Q42.3
BillableCongenital absence, atresia and stenosis of anus w/o fistula
Congenital absence, atresia and stenosis of anus without fistula
Coding Notes
Inclusion Terms
Alternative clinical terms for this condition
- Imperforate anus
Includes
Conditions included under this code
- congenital obstruction, occlusion and stricture of large intestine
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(5)
Q42.0Congenital absence, atresia and stenosis of rectum w fistula
Q42.1Congen absence, atresia and stenosis of rectum w/o fistula
Q42.2Congenital absence, atresia and stenosis of anus w fistula
Q42.8Congenital absence, atresia and stenosis of prt lg int
Q42.9Congen absence, atresia and stenosis of lg int, part unsp
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(133)
SNOMED CT
- Anorectal agenesis975000
- VACTEL syndrome6839008
- Vertebral abnormalities, anal atresia, cardiac abnormalities, tracheo-esophageal fistula, limb defects (VACTEL) syndrome6839008
- Vertebral abnormalities, anal atresia, cardiac abnormalities, tracheo-esophageal fistula, limb defects syndrome6839008
- Stricture of anal canal55960007
- Pectenosis64153009
- Stenosis of anal canal64153009
- Anorectal stricture68627009
- Congenital occlusion of anus69817007
- Anal stricture69914001
- Stricture of anus69914001
- Congenital absence of anus75937003
- Ankyloblepharon193953008
- Anal atresia204712000
- Aproctia204712000
- Atresia ani204712000
- Congenital atresia of anus204712000
- Congenital imperforate anus204712000
- Imperforate anus204712000
- Congenital anal stenosis204723001
- Congenital anal stricture204723001
- Congenital stricture of anus204723001
- Ankyloblepharon totale253213006
- Blepharosynechia253213006
- Congenital ankyloblepharon253213006
- Fused eyelids253213006
- Low anorectal malformation253772005
- Atresia and stenosis of large intestine, rectum and anal canal268205005
- Anus absent300315008
- Ankyloblepharon filiforme adnatum400952003
- VACTERL syndrome431395004
- Vertebral abnormalities, anal atresia, cardiac abnormalities, tracheo-esophageal fistula, renal anomalies, limb defects (VACTERL) syndrome431395004
- Vertebral abnormalities, anal atresia, cardiac abnormalities, tracheo-esophageal fistula, renal anomalies, limb defects syndrome431395004
- Vertebral abnormalities, anal atresia, cardiac abnormalities, tracheo-oesophageal fistula, renal anomalies, limb defects (VACTERL) syndrome431395004
- Vertebral abnormalities, anal atresia, cardiac abnormalities, tracheo-oesophageal fistula, renal anomalies, limb defects syndrome431395004
- Congenital cataract with intellectual disability and anal atresia and urinary defect syndrome715989002
- Karandikar Maria Kamble syndrome715989002
- VACTERL syndrome with hydrocephalus719043002
- Vertebral abnormality, anal atresia, cardiac abnormality, tracheo-esophageal fistula, renal anomaly, limb defect syndrome with hydrocephalus719043002
- Vertebral abnormality, anal atresia, cardiac abnormality, tracheo-oesophageal fistula, renal anomaly, limb defect syndrome with hydrocephalus719043002
- Casamassima Morton Nance syndrome723610009
- Spondylocostal dysostosis with anal atresia and genitourinary malformation syndrome723610009
- PELVIS (Perineal haemangioma, external genitalia malformation, lipomyelomeningocele, vesicorenal abnormality, imperforate anus) syndrome725138002
- PELVIS (perineal hemangioma, external genitalia malformation, lipomyelomeningocele, vesicorenal abnormality, imperforate anus) syndrome725138002
- PELVIS syndrome725138002
- Perineal haemangioma, external genitalia malformation, lipomyelomeningocele, vesicorenal abnormality, imperforate anus syndrome725138002
- Perineal hemangioma, external genitalia malformation, lipomyelomeningocele, vesicorenal abnormality, imperforate anus syndrome725138002
- Ankyloblepharon filiforme adnatum with imperforate anus syndrome773770009
- Aughton Hufnagle syndrome773770009
UMLS
- ANUS, IMPERFORATEC0003466
- Anal AtresiaC0003466
- Anal AtresiasC0003466
- Anal atresiaC0003466
- Anal atresia (disorder)C0003466
- Anus imperforateC0003466
- Anus, ImperforateC0003466
- AproctiaC0003466
- Atresia aniC0003466
- Atresia, AnalC0003466
- Atresias, AnalC0003466
- Congenital anal atresiaC0003466
- Congenital atresia of anusC0003466
- Congenital imperforate anusC0003466
- Imperforate AnusC0003466
- Imperforate anusC0003466
- anal atresiaC0003466
- anus atresiaC0003466
- anus imperforateC0003466
- anus imperforatedC0003466
- atresia aniC0003466
- imperforate anuC0003466
- imperforate anusC0003466
- Congenital absence, atresia and stenosis of anus w/o fistulaC0495559
- Congenital absence, atresia and stenosis of anus without fistulaC0495559
Clinical Terms
- ANUS, IMPERFORATE
- imperforate anu
- Ankyloblepharon totale
- Congenital ankyloblepharon
- Fused eyelids
- Aughton Hufnagle syndrome
- Congenital anal stenosis
- Stricture of anus
- Perineal haemangioma, external genitalia malformation, lipomyelomeningocele, vesicorenal abnormality, imperforate anus syndrome
- Ankyloblepharon
- anus atresia
- Atresia, Anal
- Imperforate Anus
- anus imperforated
- Vertebral abnormalities, anal atresia, cardiac abnormalities, tracheo-esophageal fistula, limb defects (VACTEL) syndrome
- Anus imperforate
- Vertebral abnormalities, anal atresia, cardiac abnormalities, tracheo-esophageal fistula, limb defects syndrome
- Blepharosynechia
- Anorectal agenesis
- Stricture of anal canal
- Vertebral abnormality, anal atresia, cardiac abnormality, tracheo-esophageal fistula, renal anomaly, limb defect syndrome with hydrocephalus
- Congenital stricture of anus
- Atresia ani
- Anal stricture
- Vertebral abnormalities, anal atresia, cardiac abnormalities, tracheo-esophageal fistula, renal anomalies, limb defects (VACTERL) syndrome
- anal atresia
- Congenital imperforate anus
- Congenital occlusion of anus
- Vertebral abnormalities, anal atresia, cardiac abnormalities, tracheo-oesophageal fistula, renal anomalies, limb defects syndrome
- Spondylocostal dysostosis with anal atresia and genitourinary malformation syndrome
- VACTERL syndrome
- Vertebral abnormality, anal atresia, cardiac abnormality, tracheo-oesophageal fistula, renal anomaly, limb defect syndrome with hydrocephalus
- Congenital anal atresia
- Anus absent
- Congenital anal stricture
- Aproctia
- Congenital cataract with intellectual disability and anal atresia and urinary defect syndrome
- PELVIS (Perineal haemangioma, external genitalia malformation, lipomyelomeningocele, vesicorenal abnormality, imperforate anus) syndrome
- Anal atresia (disorder)
- Vertebral abnormalities, anal atresia, cardiac abnormalities, tracheo-esophageal fistula, renal anomalies, limb defects syndrome
- Perineal hemangioma, external genitalia malformation, lipomyelomeningocele, vesicorenal abnormality, imperforate anus syndrome
- Vertebral abnormalities, anal atresia, cardiac abnormalities, tracheo-oesophageal fistula, renal anomalies, limb defects (VACTERL) syndrome
- PELVIS (perineal hemangioma, external genitalia malformation, lipomyelomeningocele, vesicorenal abnormality, imperforate anus) syndrome
- Ankyloblepharon filiforme adnatum with imperforate anus syndrome
- Casamassima Morton Nance syndrome
- Anorectal stricture
- Congenital atresia of anus
- Stenosis of anal canal
- Low anorectal malformation
- Pectenosis
- VACTERL syndrome with hydrocephalus
- Atresias, Anal
- Atresia and stenosis of large intestine, rectum and anal canal
- PELVIS syndrome
- Congenital absence of anus
- Ankyloblepharon filiforme adnatum
- Anal Atresias
- Karandikar Maria Kamble syndrome
- VACTEL syndrome
Frequently Asked Questions
What is the ICD-10 code for congenital absence, atresia and stenosis of anus w/o fistula?
The ICD-10-CM code for congenital absence, atresia and stenosis of anus w/o fistula is Q42.3. The full clinical description is "Congenital absence, atresia and stenosis of anus without fistula". Q42.3 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q42.3 mean?
ICD-10-CM code Q42.3 represents “Congenital absence, atresia and stenosis of anus without fistula”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q42.3 a billable code?
Yes, Q42.3 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q42.3 in?
Q42.3 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What SNOMED CT codes does Q42.3 map to?
Q42.3 maps to 22 SNOMED CT concepts: 204712000, 69914001, 193953008, 400952003, 773770009, and 17 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q42.3?
Q42.3 is linked to 2 UMLS Concept Unique Identifiers: C0003466, C0495559. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q42.3 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like congenital absence, atresia and stenosis of anus w/o fistula affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q42.3?
Q42.3 maps to the ICD-11 code: LB17.Z (Structural developmental anomalies of anal canal, unspecified).
Automate ICD-10 Coding With AI
Send clinical text to the AutoICD API and get back structured ICD-10 codes with confidence scores. Integrates into any EHR or billing system in minutes.
Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.