCS DeficienciesC0268581
- HLCS DeficiencyC0268581
- HLCS deficiencyC0268581
- HOLOCARBOXYLASE SYNTHETASE DEFICC0268581
- HOLOCARBOXYLASE SYNTHETASE DEFICIENCYC0268581
- Holocarboxylase Synthetase DeficienciesC0268581
- Holocarboxylase Synthetase DeficiencyC0268581
- Holocarboxylase synthase deficiencyC0268581
- Holocarboxylase synthase deficiency (disorder)C0268581
- Holocarboxylase synthetase deficiencyC0268581
- Infantile Multiple Carboxylase DeficiencyC0268581
- Infantile multiple carboxylase deficiencyC0268581
- MULTIPLE CARBOXYLASE DEFIC NEONATAL FORMC0268581
- MULTIPLE CARBOXYLASE DEFICIENCY, EARLY ONSETC0268581
- MULTIPLE CARBOXYLASE DEFICIENCY, NEONATAL FORMC0268581
- Multiple Carboxylase DeficiencyC0268581
- Multiple Carboxylase Deficiency, Early OnsetC0268581
- Multiple Carboxylase Deficiency, Neonatal FormC0268581
- Neonatal Holocarboxylase Synthetase DeficiencyC0268581
- Neonatal Multiple Carboxylase DeficiencyC0268581
- Neonatal multiple carboxylase deficiencyC0268581
- Other biotin-dependent carboxylase deficiencyC2873845
- Other multiple carboxylase deficiencyC2873844
Frequently Asked Questions
What is the ICD-10 code for other biotin-dependent carboxylase deficiency?
The ICD-10-CM code for other biotin-dependent carboxylase deficiency is D81.818. The full clinical description is "Other biotin-dependent carboxylase deficiency". D81.818 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code D81.818 mean?
ICD-10-CM code D81.818 represents "Other biotin-dependent carboxylase deficiency". It is classified under Chapter 3: Diseases of the Blood and Blood-Forming Organs and is a billable/specific code that can be used on a claim.
Is D81.818 a billable code?
Yes, D81.818 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is D81.818 in?
D81.818 is in Chapter 3: Diseases of the Blood and Blood-Forming Organs (codes D50-D89).
What codes cannot be used with D81.818?
D81.818 has Excludes1 notes indicating codes that cannot be used together with it, including: autoimmune disease (systemic) NOS (M35.9); functional disorders of polymorphonuclear neutrophils (D71); human immunodeficiency virus [HIV] disease (B20); and 2 more.
What SNOMED CT codes does D81.818 map to?
D81.818 maps to 2 SNOMED CT concepts: 360369003, 1172966001. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for D81.818?
D81.818 is linked to 3 UMLS Concept Unique Identifiers: C0268581, C2873845, C2873844. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.