Q33.0

Billable

Congenital cystic lung

Congenital cystic lung

Status

Billable / Specific

Parent Code

Q33

ICD-11 Mapping

1 equivalent

Coding Notes

Inclusion Terms

Alternative clinical terms for this condition

  • Congenital cystic lung disease
  • Congenital honeycomb lung
  • Congenital polycystic lung disease

Excludes 1

Codes that cannot be used together with this code (mutual exclusion)

Excludes 2

Conditions not included here, but the patient may have both

Related Codes(8)
Q33.1

Accessory lobe of lung

BillableQ33.2

Sequestration of lung

BillableQ33.3

Agenesis of lung

BillableQ33.4

Congenital bronchiectasis

BillableQ33.5

Ectopic tissue in lung

BillableQ33.6

Congenital hypoplasia and dysplasia of lung

BillableQ33.8

Other congenital malformations of lung

BillableQ33.9

Congenital malformation of lung, unspecified

Billable
ICD-11 Equivalents(1)

ICD-11 Equivalents

View full mapping

Corresponding ICD-11 codes from the WHO crosswalk mapping

LA75.4Congenital pulmonary airway malformationsequivalentPrimary
Also Known As / Clinical Terms(79)

SNOMED CT

UMLS

Clinical Terms

  • Wilms tumor
  • Congenital cystic adenomatoid malformation of the lung
  • Congenital pulmonary airway malformation type 1
  • Congenital pulmonary airway malformation type 2
  • Multiple congenital bronchogenic cysts
  • GLOW syndrome
  • Congenital honeycomb lung
  • Nephroblastoma
  • Congenital honeycomb lung (disorder)
  • Cystic lung, congenital
  • Global developmental delay, lung cysts, overgrowth, Wilms tumour syndrome
  • Multiple lung cysts
  • Congenital bronchogenic cyst
  • Congenital cystic lung (disorder)
  • Congenital polycystic lung disease
  • congenital lung cysts
  • Congenital cystic adenomatoid malformation of lung
  • Congenital polycystic lung
  • Global developmental delay, lung cysts, overgrowth, Wilms tumor syndrome
  • congenital lung cyst
  • Cyst of lung
  • Congenital cystic disease of lung
  • Multiple cysts of lung
  • Congenital pulmonary airway malformation type 4
  • Congenital polycystic disease of lung
  • Congenital pulmonary airway malformation type 3
  • Wilms tumour
  • Wilm's tumor
  • Lung cyst
  • Congenital pulmonary airway malformation
  • GLOW (global developmental delay, lung cysts, overgrowth, Wilms tumor) syndrome
  • Congenital cystic lung disease
  • CPAM - Congenital pulmonary airway malformation
  • GLOW (global developmental delay, lung cysts, overgrowth, Wilms tumour) syndrome
  • Congenital pulmonary airway malformation type 0
Frequently Asked Questions
What is the ICD-10 code for congenital cystic lung?

The ICD-10-CM code for congenital cystic lung is Q33.0. The full clinical description is "Congenital cystic lung". Q33.0 is a billable/specific code that can be used on insurance claims and medical billing.

What does ICD-10 code Q33.0 mean?

ICD-10-CM code Q33.0 represents “Congenital cystic lung”. It is classified under Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities and is a billable/specific code that can be used on a claim.

Is Q33.0 a billable code?

Yes, Q33.0 is a billable/specific ICD-10-CM code and can be used to indicate a diagnosis on a medical claim.

What chapter is Q33.0 in?

Q33.0 is in Chapter 17: Congenital Malformations, Deformations and Chromosomal Abnormalities (codes Q00-Q99).

What codes cannot be used with Q33.0?

Q33.0 has Excludes1 notes indicating codes that cannot be used together with it, including: cystic fibrosis (E84.0); cystic lung disease, acquired or unspecified (J98.4).

What SNOMED CT codes does Q33.0 map to?

Q33.0 maps to 13 SNOMED CT concepts: 111318005, 762195006, 87119009, 59128005, 890394003, and 8 more. SNOMED CT is a clinical terminology used in electronic health records.

What are the UMLS CUIs for Q33.0?

Q33.0 is linked to 3 UMLS Concept Unique Identifiers: C0158641, C0265779, C0555213. The UMLS (Unified Medical Language System) integrates multiple biomedical vocabularies maintained by the U.S. National Library of Medicine.

How does Q33.0 relate to ICF functioning codes?

ICF (International Classification of Functioning, Disability and Health) codes describe how conditions like congenital cystic lung affect a person's functioning: body functions, activities, participation, and environmental factors. AutoICD provides ICF Core Sets for 12+ conditions and can map clinical text to ICF categories automatically. Browse the ICF directory to explore functioning codes.

What is the ICD-11 equivalent of Q33.0?

Q33.0 maps to the ICD-11 code: LA75.4 (Congenital pulmonary airway malformations).

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Includes SNOMED Clinical Terms® (SNOMED CT®) used by permission of SNOMED International. Includes content from the UMLS Metathesaurus, courtesy of the U.S. National Library of Medicine.