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Q42.3

Billable

Congenital absence, atresia and stenosis of anus w/o fistula

Congenital absence, atresia and stenosis of anus without fistula

Coding Notes

Inclusion Terms

Alternative clinical terms for this condition

  • Imperforate anus

Includes

Conditions included under this code

  • congenital obstruction, occlusion and stricture of large intestine

Excludes 2

Conditions not included here, but the patient may have both

Related Codes(5)
ICD-11 Equivalents(1)

ICD-11 Equivalents

View full mapping

Corresponding ICD-11 codes from the WHO crosswalk mapping

Also Known As / Clinical Terms(133)

SNOMED CT

Clinical Terms

  • ANUS, IMPERFORATE
  • imperforate anu
  • Ankyloblepharon totale
  • Congenital ankyloblepharon
  • Fused eyelids
  • Aughton Hufnagle syndrome
  • Congenital anal stenosis
  • Stricture of anus
  • Perineal haemangioma, external genitalia malformation, lipomyelomeningocele, vesicorenal abnormality, imperforate anus syndrome
  • Ankyloblepharon
  • anus atresia
  • Atresia, Anal
  • Imperforate Anus
  • anus imperforated
  • Vertebral abnormalities, anal atresia, cardiac abnormalities, tracheo-esophageal fistula, limb defects (VACTEL) syndrome
  • Anus imperforate
  • Vertebral abnormalities, anal atresia, cardiac abnormalities, tracheo-esophageal fistula, limb defects syndrome
  • Blepharosynechia
  • Anorectal agenesis
  • Stricture of anal canal
  • Vertebral abnormality, anal atresia, cardiac abnormality, tracheo-esophageal fistula, renal anomaly, limb defect syndrome with hydrocephalus
  • Congenital stricture of anus
  • Atresia ani
  • Anal stricture
  • Vertebral abnormalities, anal atresia, cardiac abnormalities, tracheo-esophageal fistula, renal anomalies, limb defects (VACTERL) syndrome
  • anal atresia
  • Congenital imperforate anus
  • Congenital occlusion of anus
  • Vertebral abnormalities, anal atresia, cardiac abnormalities, tracheo-oesophageal fistula, renal anomalies, limb defects syndrome
  • Spondylocostal dysostosis with anal atresia and genitourinary malformation syndrome
  • VACTERL syndrome
  • Vertebral abnormality, anal atresia, cardiac abnormality, tracheo-oesophageal fistula, renal anomaly, limb defect syndrome with hydrocephalus
  • Congenital anal atresia
  • Anus absent
  • Congenital anal stricture
  • Aproctia
  • Congenital cataract with intellectual disability and anal atresia and urinary defect syndrome
  • PELVIS (Perineal haemangioma, external genitalia malformation, lipomyelomeningocele, vesicorenal abnormality, imperforate anus) syndrome
  • Anal atresia (disorder)
  • Vertebral abnormalities, anal atresia, cardiac abnormalities, tracheo-esophageal fistula, renal anomalies, limb defects syndrome
  • Perineal hemangioma, external genitalia malformation, lipomyelomeningocele, vesicorenal abnormality, imperforate anus syndrome
  • Vertebral abnormalities, anal atresia, cardiac abnormalities, tracheo-oesophageal fistula, renal anomalies, limb defects (VACTERL) syndrome
  • PELVIS (perineal hemangioma, external genitalia malformation, lipomyelomeningocele, vesicorenal abnormality, imperforate anus) syndrome
  • Ankyloblepharon filiforme adnatum with imperforate anus syndrome
  • Casamassima Morton Nance syndrome
  • Anorectal stricture
  • Congenital atresia of anus
  • Stenosis of anal canal
  • Low anorectal malformation
  • Pectenosis
  • VACTERL syndrome with hydrocephalus
  • Atresias, Anal
  • Atresia and stenosis of large intestine, rectum and anal canal
  • PELVIS syndrome
  • Congenital absence of anus
  • Ankyloblepharon filiforme adnatum
  • Anal Atresias
  • Karandikar Maria Kamble syndrome
  • VACTEL syndrome
Frequently Asked Questions
What is the ICD-10 code for congenital absence, atresia and stenosis of anus w/o fistula?

The ICD-10-CM code for congenital absence, atresia and stenosis of anus w/o fistula is Q42.3. The full clinical description is "Congenital absence, atresia and stenosis of anus without fistula". Q42.3 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code Q42.3 mean?

ICD-10-CM code Q42.3 represents “Congenital absence, atresia and stenosis of anus without fistula”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.

Is Q42.3 a billable code?

Yes, Q42.3 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is Q42.3 in?

Q42.3 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).

What SNOMED CT codes does Q42.3 map to?

Q42.3 maps to 22 SNOMED CT concepts: 204712000, 69914001, 193953008, 400952003, 773770009, and 17 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for Q42.3?

Q42.3 is linked to 2 UMLS Concept Unique Identifiers: C0003466, C0495559. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does Q42.3 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like congenital absence, atresia and stenosis of anus w/o fistula affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of Q42.3?

Q42.3 maps to the ICD-11 code: LB17.Z (Structural developmental anomalies of anal canal, unspecified).

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.