Q61.4
BillableRenal dysplasia
Renal dysplasia
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Multicystic dysplastic kidney
- Multicystic kidney (development)
- Multicystic kidney disease
- Multicystic renal dysplasia
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(7)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(207)
SNOMED CT
- Cirrhosis of pancreas25942009
- Fibrosis of pancreas25942009
- Congenital absence of cerebral hemispheres30023002
- Hydranencephaly30023002
- Congenital absence of the kidney204942005
- Renal agenesis204942005
- Congenital renal dysplasia204949001
- Dysplasia of kidney204949001
- Dysplastic kidney204949001
- Renal dysplasia204949001
- Bilateral renal dysgenesis204950001
- Bilateral renal dysplasia204950001
- Autosomal recessive medullary cystic disease204958008
- Familial juvenile medullary cystic kidney disease204958008
- Familial juvenile nephronophthisis204958008
- Nephronophthisis204958008
- Loken Senior syndrome236531005
- Renal dysplasia and retinal aplasia236531005
- Multiple renal cysts253883006
- Conorenal syndrome254092004
- Renal dysplasia, retinal pigmentary dystrophy, cerebellar ataxia, skeletal dysplasia syndrome254092004
- Saldino-Mainzer dysplasia254092004
- Left kidney absent443768001
- Right kidney absent443806007
- Renal dysplasia due to fetal exposure to angiotensin converting enzyme inhibitor710571007
- Renal dysplasia due to foetal exposure to angiotensin converting enzyme inhibitor710571007
- Primary renal dysplasia717742006
- Secondary renal dysplasia717744007
- Bilateral secondary renal dysplasia717745008
- Secondary renal dysplasia, bilateral717745008
- Bilateral multicystic renal dysplasia717749002
- Multicystic renal dysplasia, bilateral717749002
- BRESEK (brain anomaly, severe mental retardation, ectodermal dysplasia, skeletal deformity, ear anomaly, kidney dysplasia) syndrome717945001
- BRESEK syndrome717945001
- Brain anomaly, severe intellectual disability, ectodermal dysplasia, skeletal deformity, ear anomaly, kidney dysplasia syndrome717945001
- Brain anomaly, severe mental retardation, ectodermal dysplasia, skeletal deformity, ear anomaly, kidney dysplasia syndrome717945001
- X-linked mental retardation Reish type717945001
- Renal dysplasia with limb defect syndrome719840003
- Renal dysplasia, mesomelia, radiohumeral fusion syndrome719840003
- Ulbright Hodes syndrome719840003
- Thymic, renal, anal, lung dysplasia syndrome723555007
- Thymic-renal-anal-lung dysplasia723555007
- MCKD - Multicystic kidney disease737562008
- Multicystic dysplastic kidney737562008
- Multicystic renal dysplasia737562008
- Agenesis of left kidney762907005
- Left renal agenesis762907005
- Agenesis of right kidney762908000
- Right renal agenesis762908000
- Agenesis of right kidney co-occurrent with congenital dysplasia of left kidney762911004
- Agenesis of right kidney co-occurrent with dysplasia of left kidney762911004
- Right renal agenesis co-occurrent with left renal dysplasia762911004
- Agenesis of left kidney co-occurrent with congenital dysplasia of right kidney762912006
- Agenesis of left kidney co-occurrent with dysplasia of right kidney762912006
- Left renal agenesis co-occurrent with right renal dysplasia762912006
- Ivemark II syndrome763891005
- Renal hepatic pancreatic dysplasia763891005
- Renohepaticopancreatic dysplasia763891005
- Dysplasia of left kidney765775002
- Dysplasia of right kidney765776001
- Torticollis, keloids, cryptorchidism, renal dysplasia syndrome771266007
- Cystic dysplasia of kidney1155732005
- Cystic renal dysplasia1155732005
- MARCH syndrome1169358003
- Multinucleated neurons, anhydramnios, renal dysplasia, cerebellar hypoplasia, hydranencephaly syndrome1169358003
- Unilateral MCKD (multicystic kidney disease)1187460003
- Unilateral multicystic renal dysplasia1187460003
- Retinal pigment epithelial dystrophy342581000119102
UMLS
- Congenital renal dysplasiaC3536714
- Congenital renal dysplasia NOSC3536714
- Dysplasia of kidneyC3536714
- Dysplastic kidneyC3536714
- Dysplastic kidneysC3536714
- Primitive renal tubule syndromeC3536714
- Renal dysplasiaC3536714
- Renal dysplasia (disorder)C3536714
- dysplasia kidneyC3536714
- dysplasia kidneysC3536714
- dysplasia renalC3536714
- dysplastic kidneyC3536714
- dysplastic kidneysC3536714
- kidney dysplasiaC3536714
- renal dysplasiaC3536714
- Dysplasia, Multicystic KidneyC3714581
- Dysplasia, Multicystic RenalC3714581
- Dysplasias, Multicystic KidneyC3714581
- Dysplasias, Multicystic RenalC3714581
- Kidney Dysplasia, MulticysticC3714581
- Kidney Dysplasias, MulticysticC3714581
- MCKD - Multicystic kidney diseaseC3714581
- Multicystic Dysplastic KidneyC3714581
- Multicystic Dysplastic KidneysC3714581
- Multicystic KidneyC3714581
- Multicystic Kidney DysplasiaC3714581
- Multicystic Kidney DysplasiasC3714581
- Multicystic KidneysC3714581
- Multicystic Renal DysplasiaC3714581
- Multicystic Renal DysplasiasC3714581
- Multicystic dysplastic kidneyC3714581
- Multicystic dysplastic kidneysC3714581
- Multicystic kidneyC3714581
- Multicystic kidney dysplasiaC3714581
- Multicystic kidneysC3714581
- Multicystic renal dysplasiaC3714581
- Multicystic renal dysplasia (disorder)C3714581
- Renal Dysplasia, MulticysticC3714581
- Renal Dysplasias, MulticysticC3714581
- multicystic dysplastic kidneyC3714581
- multicystic dysplastic kidneysC3714581
- multicystic kidneyC3714581
- multicystic kidney dysplasiaC3714581
- multicystic kidneysC3714581
- multicystic renal dysplasiaC3714581
- Multicystic kidney (development)C2910226
- Multicystic kidney diseaseC2910227
Clinical Terms
- Congenital renal dysplasia NOS
- Multicystic Dysplastic Kidney
- Multicystic Renal Dysplasias
- Conorenal syndrome
- Congenital absence of the kidney
- Cystic renal dysplasia
- Multicystic kidney disease
- dysplastic kidneys
- Dysplasia, Multicystic Renal
- dysplasia kidney
- Right kidney absent
- dysplasia renal
- Saldino-Mainzer dysplasia
- Familial juvenile nephronophthisis
- Renal Dysplasias, Multicystic
- Autosomal recessive medullary cystic disease
- Secondary renal dysplasia
- Multicystic renal dysplasia, bilateral
- Cirrhosis of pancreas
- Dysplasias, Multicystic Renal
- multicystic dysplastic kidneys
- Familial juvenile medullary cystic kidney disease
- Multiple renal cysts
- Multicystic kidneys
- Ulbright Hodes syndrome
- MCKD - Multicystic kidney disease
- Right renal agenesis
- Multicystic renal dysplasia (disorder)
- multicystic kidney dysplasia
- Fibrosis of pancreas
- Unilateral MCKD (multicystic kidney disease)
- Multicystic kidney
- Cystic dysplasia of kidney
- Dysplastic kidney
- Brain anomaly, severe intellectual disability, ectodermal dysplasia, skeletal deformity, ear anomaly, kidney dysplasia syndrome
- Renal dysplasia and retinal aplasia
- BRESEK (brain anomaly, severe mental retardation, ectodermal dysplasia, skeletal deformity, ear anomaly, kidney dysplasia) syndrome
- Hydranencephaly
- Torticollis, keloids, cryptorchidism, renal dysplasia syndrome
- Dysplasias, Multicystic Kidney
- Ivemark II syndrome
- dysplasia kidneys
- Left kidney absent
- Thymic-renal-anal-lung dysplasia
- Agenesis of right kidney co-occurrent with congenital dysplasia of left kidney
- Renal hepatic pancreatic dysplasia
- Renal dysplasia (disorder)
- Bilateral renal dysplasia
- Bilateral secondary renal dysplasia
- Renal dysplasia due to foetal exposure to angiotensin converting enzyme inhibitor
- multicystic renal dysplasia
- Loken Senior syndrome
- Nephronophthisis
- Secondary renal dysplasia, bilateral
- Thymic, renal, anal, lung dysplasia syndrome
- Renal Dysplasia, Multicystic
- Left renal agenesis co-occurrent with right renal dysplasia
- Agenesis of right kidney
- Bilateral renal dysgenesis
- Dysplasia of kidney
- Dysplasia of left kidney
- Agenesis of left kidney co-occurrent with dysplasia of right kidney
- X-linked mental retardation Reish type
- Bilateral multicystic renal dysplasia
- Primary renal dysplasia
- Unilateral multicystic renal dysplasia
- Renal dysplasia due to fetal exposure to angiotensin converting enzyme inhibitor
- Congenital absence of cerebral hemispheres
- BRESEK syndrome
- Dysplasia of right kidney
- Retinal pigment epithelial dystrophy
- Renal dysplasia, retinal pigmentary dystrophy, cerebellar ataxia, skeletal dysplasia syndrome
- Agenesis of left kidney
- Agenesis of right kidney co-occurrent with dysplasia of left kidney
- Agenesis of left kidney co-occurrent with congenital dysplasia of right kidney
- Left renal agenesis
- Kidney Dysplasias, Multicystic
- Multinucleated neurons, anhydramnios, renal dysplasia, cerebellar hypoplasia, hydranencephaly syndrome
- Renal agenesis
- Multicystic Kidney Dysplasias
- Kidney Dysplasia, Multicystic
- Renohepaticopancreatic dysplasia
- Dysplasia, Multicystic Kidney
- MARCH syndrome
- kidney dysplasia
- Congenital renal dysplasia
- Brain anomaly, severe mental retardation, ectodermal dysplasia, skeletal deformity, ear anomaly, kidney dysplasia syndrome
- Multicystic kidney (development)
- Renal dysplasia, mesomelia, radiohumeral fusion syndrome
- Right renal agenesis co-occurrent with left renal dysplasia
- Primitive renal tubule syndrome
- Renal dysplasia with limb defect syndrome
Frequently Asked Questions
What is the ICD-10 code for renal dysplasia?
The ICD-10-CM code for renal dysplasia is Q61.4. The full clinical description is "Renal dysplasia". Q61.4 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q61.4 mean?
ICD-10-CM code Q61.4 represents “Renal dysplasia”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q61.4 a billable code?
Yes, Q61.4 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q61.4 in?
Q61.4 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What codes cannot be used with Q61.4?
Q61.4 has Excludes1 notes indicating codes that cannot be used together with it, including: acquired cyst of kidney (N28.1); Potter's syndrome (Q60.6); polycystic kidney disease (Q61.11-Q61.3).
What SNOMED CT codes does Q61.4 map to?
Q61.4 maps to 32 SNOMED CT concepts: 762907005, 762912006, 762908000, 762911004, 204958008, and 27 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q61.4?
Q61.4 is linked to 4 UMLS Concept Unique Identifiers: C3536714, C3714581, C2910226, C2910227. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q61.4 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like renal dysplasia affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q61.4?
Q61.4 maps to the ICD-11 code: LB30.1 (Renal dysplasia).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.