Q33.9
BillableCongenital malformation of lung, unspecified
Congenital malformation of lung, unspecified
Coding Notes
Excludes 2
Conditions not included here, but the patient may have both
Related Codes(8)
Q33.0Congenital cystic lung
Q33.1Accessory lobe of lung
Q33.2Sequestration of lung
Q33.3Agenesis of lung
Q33.4Congenital bronchiectasis
Q33.5Ectopic tissue in lung
Q33.6Congenital hypoplasia and dysplasia of lung
Q33.8Other congenital malformations of lung
ICD-11 Equivalents(1)
ICD-11 Equivalents
View full mappingCorresponding ICD-11 codes from the WHO crosswalk mapping
Also Known As / Clinical Terms(52)
SNOMED CT
- Congenital anomaly of lung47147007
- Congenital lung malformation47147007
- Congenital malformation of lung47147007
- Cutis laxa, autosomal recessive59451000
- Pulmonary hypertension due to lung disease and/or hypoxia697910001
- Pulmonary hypertension due to developmental abnormality of the lung697916007
- Anophthalmia with pulmonary hypoplasia syndrome722458000
- Matthew Wood syndrome722458000
- Syndromic microphthalmia type 9722458000
- SERKAL (sex reversion, kidney, adrenal and lung dysgenesis) syndrome723720008
- SERKAL syndrome723720008
- Sex reversion, kidney, adrenal and lung dysgenesis syndrome723720008
- CHOPS syndrome764455002
- Cognitive impairment, coarse facies, heart defects, obesity, pulmonary involvement, short stature, skeletal dysplasia syndrome764455002
- ARCL1C - autosomal recessive cutis laxa type 1C784349004
- Autosomal recessive cutis laxa type 1C784349004
- Cutis laxa with severe pulmonary, gastrointestinal and urinary anomalies784349004
- Urban Rifkin Davis syndrome784349004
- Genetic syndromic childhood obesity1359763002
UMLS
- Congenital Lung MalformationC0158644
- Congenital anomaly of lungC0158644
- Congenital anomaly of lung (disorder)C0158644
- Congenital anomaly of lung, unspecifiedC0158644
- Congenital lung malformationC0158644
- Congenital lung malformation NOSC0158644
- Congenital malformation of lungC0158644
- Congenital malformation of lung, unspecifiedC0158644
- Congenital malformations of lungC0158644
- congenital lung malformationC0158644
- pulmonary anomalyC0158644
Clinical Terms
- Matthew Wood syndrome
- Anophthalmia with pulmonary hypoplasia syndrome
- Congenital anomaly of lung, unspecified
- Pulmonary hypertension due to developmental abnormality of the lung
- Syndromic microphthalmia type 9
- SERKAL (sex reversion, kidney, adrenal and lung dysgenesis) syndrome
- Congenital anomaly of lung (disorder)
- Congenital lung malformation NOS
- pulmonary anomaly
- Congenital lung malformation
- Cognitive impairment, coarse facies, heart defects, obesity, pulmonary involvement, short stature, skeletal dysplasia syndrome
- Sex reversion, kidney, adrenal and lung dysgenesis syndrome
- Cutis laxa, autosomal recessive
- CHOPS syndrome
- Genetic syndromic childhood obesity
- Pulmonary hypertension due to lung disease and/or hypoxia
- Autosomal recessive cutis laxa type 1C
- Congenital anomaly of lung
- Urban Rifkin Davis syndrome
- ARCL1C - autosomal recessive cutis laxa type 1C
- Cutis laxa with severe pulmonary, gastrointestinal and urinary anomalies
- SERKAL syndrome
Frequently Asked Questions
What is the ICD-10 code for congenital malformation of lung, unspecified?
The ICD-10-CM code for congenital malformation of lung, unspecified is Q33.9. The full clinical description is "Congenital malformation of lung, unspecified". Q33.9 is a billable/specific code that can be used on insurance claims and medical billing.
What does ICD-10 code Q33.9 mean?
ICD-10-CM code Q33.9 represents “Congenital malformation of lung, unspecified”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.
Is Q33.9 a billable code?
Yes, Q33.9 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.
What chapter is Q33.9 in?
Q33.9 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).
What SNOMED CT codes does Q33.9 map to?
Q33.9 maps to 9 SNOMED CT concepts: 784349004, 722458000, 764455002, 47147007, 59451000, and 4 more. SNOMED CT is a clinical terminology used in electronic health records.
What are the UMLS CUIs for Q33.9?
Q33.9 is linked to 1 UMLS Concept Unique Identifier: C0158644. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.
How does Q33.9 relate to ICF functioning codes?
ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like congenital malformation of lung, unspecified affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.
What is the ICD-11 equivalent of Q33.9?
Q33.9 maps to the ICD-11 code: LA75.Z (Structural developmental anomalies of lungs, unspecified).
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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.