Q89.01
BillableAsplenia (congenital)
Asplenia (congenital)
Status
Billable / Specific
Parent Code
Q89.0Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(1)
Also Known As / Clinical Terms(62)
SNOMED CT
- CDH - Congenital diaphragmatic hernia17190001
- Congenital diaphragmatic hernia17190001
- SBS - Short bowel syndrome26629001
- SGS - Short gut syndrome26629001
- Short bowel syndrome26629001
- Short gut syndrome26629001
- Short intestine syndrome26629001
- Functional asplenia38096003
- Congenital absence of spleen93030006
- Congenital asplenia93030006
- Spleen absent300564004
- Constricted pupil301939004
- Miosis301939004
- Miotic pupil301939004
- Pupil constriction301939004
- Small pupil301939004
- Congenital miosis400962005
- Aplasia of spleen702624008
- Splenic aplasia702624008
- Asplenia707147002
- Stormorken syndrome711407000
- Stormorken-Sjaastad-Langslet syndrome711407000
- Thrombocytopathy, asplenia and miosis711407000
- Congenital short bowel syndrome715201005
- Familial isolated congenital asplenia726708009
- Agenesis of spleen1003551006
- Splenic agenesis1003551006
- Diaphragmatic hernia, short bowel, asplenia syndrome1217373008
UMLS
Clinical Terms
- Congenital absence of spleen (disorder)
- Aplasia of spleen
- Miosis
- Functional asplenia
- Congenital miosis
- Diaphragmatic hernia, short bowel, asplenia syndrome
- Miotic pupil
- Stormorken syndrome
- Congenital short bowel syndrome
- Agenesis of spleen
- Congenital asplenia
- Stormorken-Sjaastad-Langslet syndrome
- Asplenia
- Short bowel syndrome
- Pupil constriction
- SGS - Short gut syndrome
- Short gut syndrome
- Small pupil
- Thrombocytopathy, asplenia and miosis
- Congenital absence of spleen
- Constricted pupil
- SBS - Short bowel syndrome
- CDH - Congenital diaphragmatic hernia
- Splenic agenesis
- Familial isolated congenital asplenia
- Short intestine syndrome
- Congenital diaphragmatic hernia
- Spleen absent
- Splenic aplasia
Frequently Asked Questions
What is the ICD-10 code for asplenia (congenital)?
The ICD-10-CM code for asplenia (congenital) is Q89.01. The full clinical description is "Asplenia (congenital)". Q89.01 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q89.01 mean?
ICD-10-CM code Q89.01 represents “Asplenia (congenital)”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q89.01 a billable code?
Yes, Q89.01 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q89.01 in?
Q89.01 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What codes cannot be used with Q89.01?
Q89.01 has Excludes1 notes indicating codes that cannot be used together with it, including: isomerism of atrial appendages (with asplenia or polysplenia) (Q20.6).
What SNOMED CT codes does Q89.01 map to?
Q89.01 maps to 14 SNOMED CT concepts: 1003551006, 702624008, 707147002, 17190001, 93030006, and 9 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q89.01?
Q89.01 is linked to 1 UMLS Concept Unique Identifier: C0600031. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q89.01 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like asplenia (congenital) affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q89.01?
There is no direct ICD-11 mapping available for Q89.01 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.