AutoICD API

Q40.0

Billable

Congenital hypertrophic pyloric stenosis

Congenital hypertrophic pyloric stenosis

Status

Billable / Specific

Parent Code

Q40

ICD-11 Mapping

1 equivalent

Coding Notes

Inclusion Terms

Alternative clinical terms for this condition

  • Congenital or infantile constriction
  • Congenital or infantile hypertrophy
  • Congenital or infantile spasm
  • Congenital or infantile stenosis
  • Congenital or infantile stricture

Excludes 2

Conditions not included here, but the patient may have both

Related Codes(5)
Q40.1

Congenital hiatus hernia

BillableQ40.2

Other specified congenital malformations of stomach

BillableQ40.3

Congenital malformation of stomach, unspecified

BillableQ40.8

Oth congenital malformations of upper alimentary tract

BillableQ40.9

Congenital malformation of upper alimentary tract, unsp

Billable
ICD-11 Equivalents(1)

ICD-11 Equivalents

View full mapping

Corresponding ICD-11 codes from the WHO crosswalk mapping

LB13.0Congenital hypertrophic pyloric stenosisequivalentPrimary
Also Known As / Clinical Terms(96)

SNOMED CT

UMLS

Clinical Terms

  • Congenital pyloric spasm
  • Congenital or infantile spasm
  • PYLORIC STENOSIS, INFANTILE HYPERTROPHIC
  • Epidermolysis bullosa hereditaria letalis
  • Generalised junctional epidermolysis bullosa
  • Congenital junctional epidermolysis bullosa-pyloric atresia syndrome
  • Imperforate stomach
  • Hypertrophic Pyloric Stenosis
  • Atresia of stomach
  • Pyloric atresia
  • Congenital pylorospasm
  • Congenital or infantile constriction
  • Stenosis pyloric hypertrophic congenital
  • IHPS
  • Congenital or infantile stricture
  • Epidermolysis bullosa, junctional Herlitz-Pearson type
  • Atretogastria
  • Congenital hypertrophy of pylorus
  • Congenital hypertrophic pyloric stenosis (disorder)
  • Congenital or infantile stenosis
  • Intellectual disability, hypotonia, brachycephaly, pyloric stenosis, cryptorchidism syndrome
  • Generalized junctional epidermolysis bullosa
  • Stenosis, Hypertrophic Pyloric
  • Congenital stricture of pylorus
  • Congenital stenosis of stomach
  • Congenital or infantile hypertrophy
  • Gastric atresia
  • Pyloric antral stenosis
  • Pyloric obstruction
  • Congenital junctional epidermolysis bullosa
  • Epidermolysis bullosa letalis with pyloric atresia
  • Pylorus stenosis
  • Congenital narrowed stomach
  • PS - Pyloric stenosis
  • Congenital pyloric stenosis
  • Congenital pyloric hypertrophy
  • Pyloric stenosis
  • Infantile pyloric stenosis
  • Congenital constriction of pylorus
  • Pylorospasm
  • pyloric hypertrophic stenosis
  • Gastric outflow obstruction
  • PYLORIC STENOSIS, INFANTILE
  • Pyloric stenosis, hypertrophic
  • Infantile hypertrophic pyloric stenosis
Frequently Asked Questions
What is the ICD-10 code for congenital hypertrophic pyloric stenosis?

The ICD-10-CM code for congenital hypertrophic pyloric stenosis is Q40.0. The full clinical description is "Congenital hypertrophic pyloric stenosis". Q40.0 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code Q40.0 mean?

ICD-10-CM code Q40.0 represents “Congenital hypertrophic pyloric stenosis”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.

Is Q40.0 a billable code?

Yes, Q40.0 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is Q40.0 in?

Q40.0 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).

What SNOMED CT codes does Q40.0 map to?

Q40.0 maps to 16 SNOMED CT concepts: 28828001, 51062009, 48644003, 54616001, 79855003, and 11 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for Q40.0?

Q40.0 is linked to 6 UMLS Concept Unique Identifiers: C0700639, C2910174, C2910175, C2910176, C2910177, and 1 more. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does Q40.0 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like congenital hypertrophic pyloric stenosis affect a person's functioning — body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of Q40.0?

Q40.0 maps to the ICD-11 code: LB13.0 (Congenital hypertrophic pyloric stenosis).

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.