Q56.4
BillableIndeterminate sex, unspecified
Indeterminate sex, unspecified
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Ambiguous genitalia
Excludes 1
Codes that cannot be used together with this code (mutual exclusion)
- •androgen insensitivity syndromeE34.5
- •syndromes associated with anomalies in the number and form of chromosomesQ90-Q99
- •46,XX true hermaphroditeQ99.1
- •chimera 46,XX/46,XY true hermaphroditeQ99.0
- •female pseudohermaphroditism with adrenocortical disorderE25
- •pseudohermaphroditism with specified chromosomal anomalyQ96-Q99
- •pure gonadal dysgenesisQ99.1
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(4)
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(43)
SNOMED CT
- Ambiguous genitalia21321009
- SCARF (skeletal abnormality, cutis laxa, craniostenosis, ambiguous genitalia, retardation, facial abnormality) syndrome734173003
- SCARF syndrome734173003
- Skeletal abnormality, cutis laxa, craniostenosis, ambiguous genitalia, retardation, facial abnormality syndrome734173003
- Indeterminate sex32570681000036106
UMLS
- Ambiguities, GenitalC0266362
- Ambiguity, GenitalC0266362
- Ambiguous GenitaliaC0266362
- Ambiguous external genitaliaC0266362
- Ambiguous external genitalia at birthC0266362
- Ambiguous genitaliaC0266362
- Ambiguous genitalia (disorder)C0266362
- Genital AmbiguitiesC0266362
- Genital AmbiguityC0266362
- Genital ambiguityC0266362
- Genitalia external ambiguousC0266362
- Genitalia, AmbiguousC0266362
- Intersex genitaliaC0266362
- ambiguous genitaliaC0266362
- genitalia ambiguousC0266362
- Indeterminate sexC0278457
- Indeterminate sex (finding)C0278457
- Indeterminate sex, unspecifiedC0278457
- Structure of indeterminate sexC0278457
- Structure of indeterminate sex (body structure)C0278457
Clinical Terms
- Ambiguous Genitalia
- Genitalia, Ambiguous
- Indeterminate sex (finding)
- Genital Ambiguities
- Skeletal abnormality, cutis laxa, craniostenosis, ambiguous genitalia, retardation, facial abnormality syndrome
- Ambiguous external genitalia at birth
- SCARF (skeletal abnormality, cutis laxa, craniostenosis, ambiguous genitalia, retardation, facial abnormality) syndrome
- genitalia ambiguous
- Ambiguous genitalia (disorder)
- Genital Ambiguity
- Structure of indeterminate sex
- Genitalia external ambiguous
- SCARF syndrome
- Structure of indeterminate sex (body structure)
- Ambiguities, Genital
- Intersex genitalia
- Ambiguous external genitalia
- Ambiguity, Genital
Frequently Asked Questions
What is the ICD-10 code for indeterminate sex, unspecified?
The ICD-10-CM code for indeterminate sex, unspecified is Q56.4. The full clinical description is "Indeterminate sex, unspecified". Q56.4 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q56.4 mean?
ICD-10-CM code Q56.4 represents “Indeterminate sex, unspecified”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q56.4 a billable code?
Yes, Q56.4 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q56.4 in?
Q56.4 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What codes cannot be used with Q56.4?
Q56.4 has Excludes1 notes indicating codes that cannot be used together with it, including: androgen insensitivity syndrome (E34.5-); syndromes associated with anomalies in the number and form of chromosomes (Q90-Q99); 46,XX true hermaphrodite (Q99.1); and 4 more.
What SNOMED CT codes does Q56.4 map to?
Q56.4 maps to 3 SNOMED CT concepts: 21321009, 32570681000036106, 734173003. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q56.4?
Q56.4 is linked to 2 UMLS Concept Unique Identifiers: C0266362, C0278457. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q56.4 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like indeterminate sex, unspecified affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q56.4?
Q56.4 maps to the ICD-11 code: LD2A.Z (Malformative disorders of sex development, unspecified).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.