Q87.81
BillableAlport syndrome
Alport syndrome
Status
Billable / Specific
Parent Code
Q87.8Coding Notes
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
Use Additional Code
Additional codes that should follow this code
- code(s) to identify all associated manifestations
- •code to identify stage of chronic kidney diseaseN18.1-N18.6
Related Codes(6)
Also Known As / Clinical Terms(62)
SNOMED CT
- Congenital elliptocytosis191169008
- HE - hereditary elliptocytosis191169008
- Hereditary elliptocytosis191169008
- Hereditary ovalocytosis191169008
- X-linked sensorineural hearing loss232329002
- Congenital nephritis276585000
- Alport syndrome autosomal dominant717766000
- Alport syndrome autosomal recessive717767009
- Alport syndrome X-linked717768004
- AMME complex720982007
- AMME syndrome720982007
- Alport syndrome, intellectual disability, midface hypoplasia, elliptocytosis syndrome720982007
- X-linked diffuse leiomyomatosis with Alport syndrome726106004
- X-linked diffuse leiomyomatosis, Alport syndrome726106004
- Alport syndrome770414008
- Disorder of glomerulus due to Alport syndrome1148887009
- Glomerular disease due to Alport syndrome1148887009
UMLS
- Alport SyndromeC1567741
- Alport syndromeC1567741
- Alport syndrome (disorder)C1567741
- Alport's SyndromeC1567741
- Alport's syndromeC1567741
- Hematuria Nephropathy Deafness SyndromeC1567741
- Hematuria-Nephropathy-Deafness SyndromeC1567741
- Hematuria-nephropathy-deafness syndromeC1567741
- Hematuric hereditary nephritisC1567741
- Hemorrhagic familial nephritisC1567741
- Hereditary NephritisC1567741
- Hereditary nephritisC1567741
- Syndrome, AlportC1567741
- Syndrome, Hematuria-Nephropathy-DeafnessC1567741
- alport syndromeC1567741
- alport's syndromeC1567741
- alports syndromeC1567741
- syndrome alportC1567741
Clinical Terms
- alport's syndrome
- Alport syndrome autosomal recessive
- X-linked diffuse leiomyomatosis with Alport syndrome
- Congenital elliptocytosis
- Hereditary nephritis
- Alport syndrome X-linked
- syndrome alport
- Alport syndrome autosomal dominant
- Alport syndrome, intellectual disability, midface hypoplasia, elliptocytosis syndrome
- AMME syndrome
- X-linked sensorineural hearing loss
- Alport syndrome (disorder)
- X-linked diffuse leiomyomatosis, Alport syndrome
- Hematuria-nephropathy-deafness syndrome
- Hereditary ovalocytosis
- Glomerular disease due to Alport syndrome
- Syndrome, Hematuria-Nephropathy-Deafness
- HE - hereditary elliptocytosis
- Syndrome, Alport
- Hematuric hereditary nephritis
- Hematuria Nephropathy Deafness Syndrome
- Hemorrhagic familial nephritis
- AMME complex
- Congenital nephritis
- Hereditary elliptocytosis
- alports syndrome
- Disorder of glomerulus due to Alport syndrome
Frequently Asked Questions
What is the ICD-10 code for alport syndrome?
The ICD-10-CM code for alport syndrome is Q87.81. The full clinical description is "Alport syndrome". Q87.81 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q87.81 mean?
ICD-10-CM code Q87.81 represents “Alport syndrome”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q87.81 a billable code?
Yes, Q87.81 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q87.81 in?
Q87.81 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What codes cannot be used with Q87.81?
Q87.81 has Excludes1 notes indicating codes that cannot be used together with it, including: Zellweger syndrome (E71.510).
Are additional codes required with Q87.81?
Yes, when using Q87.81, also report: code(s) to identify all associated manifestations; stage of chronic kidney disease (N18.1-N18.6).
What SNOMED CT codes does Q87.81 map to?
Q87.81 maps to 10 SNOMED CT concepts: 720982007, 770414008, 717768004, 717766000, 717767009, and 5 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q87.81?
Q87.81 is linked to 1 UMLS Concept Unique Identifier: C1567741. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q87.81 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like alport syndrome affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q87.81?
There is no direct ICD-11 mapping available for Q87.81 in the WHO crosswalk tables. This may mean the concept is classified differently in ICD-11. Use the ICD-10 to ICD-11 converter to search for related codes.
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.