Q44.5
BillableOther congenital malformations of bile ducts
Other congenital malformations of bile ducts
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Accessory hepatic duct
- Biliary duct duplication
- Congenital malformation of bile duct NOS
- Cystic duct duplication
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(7)
Q44.0Agenesis, aplasia and hypoplasia of gallbladder
Q44.1Other congenital malformations of gallbladder
Q44.2Atresia of bile ducts
Q44.3Congenital stenosis and stricture of bile ducts
Q44.4Choledochal cyst
Q44.6Cystic disease of liver
Q44.7Other congenital malformations of liver
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(145)
SNOMED CT
- Congenital absence of bile duct1287007
- Bile duct anomalies4711003
- Biliary malformation4711003
- Congenital anomaly of bile ducts4711003
- Congenital duplication of cystic duct36619004
- Duplication of cystic duct36619004
- Congenital hyperplasia of intrahepatic bile duct40028009
- Biliary fistula53206008
- Biliary tract fistula53206008
- Fistula of bile duct53206008
- Perforation of biliary tree with fistula formation53206008
- Accessory bile duct56013008
- Congenital duplication of biliary duct56013008
- Duplication of bile duct56013008
- Congenital hypoplasia of bile duct68094008
- Congenital short bile duct68094008
- Accessory hepatic duct78560000
- Congenital hepatic fibrosis79607001
- Congenital abnormal long growth of bile duct92885004
- Congenital elongated bile duct92885004
- Bronchobiliary fistula95561009
- Congenital dilatation of lobar intrahepatic bile duct111331000
- Agenesis of hepatic ducts204781002
- Congenital absence of hepatic ducts204781002
- Liver and/or biliary duplication204790009
- Congenital diverticulum of bile duct204798002
- Congenital tracheal fistula233779005
- Congenital disorder of gallbladder and biliary tract235913009
- Biliary anomalies253804002
- Tracheobiliary fistula253809007
- Pancreatic duct anomaly253815007
- Congenital abnormality of liver and/or biliary tract268213006
- Liver and biliary system anomalies268213006
- Intrahepatic biliary hypoplasia276723008
- Cystic dilation of intrahepatic duct307133008
- Congenital biliary duct cyst398197009
- Congenital choledochal cyst398197009
- Congenital cystic dilatation of wall of biliary tract398197009
- Cystic dilatation of common bile duct440471007
- Caroli disease717232005
- Congenital bronchobiliary fistula719452004
- Congenital tracheobiliary fistula720394008
- Congenital developmental anomaly of cystic duct722868004
- Congenital respiratory biliary fistula818951009
- Congenital absence of cystic duct890201000
- Anomalous arrangement of pancreatobiliary duct890217006
- Congenital anomalous arrangement of pancreatobiliary duct890217006
- Congenital anomaly of biliary tract897541006
- Agenesis of bile duct1003567000
- Congenital PIBD (paucity of intrahepatic bile ducts)1144892000
- Congenital paucity of interlobular bile ducts1144892000
- Congenital paucity of intrahepatic bile ducts1144892000
- Congenital dilatation of CBD (common bile duct)1155727009
- Congenital dilatation of common bile duct1155727009
- Congenital dilation of CBD (common bile duct)1155727009
- Congenital dilation of common bile duct1155727009
- Congenital choledochal cyst of common bile duct1204346009
- Congenital cystic dilatation of common bile duct1204346009
- Choledochal cyst1204371007
- Choledochocyst1204371007
- Cystic dilatation of wall of biliary tract1204371007
- Caroli syndrome1237346001
- Congenital dilatation of lobar intrahepatic bile duct with obstruction97961000119108
UMLS
- Accessory bile ductC0266247
- Biliary duct duplicationC0266247
- Congenital duplication of biliary ductC0266247
- Congenital duplication of biliary duct (disorder)C0266247
- Duplication of bile ductC0266247
- Accessory hepatic ductC0266260
- Accessory hepatic duct (disorder)C0266260
- Congenital duplication of cystic ductC0266248
- Congenital duplication of cystic duct (disorder)C0266248
- Cystic duct duplicationC0266248
- Duplication of cystic ductC0266248
- Congenital malformation of bile duct NOSC2910190
- Other congenital malformations of bile ductsC0478036
Clinical Terms
- Congenital cystic dilatation of wall of biliary tract
- Congenital duplication of cystic duct (disorder)
- Congenital absence of hepatic ducts
- Tracheobiliary fistula
- Congenital bronchobiliary fistula
- Congenital anomaly of bile ducts
- Congenital dilation of common bile duct
- Fistula of bile duct
- Accessory hepatic duct (disorder)
- Choledochal cyst
- Congenital tracheal fistula
- Congenital anomalous arrangement of pancreatobiliary duct
- Congenital hyperplasia of intrahepatic bile duct
- Liver and biliary system anomalies
- Congenital dilatation of CBD (common bile duct)
- Congenital dilatation of common bile duct
- Intrahepatic biliary hypoplasia
- Caroli disease
- Congenital diverticulum of bile duct
- Anomalous arrangement of pancreatobiliary duct
- Biliary malformation
- Congenital respiratory biliary fistula
- Congenital choledochal cyst
- Cystic dilatation of common bile duct
- Cystic dilatation of wall of biliary tract
- Congenital malformation of bile duct NOS
- Cystic duct duplication
- Congenital abnormal long growth of bile duct
- Biliary tract fistula
- Congenital biliary duct cyst
- Biliary anomalies
- Choledochocyst
- Congenital duplication of biliary duct
- Congenital tracheobiliary fistula
- Cystic dilation of intrahepatic duct
- Congenital dilation of CBD (common bile duct)
- Congenital duplication of cystic duct
- Pancreatic duct anomaly
- Congenital duplication of biliary duct (disorder)
- Duplication of cystic duct
- Congenital dilatation of lobar intrahepatic bile duct with obstruction
- Congenital hypoplasia of bile duct
- Accessory hepatic duct
- Agenesis of bile duct
- Congenital absence of cystic duct
- Congenital cystic dilatation of common bile duct
- Congenital developmental anomaly of cystic duct
- Biliary fistula
- Bile duct anomalies
- Congenital anomaly of biliary tract
- Duplication of bile duct
- Liver and/or biliary duplication
- Congenital abnormality of liver and/or biliary tract
- Congenital choledochal cyst of common bile duct
- Congenital disorder of gallbladder and biliary tract
- Biliary duct duplication
- Congenital paucity of interlobular bile ducts
- Congenital short bile duct
- Congenital absence of bile duct
- Perforation of biliary tree with fistula formation
- Accessory bile duct
- Congenital PIBD (paucity of intrahepatic bile ducts)
- Congenital hepatic fibrosis
- Congenital dilatation of lobar intrahepatic bile duct
- Agenesis of hepatic ducts
- Caroli syndrome
- Congenital paucity of intrahepatic bile ducts
- Congenital elongated bile duct
- Bronchobiliary fistula
Frequently Asked Questions
What is the ICD-10 code for other congenital malformations of bile ducts?
The ICD-10-CM code for other congenital malformations of bile ducts is Q44.5. The full clinical description is "Other congenital malformations of bile ducts". Q44.5 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q44.5 mean?
ICD-10-CM code Q44.5 represents “Other congenital malformations of bile ducts”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q44.5 a billable code?
Yes, Q44.5 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q44.5 in?
Q44.5 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What SNOMED CT codes does Q44.5 map to?
Q44.5 maps to 40 SNOMED CT concepts: 56013008, 78560000, 1003567000, 204781002, 890217006, and 35 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q44.5?
Q44.5 is linked to 5 UMLS Concept Unique Identifiers: C0266247, C0266260, C0266248, C2910190, C0478036. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q44.5 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like other congenital malformations of bile ducts affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q44.5?
Q44.5 maps to the ICD-11 code: LB20.2Z (Structural developmental anomalies of bile ducts, unspecified).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.