Q64.9
BillableCongenital malformation of urinary system, unspecified
Congenital malformation of urinary system, unspecified
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Congenital anomaly NOS of urinary system
- Congenital deformity NOS of urinary system
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(9)
Q64.0Epispadias
Q64.1Exstrophy of urinary bladder
Q64.2Congenital posterior urethral valves
Q64.3Other atresia and stenosis of urethra and bladder neck
Q64.4Malformation of urachus
Q64.5Congenital absence of bladder and urethra
Q64.6Congenital diverticulum of bladder
Q64.7Oth and unsp congenital malformations of bladder and urethra
Q64.8Other specified congenital malformations of urinary system
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(82)
SNOMED CT
- Cutis laxa, autosomal recessive59451000
- Congenital anomaly of the urinary tract118642009
- Congenital anomaly of the urinary tract proper118642009
- Congenital deformity of the urinary tract118642009
- Anal atresia204712000
- Aproctia204712000
- Atresia ani204712000
- Congenital atresia of anus204712000
- Congenital imperforate anus204712000
- Imperforate anus204712000
- Congenital abnormality of urinary system253859003
- Congenital anomaly of the urinary system253859003
- Congenital malformation of the urinary system253859003
- Congenital anomaly of male urogenital tract428522008
- Congenital male urogenital anomaly428522008
- Congenital female urogenital anomaly428680008
- Congenital cataract with intellectual disability and anal atresia and urinary defect syndrome715989002
- Karandikar Maria Kamble syndrome715989002
- Braun Bayer syndrome724092009
- Nephrosis, deafness, urinary tract, digital malformation syndrome724092009
- ARCL1C - autosomal recessive cutis laxa type 1C784349004
- Autosomal recessive cutis laxa type 1C784349004
- Cutis laxa with severe pulmonary, gastrointestinal and urinary anomalies784349004
- Urban Rifkin Davis syndrome784349004
- Cardiac urogenital syndrome1332387008
- MYRF-related cardiac urogenital syndrome1332387008
- Myelin regulatory factor-related cardiac urogenital syndrome1332387008
UMLS
- Congenital Abnormality of the Urinary SystemC0158698
- Congenital Urinary System AbnormalityC0158698
- Congenital abnormality of urinary systemC0158698
- Congenital anomaly NOS of urinary systemC0158698
- Congenital anomaly of the urinary systemC0158698
- Congenital anomaly of the urinary tractC0158698
- Congenital anomaly of the urinary tract properC0158698
- Congenital anomaly of the urinary tract proper (disorder)C0158698
- Congenital deformity NOS of urinary systemC0158698
- Congenital deformity of the urinary tractC0158698
- Congenital malformation of the urinary systemC0158698
- Congenital malformation of the urinary system (disorder)C0158698
- Congenital malformation of urinary system, unspecifiedC0158698
- Congenital malformations of the urinary system (Q60-Q64)C0158698
- Congenital urinary tract anomaly NOSC0158698
- Urinary tract malformationC0158698
- Urinary tract malformation NOSC0158698
- urinary tract malformationC0158698
Clinical Terms
- Nephrosis, deafness, urinary tract, digital malformation syndrome
- Congenital anomaly of male urogenital tract
- Congenital Abnormality of the Urinary System
- Congenital female urogenital anomaly
- Congenital anomaly of the urinary system
- Congenital deformity of the urinary tract
- Imperforate anus
- Congenital Urinary System Abnormality
- Cardiac urogenital syndrome
- Atresia ani
- urinary tract malformation
- Congenital male urogenital anomaly
- Myelin regulatory factor-related cardiac urogenital syndrome
- Congenital malformation of the urinary system
- Congenital anomaly of the urinary tract
- Aproctia
- Congenital cataract with intellectual disability and anal atresia and urinary defect syndrome
- Congenital malformations of the urinary system (Q60-Q64)
- Anal atresia
- Cutis laxa, autosomal recessive
- Urinary tract malformation NOS
- Braun Bayer syndrome
- Congenital abnormality of urinary system
- MYRF-related cardiac urogenital syndrome
- Congenital atresia of anus
- Congenital anomaly of the urinary tract proper
- Autosomal recessive cutis laxa type 1C
- Congenital deformity NOS of urinary system
- Congenital malformation of the urinary system (disorder)
- Urban Rifkin Davis syndrome
- ARCL1C - autosomal recessive cutis laxa type 1C
- Congenital anomaly of the urinary tract proper (disorder)
- Congenital urinary tract anomaly NOS
- Cutis laxa with severe pulmonary, gastrointestinal and urinary anomalies
- Congenital anomaly NOS of urinary system
- Congenital imperforate anus
- Karandikar Maria Kamble syndrome
Frequently Asked Questions
What is the ICD-10 code for congenital malformation of urinary system, unspecified?
The ICD-10-CM code for congenital malformation of urinary system, unspecified is Q64.9. The full clinical description is "Congenital malformation of urinary system, unspecified". Q64.9 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q64.9 mean?
ICD-10-CM code Q64.9 represents “Congenital malformation of urinary system, unspecified”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q64.9 a billable code?
Yes, Q64.9 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q64.9 in?
Q64.9 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What SNOMED CT codes does Q64.9 map to?
Q64.9 maps to 10 SNOMED CT concepts: 784349004, 204712000, 724092009, 1332387008, 253859003, and 5 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q64.9?
Q64.9 is linked to 1 UMLS Concept Unique Identifier: C0158698. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q64.9 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like congenital malformation of urinary system, unspecified affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q64.9?
Q64.9 maps to the ICD-11 code: LB3Z (Structural developmental anomalies of the urinary system, unspecified).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.